{"id":17304,"date":"2025-08-26T12:06:27","date_gmt":"2025-08-26T10:06:27","guid":{"rendered":"https:\/\/orthopus.com\/?page_id=17304"},"modified":"2025-09-01T15:39:34","modified_gmt":"2025-09-01T13:39:34","slug":"dystrophie-musculaire-traitement-technologie","status":"publish","type":"page","link":"https:\/\/orthopus.com\/fr\/maladies-neuromusculaires\/traitement-maladie-neuromusculaire\/dystrophie-musculaire-traitement-technologie\/","title":{"rendered":"Dystrophies musculaires : Traitement et Technologie"},"content":{"rendered":"\t\t<div data-elementor-type=\"wp-page\" data-elementor-id=\"17304\" class=\"elementor elementor-17304\" data-elementor-post-type=\"page\">\n\t\t\t\t<div class=\"elementor-element elementor-element-baadc77 e-flex e-con-boxed e-con e-parent\" data-id=\"baadc77\" data-element_type=\"container\" data-e-type=\"container\" data-settings=\"{&quot;jet_parallax_layout_list&quot;:[]}\">\n\t\t\t\t\t<div class=\"e-con-inner\">\n\t\t\t\t<div class=\"elementor-element elementor-element-e2fa5c1 elementor-widget elementor-widget-heading\" data-id=\"e2fa5c1\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"heading.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t<h1 class=\"elementor-heading-title elementor-size-default\">Dystrophies musculaires : d\u00e9finition et solutions pour am\u00e9liorer le quotidien<\/h1>\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t<div class=\"elementor-element elementor-element-cdfcb80 e-flex e-con-boxed e-con e-parent\" data-id=\"cdfcb80\" data-element_type=\"container\" data-e-type=\"container\" data-settings=\"{&quot;jet_parallax_layout_list&quot;:[]}\">\n\t\t\t\t\t<div class=\"e-con-inner\">\n\t\t\t\t<div class=\"elementor-element elementor-element-ac32432 elementor-widget elementor-widget-image\" data-id=\"ac32432\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"image.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t\t\t\t\t\t\t<img fetchpriority=\"high\" decoding=\"async\" width=\"800\" height=\"533\" src=\"https:\/\/orthopus.com\/wp-content\/uploads\/2025\/08\/dystrophies-musculaires.jpg\" class=\"attachment-full size-full wp-image-17389\" alt=\"\" srcset=\"https:\/\/orthopus.com\/wp-content\/uploads\/2025\/08\/dystrophies-musculaires.jpg 800w, https:\/\/orthopus.com\/wp-content\/uploads\/2025\/08\/dystrophies-musculaires-300x200.jpg 300w, https:\/\/orthopus.com\/wp-content\/uploads\/2025\/08\/dystrophies-musculaires-768x512.jpg 768w, https:\/\/orthopus.com\/wp-content\/uploads\/2025\/08\/dystrophies-musculaires-600x400.jpg 600w, https:\/\/orthopus.com\/wp-content\/uploads\/2025\/08\/dystrophies-musculaires-200x133.jpg 200w\" sizes=\"(max-width: 800px) 100vw, 800px\" \/>\t\t\t\t\t\t\t\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t<div class=\"elementor-element elementor-element-9ab079b e-flex e-con-boxed e-con e-parent\" data-id=\"9ab079b\" data-element_type=\"container\" data-e-type=\"container\" data-settings=\"{&quot;jet_parallax_layout_list&quot;:[]}\">\n\t\t\t\t\t<div class=\"e-con-inner\">\n\t\t\t\t<div class=\"elementor-element elementor-element-b9fad09 elementor-widget elementor-widget-text-editor\" data-id=\"b9fad09\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<p data-block-id=\"a7bfb672-52e3-4558-963c-44cad5d06495\" data-pm-slice=\"1 1 []\">Les dystrophies musculaires repr\u00e9sentent un <strong>ensemble de <a href=\"https:\/\/orthopus.com\/fr\/maladies-neuromusculaires\/\">maladies<\/a> g\u00e9n\u00e9tiques rares<\/strong> qui \u00e9voluent avec le temps. Dans la plupart des cas, elles sont souvent h\u00e9r\u00e9ditaires et atteignent les <strong>muscles squelettiques<\/strong>. Ce sont ceux que l\u2019on contr\u00f4le pour bouger, parler ou respirer. Ces maladies provoquent une <strong>d\u00e9t\u00e9rioration progressive<\/strong> des fibres musculaires, c\u2019est-\u00e0-dire les cellules qui permettent aux muscles de se contracter, ce qui entra\u00eene une <strong>perte de force<\/strong> et une <strong>r\u00e9duction de l\u2019autonomie<\/strong>.<\/p><p data-block-id=\"fbed4606-ada2-41a1-b4a8-4e4b5fcdc580\">Elles peuvent se manifester aussi bien chez <strong>les enfants que chez les adultes<\/strong>, avec des formes plus ou moins graves selon le type de dystrophie.<\/p><p data-block-id=\"34e9524e-df11-424a-acbf-b08fb02c2ec8\">Aujourd\u2019hui, il n\u2019existe pas de <strong>traitement curatif<\/strong>. Une prise en charge pr\u00e9coce, un <strong>suivi m\u00e9dical coordonn\u00e9<\/strong> et l\u2019<strong>aide des technologies d\u2019assistance peuvent ralentir l\u2019\u00e9volution de la maladie et am\u00e9liorer la qualit\u00e9 de vie<\/strong>.<\/p>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t<div class=\"elementor-element elementor-element-9a476f9 e-flex e-con-boxed e-con e-parent\" data-id=\"9a476f9\" data-element_type=\"container\" data-e-type=\"container\" data-settings=\"{&quot;jet_parallax_layout_list&quot;:[]}\">\n\t\t\t\t\t<div class=\"e-con-inner\">\n\t\t\t\t<div class=\"elementor-element elementor-element-9e45dc3 elementor-widget elementor-widget-spacer\" data-id=\"9e45dc3\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"spacer.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t<div class=\"elementor-spacer\">\n\t\t\t<div class=\"elementor-spacer-inner\"><\/div>\n\t\t<\/div>\n\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t<div class=\"elementor-element elementor-element-06ecc2a e-flex e-con-boxed e-con e-parent\" data-id=\"06ecc2a\" data-element_type=\"container\" data-e-type=\"container\" data-settings=\"{&quot;jet_parallax_layout_list&quot;:[]}\">\n\t\t\t\t\t<div class=\"e-con-inner\">\n\t\t\t\t<div class=\"elementor-element elementor-element-03f7ba5 elementor-widget elementor-widget-heading\" data-id=\"03f7ba5\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"heading.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t<h2 class=\"elementor-heading-title elementor-size-default\">Comprendre la dystrophie musculaire<\/h2>\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t<div class=\"elementor-element elementor-element-757ec5e e-flex e-con-boxed e-con e-parent\" data-id=\"757ec5e\" data-element_type=\"container\" data-e-type=\"container\" data-settings=\"{&quot;jet_parallax_layout_list&quot;:[]}\">\n\t\t\t\t\t<div class=\"e-con-inner\">\n\t\t\t\t<div class=\"elementor-element elementor-element-8e54feb elementor-widget elementor-widget-text-editor\" data-id=\"8e54feb\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<p data-block-id=\"721994bd-ca11-4c95-ad05-161830a169ef\" data-pm-slice=\"1 1 []\"><strong>Il existe plus d\u2019une trentaine de formes de dystrophies musculaires<\/strong>, chacune \u00e9tant li\u00e9e \u00e0 une anomalie g\u00e9n\u00e9tique. Elles touchent la structure ou la production de prot\u00e9ines indispensables au bon fonctionnement du muscle. R\u00e9sultat : <strong>les muscles se r\u00e9g\u00e9n\u00e8rent mal et s\u2019ab\u00eement peu \u00e0 peu<\/strong>. Ces maladies sont tr\u00e8s vari\u00e9es : certaines apparaissent d\u00e8s la naissance, \u00e0 l\u2019adolescence ou \u00e0 l\u2019\u00e2ge adulte. Leur <strong>\u00e9volution<\/strong> est \u00e9galement tr\u00e8s <strong>diff\u00e9rente<\/strong>. Quelques-unes progressent lentement, tandis que d\u2019autres provoquent une perte rapide de la mobilit\u00e9.<\/p>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t<div class=\"elementor-element elementor-element-0949e66 e-flex e-con-boxed e-con e-parent\" data-id=\"0949e66\" data-element_type=\"container\" data-e-type=\"container\" data-settings=\"{&quot;jet_parallax_layout_list&quot;:[]}\">\n\t\t\t\t\t<div class=\"e-con-inner\">\n\t\t\t\t<div class=\"elementor-element elementor-element-f553c46 elementor-widget elementor-widget-spacer\" data-id=\"f553c46\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"spacer.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t<div class=\"elementor-spacer\">\n\t\t\t<div class=\"elementor-spacer-inner\"><\/div>\n\t\t<\/div>\n\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t<div class=\"elementor-element elementor-element-e232245 e-flex e-con-boxed e-con e-parent\" data-id=\"e232245\" data-element_type=\"container\" data-e-type=\"container\" data-settings=\"{&quot;jet_parallax_layout_list&quot;:[]}\">\n\t\t\t\t\t<div class=\"e-con-inner\">\n\t\t\t\t<div class=\"elementor-element elementor-element-785e3c6 elementor-widget elementor-widget-heading\" data-id=\"785e3c6\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"heading.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t<h2 class=\"elementor-heading-title elementor-size-default\">Les sympt\u00f4mes des dystrophies musculaires<\/h2>\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t<div class=\"elementor-element elementor-element-51a3ad1 e-flex e-con-boxed e-con e-parent\" data-id=\"51a3ad1\" data-element_type=\"container\" data-e-type=\"container\" data-settings=\"{&quot;jet_parallax_layout_list&quot;:[]}\">\n\t\t\t\t\t<div class=\"e-con-inner\">\n\t\t\t\t<div class=\"elementor-element elementor-element-8b20717 elementor-widget elementor-widget-text-editor\" data-id=\"8b20717\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<p>Le sympt\u00f4me principal est une <strong>faiblesse musculaire progressive qui s\u2019aggrave au fil du temps<\/strong>. La d\u00e9g\u00e9n\u00e9rescence musculaire entra\u00eene une diminution de la force, des difficult\u00e9s \u00e0 marcher ou pour r\u00e9aliser des gestes du quotidien.<\/p><p>L\u2019\u00e2ge d\u2019apparition varie selon le type de dystrophie. Par exemple, les premiers sympt\u00f4mes de la <a href=\"https:\/\/orthopus.com\/fr\/maladies-neuromusculaires\/dystrophie-musculaire-de-duchenne\/\">dystrophie musculaire de Duchenne<\/a> apparaissent g\u00e9n\u00e9ralement avant 5 ans.<\/p><p>En France, les dystrophies musculaires concernent plusieurs milliers de personnes. On estime que la <a href=\"https:\/\/orthopus.com\/fr\/maladies-neuromusculaires\/dystrophie-musculaire-de-duchenne\/\">dystrophie de Duchenne<\/a> touche environ <a href=\"https:\/\/www.has-sante.fr\/upload\/docs\/application\/pdf\/2019-11\/pnds_duchenne_raccourci_18_pages_final_nov_2019_.pdf\">1 gar\u00e7on sur 3300 naissances<\/a>.<\/p>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t<div class=\"elementor-element elementor-element-b9b1620 e-flex e-con-boxed e-con e-parent\" data-id=\"b9b1620\" data-element_type=\"container\" data-e-type=\"container\" data-settings=\"{&quot;jet_parallax_layout_list&quot;:[]}\">\n\t\t\t\t\t<div class=\"e-con-inner\">\n\t\t\t\t<div class=\"elementor-element elementor-element-3727d6e elementor-widget elementor-widget-spacer\" data-id=\"3727d6e\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"spacer.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t<div class=\"elementor-spacer\">\n\t\t\t<div class=\"elementor-spacer-inner\"><\/div>\n\t\t<\/div>\n\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t<div class=\"elementor-element elementor-element-aa1285b e-flex e-con-boxed e-con e-parent\" data-id=\"aa1285b\" data-element_type=\"container\" data-e-type=\"container\" data-settings=\"{&quot;jet_parallax_layout_list&quot;:[]}\">\n\t\t\t\t\t<div class=\"e-con-inner\">\n\t\t\t\t<div class=\"elementor-element elementor-element-db52a8e elementor-widget elementor-widget-heading\" data-id=\"db52a8e\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"heading.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t<h4 class=\"elementor-heading-title elementor-size-default\">Manifestations communes \u00e0 toutes les dystrophies musculaires<\/h4>\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t<div class=\"elementor-element elementor-element-67885b9 e-flex e-con-boxed e-con e-parent\" data-id=\"67885b9\" data-element_type=\"container\" data-e-type=\"container\" data-settings=\"{&quot;jet_parallax_layout_list&quot;:[]}\">\n\t\t\t\t\t<div class=\"e-con-inner\">\n\t\t\t\t<div class=\"elementor-element elementor-element-36dcc98 elementor-widget elementor-widget-text-editor\" data-id=\"36dcc98\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<p>Bien qu\u2019il existe plusieurs formes, les sympt\u00f4mes sont communs \u00e0 l\u2019ensemble des dystrophies musculaires :<\/p><ul><li><strong>Chutes fr\u00e9quentes, perte de la marche :<\/strong> d\u00fbes \u00e0 la faiblesse musculaire progressive, elles sont souvent un indicateur cl\u00e9 d\u2019identification de la dystrophie.<\/li><li><strong>Crampes, douleurs musculaires :<\/strong> souvent d\u00e9clench\u00e9es par l\u2019effort physique, elles sont la cons\u00e9quence de la souffrance des fibres musculaires (cellules du muscle qui permettent de bouger en se contractant et en se rel\u00e2chant).<\/li><li><strong>Troubles respiratoires :<\/strong> dans les formes \u00e9volutives, les muscles respiratoires s\u2019affaiblissent, entra\u00eenant une r\u00e9duction des capacit\u00e9s pulmonaires.<\/li><li><strong>Complications cardiaques : <\/strong>certaines formes affectent \u00e9galement les muscles cardiaques dont le c\u0153ur, notamment chez les personnes atteintes de dystrophie de <a href=\"https:\/\/orthopus.com\/fr\/maladies-neuromusculaires\/dystrophie-musculaire-de-duchenne\/\">Duchenne<\/a> ou de <a href=\"https:\/\/orthopus.com\/fr\/maladies-neuromusculaires\/dystrophie-musculaire-de-becker\/\">Becker<\/a>.<\/li><\/ul>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t<div class=\"elementor-element elementor-element-4ba4640 e-flex e-con-boxed e-con e-parent\" data-id=\"4ba4640\" data-element_type=\"container\" data-e-type=\"container\" data-settings=\"{&quot;jet_parallax_layout_list&quot;:[]}\">\n\t\t\t\t\t<div class=\"e-con-inner\">\n\t\t\t\t<div class=\"elementor-element elementor-element-a902bed elementor-widget elementor-widget-image\" data-id=\"a902bed\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"image.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t\t\t\t\t\t\t<img decoding=\"async\" width=\"1024\" height=\"576\" src=\"https:\/\/orthopus.com\/wp-content\/uploads\/2025\/08\/Symptomes-dystrophie-musculaire-1024x576.webp\" class=\"attachment-large size-large wp-image-17308\" alt=\"\" srcset=\"https:\/\/orthopus.com\/wp-content\/uploads\/2025\/08\/Symptomes-dystrophie-musculaire-1024x576.webp 1024w, https:\/\/orthopus.com\/wp-content\/uploads\/2025\/08\/Symptomes-dystrophie-musculaire-300x169.webp 300w, https:\/\/orthopus.com\/wp-content\/uploads\/2025\/08\/Symptomes-dystrophie-musculaire-768x432.webp 768w, https:\/\/orthopus.com\/wp-content\/uploads\/2025\/08\/Symptomes-dystrophie-musculaire-1536x864.webp 1536w, https:\/\/orthopus.com\/wp-content\/uploads\/2025\/08\/Symptomes-dystrophie-musculaire-2048x1152.webp 2048w, https:\/\/orthopus.com\/wp-content\/uploads\/2025\/08\/Symptomes-dystrophie-musculaire-150x85.webp 150w, https:\/\/orthopus.com\/wp-content\/uploads\/2025\/08\/Symptomes-dystrophie-musculaire-1920x1080.webp 1920w, https:\/\/orthopus.com\/wp-content\/uploads\/2025\/08\/Symptomes-dystrophie-musculaire-600x338.webp 600w, https:\/\/orthopus.com\/wp-content\/uploads\/2025\/08\/Symptomes-dystrophie-musculaire-200x113.webp 200w\" sizes=\"(max-width: 1024px) 100vw, 1024px\" \/>\t\t\t\t\t\t\t\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t<div class=\"elementor-element elementor-element-50d542c e-flex e-con-boxed e-con e-parent\" data-id=\"50d542c\" data-element_type=\"container\" data-e-type=\"container\" data-settings=\"{&quot;jet_parallax_layout_list&quot;:[]}\">\n\t\t\t\t\t<div class=\"e-con-inner\">\n\t\t\t\t<div class=\"elementor-element elementor-element-f022031 elementor-widget elementor-widget-spacer\" data-id=\"f022031\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"spacer.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t<div class=\"elementor-spacer\">\n\t\t\t<div class=\"elementor-spacer-inner\"><\/div>\n\t\t<\/div>\n\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t<div class=\"elementor-element elementor-element-19cded8 e-flex e-con-boxed e-con e-parent\" data-id=\"19cded8\" data-element_type=\"container\" data-e-type=\"container\" data-settings=\"{&quot;jet_parallax_layout_list&quot;:[]}\">\n\t\t\t\t\t<div class=\"e-con-inner\">\n\t\t\t\t<div class=\"elementor-element elementor-element-89d1548 elementor-widget elementor-widget-heading\" data-id=\"89d1548\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"heading.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t<h4 class=\"elementor-heading-title elementor-size-default\">Sympt\u00f4mes sp\u00e9cifiques \u00e0 certaines formes<\/h4>\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t<div class=\"elementor-element elementor-element-e00b805 e-flex e-con-boxed e-con e-parent\" data-id=\"e00b805\" data-element_type=\"container\" data-e-type=\"container\" data-settings=\"{&quot;jet_parallax_layout_list&quot;:[]}\">\n\t\t\t\t\t<div class=\"e-con-inner\">\n\t\t\t\t<div class=\"elementor-element elementor-element-989bbcd elementor-widget elementor-widget-text-editor\" data-id=\"989bbcd\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<p>Chaque dystrophie pr\u00e9sente \u00e9galement des caract\u00e9ristiques distinctives qui permettent d\u2019en affiner le diagnostic. \u00c0 titre d\u2019exemple, on remarque dans les cas de dystrophies suivantes certaines sp\u00e9cificit\u00e9s :<\/p><ul><li><strong>Dystrophie myotonique :<\/strong> la myotonie g\u00eane quelques gestes du quotidien, c\u2019est-\u00e0-dire que les muscles ont du mal \u00e0 se rel\u00e2cher apr\u00e8s une contraction, comme par exemple desserrer la main ou rel\u00e2cher une poign\u00e9e.<\/li><li><strong><a href=\"https:\/\/orthopus.com\/fr\/maladies-neuromusculaires\/dystrophie-musculaire-de-duchenne\/\">Dystrophie de Duchenne<\/a> :<\/strong> les enfants d\u00e9montrent une pseudo-hypertrophie des mollets (les muscles paraissent plus gros, mais sans \u00eatre plus forts), une marche sur la pointe des pieds, et une difficult\u00e9 \u00e0 se relever du sol.<\/li><\/ul><p>Nous pouvons les comparer pour mieux comprendre leurs sp\u00e9cificit\u00e9s :<\/p>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t<section class=\"elementor-section elementor-top-section elementor-element elementor-element-15264e0 elementor-hidden-tablet elementor-hidden-mobile elementor-section-boxed elementor-section-height-default elementor-section-height-default\" data-id=\"15264e0\" data-element_type=\"section\" data-e-type=\"section\" data-settings=\"{&quot;jet_parallax_layout_list&quot;:[],&quot;background_background&quot;:&quot;classic&quot;}\">\n\t\t\t\t\t\t<div class=\"elementor-container elementor-column-gap-default\">\n\t\t\t\t\t<div class=\"elementor-column elementor-col-33 elementor-top-column elementor-element elementor-element-fc30c2c\" data-id=\"fc30c2c\" data-element_type=\"column\" data-e-type=\"column\" data-settings=\"{&quot;background_background&quot;:&quot;classic&quot;}\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-470c0d5 elementor-widget elementor-widget-text-editor\" data-id=\"470c0d5\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<strong>Caract\u00e9ristiques<\/strong>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t<div class=\"elementor-column elementor-col-33 elementor-top-column elementor-element elementor-element-99acd04\" data-id=\"99acd04\" data-element_type=\"column\" data-e-type=\"column\" data-settings=\"{&quot;background_background&quot;:&quot;classic&quot;}\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-b36d04d elementor-widget elementor-widget-text-editor\" data-id=\"b36d04d\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<p><a href=\"https:\/\/www.afm-telethon.fr\/fr\/fiches-maladies\/maladie-de-steinert\"><strong>Dystrophie Myotonique<\/strong><\/a><\/p>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t<div class=\"elementor-column elementor-col-33 elementor-top-column elementor-element elementor-element-aaec210\" data-id=\"aaec210\" data-element_type=\"column\" data-e-type=\"column\" data-settings=\"{&quot;background_background&quot;:&quot;classic&quot;}\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-9fa7770 elementor-widget elementor-widget-text-editor\" data-id=\"9fa7770\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<p><a href=\"https:\/\/www.afm-telethon.fr\/fr\/fiches-maladies\/dystrophie-musculaire-de-duchenne\"><strong>Dystrophie de Duchenne (DMD)<\/strong><\/a><\/p>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/section>\n\t\t\t\t<section class=\"elementor-section elementor-top-section elementor-element elementor-element-6003324 elementor-hidden-tablet elementor-hidden-mobile elementor-section-boxed elementor-section-height-default elementor-section-height-default\" data-id=\"6003324\" data-element_type=\"section\" data-e-type=\"section\" data-settings=\"{&quot;jet_parallax_layout_list&quot;:[]}\">\n\t\t\t\t\t\t<div class=\"elementor-container elementor-column-gap-default\">\n\t\t\t\t\t<div class=\"elementor-column elementor-col-33 elementor-top-column elementor-element elementor-element-45a593b\" data-id=\"45a593b\" data-element_type=\"column\" data-e-type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-3ddb1c3 elementor-widget elementor-widget-text-editor\" data-id=\"3ddb1c3\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<strong>Type de maladie<\/strong>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t<div class=\"elementor-column elementor-col-33 elementor-top-column elementor-element elementor-element-4bd0e66\" data-id=\"4bd0e66\" data-element_type=\"column\" data-e-type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-c9a3b77 elementor-widget elementor-widget-text-editor\" data-id=\"c9a3b77\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\tG\u00e9n\u00e9tique, \u00e9volution lente\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t<div class=\"elementor-column elementor-col-33 elementor-top-column elementor-element elementor-element-709b81e\" data-id=\"709b81e\" data-element_type=\"column\" data-e-type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-1c873b4 elementor-widget elementor-widget-text-editor\" data-id=\"1c873b4\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\tG\u00e9n\u00e9tique, \u00e9volution rapide\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/section>\n\t\t\t\t<section class=\"elementor-section elementor-top-section elementor-element elementor-element-4b179f6 elementor-hidden-tablet elementor-hidden-mobile elementor-section-boxed elementor-section-height-default elementor-section-height-default\" data-id=\"4b179f6\" data-element_type=\"section\" data-e-type=\"section\" data-settings=\"{&quot;jet_parallax_layout_list&quot;:[]}\">\n\t\t\t\t\t\t<div class=\"elementor-container elementor-column-gap-default\">\n\t\t\t\t\t<div class=\"elementor-column elementor-col-33 elementor-top-column elementor-element elementor-element-4f32618\" data-id=\"4f32618\" data-element_type=\"column\" data-e-type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-b5630b6 elementor-widget elementor-widget-text-editor\" data-id=\"b5630b6\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<strong>Transmission<\/strong>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t<div class=\"elementor-column elementor-col-33 elementor-top-column elementor-element elementor-element-13773dd\" data-id=\"13773dd\" data-element_type=\"column\" data-e-type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-ba41b03 elementor-widget elementor-widget-text-editor\" data-id=\"ba41b03\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\tLa transmission de la pathologie est possible si un des parents transmet un g\u00e8ne porteur d\u2019une anomalie, c\u2019est ce qu\u2019on appelle l&#8217;autosomique dominante\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t<div class=\"elementor-column elementor-col-33 elementor-top-column elementor-element elementor-element-3f4b472\" data-id=\"3f4b472\" data-element_type=\"column\" data-e-type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-190af13 elementor-widget elementor-widget-text-editor\" data-id=\"190af13\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\tLa pathologie se transmet par le chromosome X, donc elle touche surtout les gar\u00e7ons, car ils n\u2019en ont qu\u2019un. Elle est essentiellement transmise par la m\u00e8re\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/section>\n\t\t\t\t<section class=\"elementor-section elementor-top-section elementor-element elementor-element-b157fb3 elementor-hidden-tablet elementor-hidden-mobile elementor-section-boxed elementor-section-height-default elementor-section-height-default\" data-id=\"b157fb3\" data-element_type=\"section\" data-e-type=\"section\" data-settings=\"{&quot;jet_parallax_layout_list&quot;:[]}\">\n\t\t\t\t\t\t<div class=\"elementor-container elementor-column-gap-default\">\n\t\t\t\t\t<div class=\"elementor-column elementor-col-33 elementor-top-column elementor-element elementor-element-7a6ceef\" data-id=\"7a6ceef\" data-element_type=\"column\" data-e-type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-245ef3d elementor-widget elementor-widget-text-editor\" data-id=\"245ef3d\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<strong>D\u00e9but des sympt\u00f4mes<\/strong>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t<div class=\"elementor-column elementor-col-33 elementor-top-column elementor-element elementor-element-9de9298\" data-id=\"9de9298\" data-element_type=\"column\" data-e-type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-d87912c elementor-widget elementor-widget-text-editor\" data-id=\"d87912c\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\tEnfance, adolescence ou \u00e2ge adulte (variable selon le type)\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t<div class=\"elementor-column elementor-col-33 elementor-top-column elementor-element elementor-element-1e0ddab\" data-id=\"1e0ddab\" data-element_type=\"column\" data-e-type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-521d152 elementor-widget elementor-widget-text-editor\" data-id=\"521d152\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\tPetite enfance (2\/3 \u00e0 5 ans)\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/section>\n\t\t\t\t<section class=\"elementor-section elementor-top-section elementor-element elementor-element-e824f18 elementor-hidden-tablet elementor-hidden-mobile elementor-section-boxed elementor-section-height-default elementor-section-height-default\" data-id=\"e824f18\" data-element_type=\"section\" data-e-type=\"section\" data-settings=\"{&quot;jet_parallax_layout_list&quot;:[]}\">\n\t\t\t\t\t\t<div class=\"elementor-container elementor-column-gap-default\">\n\t\t\t\t\t<div class=\"elementor-column elementor-col-33 elementor-top-column elementor-element elementor-element-de9aa76\" data-id=\"de9aa76\" data-element_type=\"column\" data-e-type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-a1664d2 elementor-widget elementor-widget-text-editor\" data-id=\"a1664d2\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<strong>Muscl\u00e9s touch\u00e9s en premier<\/strong>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t<div class=\"elementor-column elementor-col-33 elementor-top-column elementor-element elementor-element-2761b6b\" data-id=\"2761b6b\" data-element_type=\"column\" data-e-type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-a93058b elementor-widget elementor-widget-text-editor\" data-id=\"a93058b\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\tVisage, cou, mains, jambes (variable)\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t<div class=\"elementor-column elementor-col-33 elementor-top-column elementor-element elementor-element-b4576b7\" data-id=\"b4576b7\" data-element_type=\"column\" data-e-type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-6d328ae elementor-widget elementor-widget-text-editor\" data-id=\"6d328ae\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\tMuscles des hanches et cuisses puis \u00e9paules, bras, tronc\u2026\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/section>\n\t\t\t\t<section class=\"elementor-section elementor-top-section elementor-element elementor-element-5356efe elementor-hidden-tablet elementor-hidden-mobile elementor-section-boxed elementor-section-height-default elementor-section-height-default\" data-id=\"5356efe\" data-element_type=\"section\" data-e-type=\"section\" data-settings=\"{&quot;jet_parallax_layout_list&quot;:[]}\">\n\t\t\t\t\t\t<div class=\"elementor-container elementor-column-gap-default\">\n\t\t\t\t\t<div class=\"elementor-column elementor-col-33 elementor-top-column elementor-element elementor-element-ec204a9\" data-id=\"ec204a9\" data-element_type=\"column\" data-e-type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-5108e1d elementor-widget elementor-widget-text-editor\" data-id=\"5108e1d\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<strong>Sympt\u00f4mes typiques<\/strong>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t<div class=\"elementor-column elementor-col-33 elementor-top-column elementor-element elementor-element-fc32288\" data-id=\"fc32288\" data-element_type=\"column\" data-e-type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-7cf4a3a elementor-widget elementor-widget-text-editor\" data-id=\"7cf4a3a\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\tFaiblesse musculaire, raideur \u00e0 la d\u00e9tente (myotonie), fatigue, troubles cardiaques et respiratoire, parfois cognitifs\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t<div class=\"elementor-column elementor-col-33 elementor-top-column elementor-element elementor-element-21c1294\" data-id=\"21c1294\" data-element_type=\"column\" data-e-type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-b6c043d elementor-widget elementor-widget-text-editor\" data-id=\"b6c043d\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\tFaiblesse musculaire rapide, chutes fr\u00e9quentes, perte de la marche, atteintes cardiaque et respiratoire\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/section>\n\t\t\t\t<section class=\"elementor-section elementor-top-section elementor-element elementor-element-218a7aa elementor-hidden-tablet elementor-hidden-mobile elementor-section-boxed elementor-section-height-default elementor-section-height-default\" data-id=\"218a7aa\" data-element_type=\"section\" data-e-type=\"section\" data-settings=\"{&quot;jet_parallax_layout_list&quot;:[]}\">\n\t\t\t\t\t\t<div class=\"elementor-container elementor-column-gap-default\">\n\t\t\t\t\t<div class=\"elementor-column elementor-col-33 elementor-top-column elementor-element elementor-element-0482f18\" data-id=\"0482f18\" data-element_type=\"column\" data-e-type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-e4a2358 elementor-widget elementor-widget-text-editor\" data-id=\"e4a2358\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<strong>\u00c9volution<\/strong>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t<div class=\"elementor-column elementor-col-33 elementor-top-column elementor-element elementor-element-0ef251d\" data-id=\"0ef251d\" data-element_type=\"column\" data-e-type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-0aa20fc elementor-widget elementor-widget-text-editor\" data-id=\"0aa20fc\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\tLente et progressive\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t<div class=\"elementor-column elementor-col-33 elementor-top-column elementor-element elementor-element-9fd9ab3\" data-id=\"9fd9ab3\" data-element_type=\"column\" data-e-type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-541a698 elementor-widget elementor-widget-text-editor\" data-id=\"541a698\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\tRapide et s\u00e9v\u00e8re\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/section>\n\t\t\t\t<section class=\"elementor-section elementor-top-section elementor-element elementor-element-67aadc4 elementor-hidden-tablet elementor-hidden-mobile elementor-section-boxed elementor-section-height-default elementor-section-height-default\" data-id=\"67aadc4\" data-element_type=\"section\" data-e-type=\"section\" data-settings=\"{&quot;jet_parallax_layout_list&quot;:[]}\">\n\t\t\t\t\t\t<div class=\"elementor-container elementor-column-gap-default\">\n\t\t\t\t\t<div class=\"elementor-column elementor-col-33 elementor-top-column elementor-element elementor-element-ede0949\" data-id=\"ede0949\" data-element_type=\"column\" data-e-type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-4441459 elementor-widget elementor-widget-text-editor\" data-id=\"4441459\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<strong>Traitement<\/strong>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t<div class=\"elementor-column elementor-col-33 elementor-top-column elementor-element elementor-element-e75ad2c\" data-id=\"e75ad2c\" data-element_type=\"column\" data-e-type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-8f403bf elementor-widget elementor-widget-text-editor\" data-id=\"8f403bf\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\tPas de traitement curatif, prise en charge pluridisciplinaire (neurologue, kin\u00e9sith\u00e9rapeute, pneumologue, cardiologue, orthophoniste, ophtalmologue, conseiller g\u00e9n\u00e9tique, m\u00e9decin en m\u00e9decine physique et de r\u00e9adaptation)\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t<div class=\"elementor-column elementor-col-33 elementor-top-column elementor-element elementor-element-dfc9136\" data-id=\"dfc9136\" data-element_type=\"column\" data-e-type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-5bac621 elementor-widget elementor-widget-text-editor\" data-id=\"5bac621\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\tPas de traitement curatif, prise en charge pluridisciplinaire (neurologue, kin\u00e9sith\u00e9rapeute, pneumologue, cardiologue, orthophoniste, ophtalmologue, conseiller g\u00e9n\u00e9tique, m\u00e9decin en m\u00e9decine physique et de r\u00e9adaptation) + recherche en cours (th\u00e9rapie g\u00e9nique, saut d\u2019exon, etc.)\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/section>\n\t\t\t\t<section class=\"elementor-section elementor-top-section elementor-element elementor-element-b820958 elementor-hidden-tablet elementor-hidden-mobile elementor-section-boxed elementor-section-height-default elementor-section-height-default\" data-id=\"b820958\" data-element_type=\"section\" data-e-type=\"section\" data-settings=\"{&quot;jet_parallax_layout_list&quot;:[]}\">\n\t\t\t\t\t\t<div class=\"elementor-container elementor-column-gap-default\">\n\t\t\t\t\t<div class=\"elementor-column elementor-col-33 elementor-top-column elementor-element elementor-element-29a1031\" data-id=\"29a1031\" data-element_type=\"column\" data-e-type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-bdabb25 elementor-widget elementor-widget-text-editor\" data-id=\"bdabb25\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<strong>Particularit\u00e9s<\/strong>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t<div class=\"elementor-column elementor-col-33 elementor-top-column elementor-element elementor-element-41aa27a\" data-id=\"41aa27a\" data-element_type=\"column\" data-e-type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-6631e73 elementor-widget elementor-widget-text-editor\" data-id=\"6631e73\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\tAtteinte de plusieurs organes  et des muscles (multisyst\u00e9mique)\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t<div class=\"elementor-column elementor-col-33 elementor-top-column elementor-element elementor-element-9437ed6\" data-id=\"9437ed6\" data-element_type=\"column\" data-e-type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-428a616 elementor-widget elementor-widget-text-editor\" data-id=\"428a616\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\tForme la plus grave des dystrophies musculaires infantiles (handicap moteur pr\u00e9coce et esp\u00e9rance de vie r\u00e9duite)\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/section>\n\t\t<div class=\"elementor-element elementor-element-5a82db4 elementor-hidden-desktop elementor-hidden-tablet e-flex e-con-boxed e-con e-parent\" data-id=\"5a82db4\" data-element_type=\"container\" data-e-type=\"container\" data-settings=\"{&quot;jet_parallax_layout_list&quot;:[]}\">\n\t\t\t\t\t<div class=\"e-con-inner\">\n\t\t\t\t<div class=\"elementor-element elementor-element-9e52208 elementor-widget elementor-widget-jet-table\" data-id=\"9e52208\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"jet-table.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t<div class=\"elementor-jet-table jet-elements\">\n\t\t<div class=\"jet-table-wrapper jet-table-responsive-tablet jet-table-responsive-mobile\">\n\t\t\t<table class=\"jet-table jet-table--fa5-compat\">\n\t\t\t\t<thead class=\"jet-table__head\"><tr class=\"jet-table__head-row\"><th class=\"jet-table__cell elementor-repeater-item-83d94a3 jet-table__head-cell\" colspan=\"1\" scope=\"col\"><div class=\"jet-table__cell-inner\"><div class=\"jet-table__cell-content\"><div class=\"jet-table__cell-text\">Caract\u00e9ristiques<\/div><\/div><\/div><\/th><th class=\"jet-table__cell elementor-repeater-item-493e60a jet-table__head-cell\" colspan=\"1\" scope=\"col\"><div class=\"jet-table__cell-inner\"><div class=\"jet-table__cell-content\"><div class=\"jet-table__cell-text\">Dystrophie Myotonique<\/div><\/div><\/div><\/th><th class=\"jet-table__cell elementor-repeater-item-81ee20e jet-table__head-cell\" colspan=\"1\" scope=\"col\"><div class=\"jet-table__cell-inner\"><div class=\"jet-table__cell-content\"><div class=\"jet-table__cell-text\">Dystrophie Musculaire de Duchenne (DMD)<\/div><\/div><\/div><\/th><\/tr><\/thead>\n\t\t\t\t\t\t\t\t<tbody class=\"jet-table__body\"><td class=\"jet-table__cell elementor-repeater-item-758ae34 jet-table__body-cell\" colspan=\"1\"><div class=\"jet-table__cell-inner\"><div class=\"jet-table__cell-content\"><div class=\"jet-table__cell-text\">Type de maladie<\/div><\/div><\/div><\/td><td class=\"jet-table__cell elementor-repeater-item-7bfd3f6 jet-table__body-cell\"><div class=\"jet-table__cell-inner\"><div class=\"jet-table__cell-content\"><div class=\"jet-table__cell-text\">G\u00e9n\u00e9tique, \u00e9volution lente<\/div><\/div><\/div><\/td><td class=\"jet-table__cell elementor-repeater-item-53caccc jet-table__body-cell\"><div class=\"jet-table__cell-inner\"><div class=\"jet-table__cell-content\"><div class=\"jet-table__cell-text\">G\u00e9n\u00e9tique, \u00e9volution rapide<\/div><\/div><\/div><\/td><tr class=\"jet-table__body-row elementor-repeater-item-b832156\"><td class=\"jet-table__cell elementor-repeater-item-ea4dd97 jet-table__body-cell\"><div class=\"jet-table__cell-inner\"><div class=\"jet-table__cell-content\"><div class=\"jet-table__cell-text\">Transmission<\/div><\/div><\/div><\/td><td class=\"jet-table__cell elementor-repeater-item-7da20ee jet-table__body-cell\"><div class=\"jet-table__cell-inner\"><div class=\"jet-table__cell-content\"><div class=\"jet-table__cell-text\">La transmission de la pathologie est possible si un des parents transmet un g\u00e8ne porteur d\u2019une anomalie, c\u2019est ce qu\u2019on appelle l&#8217;autosomique dominante<\/div><\/div><\/div><\/td><td class=\"jet-table__cell elementor-repeater-item-fc93119 jet-table__body-cell\"><div class=\"jet-table__cell-inner\"><div class=\"jet-table__cell-content\"><div class=\"jet-table__cell-text\">La pathologie se transmet par le chromosome X, donc elle touche surtout les gar\u00e7ons, car ils n\u2019en ont qu\u2019un. Elle est essentiellement transmise par la m\u00e8re<\/div><\/div><\/div><\/td><\/tr><tr class=\"jet-table__body-row elementor-repeater-item-4c7a82b\"><td class=\"jet-table__cell elementor-repeater-item-7a286be jet-table__body-cell\"><div class=\"jet-table__cell-inner\"><div class=\"jet-table__cell-content\"><div class=\"jet-table__cell-text\">D\u00e9but des sympt\u00f4mes<\/div><\/div><\/div><\/td><td class=\"jet-table__cell elementor-repeater-item-41d85bc jet-table__body-cell\"><div class=\"jet-table__cell-inner\"><div class=\"jet-table__cell-content\"><div class=\"jet-table__cell-text\">Enfance, adolescence ou \u00e2ge adulte (variable selon le type)<\/div><\/div><\/div><\/td><td class=\"jet-table__cell elementor-repeater-item-6f3049d jet-table__body-cell\"><div class=\"jet-table__cell-inner\"><div class=\"jet-table__cell-content\"><div class=\"jet-table__cell-text\">Petite enfance (2\/3 \u00e0 5 ans)\n\n<\/div><\/div><\/div><\/td><\/tr><tr class=\"jet-table__body-row elementor-repeater-item-c1f5480\"><td class=\"jet-table__cell elementor-repeater-item-b0ad168 jet-table__body-cell\"><div class=\"jet-table__cell-inner\"><div class=\"jet-table__cell-content\"><div class=\"jet-table__cell-text\">Muscles touch\u00e9s en premier<\/div><\/div><\/div><\/td><td class=\"jet-table__cell elementor-repeater-item-56ac9be jet-table__body-cell\"><div class=\"jet-table__cell-inner\"><div class=\"jet-table__cell-content\"><div class=\"jet-table__cell-text\">Visage, cou, mains, jambes (variable)<\/div><\/div><\/div><\/td><td class=\"jet-table__cell elementor-repeater-item-9fbdc6b jet-table__body-cell\"><div class=\"jet-table__cell-inner\"><div class=\"jet-table__cell-content\"><div class=\"jet-table__cell-text\">Muscles des hanches et cuisses puis \u00e9paules, bras, tronc\u2026<\/div><\/div><\/div><\/td><\/tr><tr class=\"jet-table__body-row elementor-repeater-item-40299cb\"><td class=\"jet-table__cell elementor-repeater-item-a8d3a01 jet-table__body-cell\"><div class=\"jet-table__cell-inner\"><div class=\"jet-table__cell-content\"><div class=\"jet-table__cell-text\">Sympt\u00f4mes typiques<\/div><\/div><\/div><\/td><td class=\"jet-table__cell elementor-repeater-item-158be41 jet-table__body-cell\"><div class=\"jet-table__cell-inner\"><div class=\"jet-table__cell-content\"><div class=\"jet-table__cell-text\">Faiblesse musculaire, raideur \u00e0 la d\u00e9tente (myotonie), fatigue, troubles cardiaques et respiratoire, parfois cognitifs<\/div><\/div><\/div><\/td><td class=\"jet-table__cell elementor-repeater-item-0a5127a jet-table__body-cell\"><div class=\"jet-table__cell-inner\"><div class=\"jet-table__cell-content\"><div class=\"jet-table__cell-text\">Faiblesse musculaire rapide, chutes fr\u00e9quentes, perte de la marche, atteintes cardiaque et respiratoire<\/div><\/div><\/div><\/td><\/tr><tr class=\"jet-table__body-row elementor-repeater-item-1d43b7d\"><td class=\"jet-table__cell elementor-repeater-item-f735e94 jet-table__body-cell\"><div class=\"jet-table__cell-inner\"><div class=\"jet-table__cell-content\"><div class=\"jet-table__cell-text\">\u00c9volution<\/div><\/div><\/div><\/td><td class=\"jet-table__cell elementor-repeater-item-418d497 jet-table__body-cell\"><div class=\"jet-table__cell-inner\"><div class=\"jet-table__cell-content\"><div class=\"jet-table__cell-text\">Lente et progressive<\/div><\/div><\/div><\/td><td class=\"jet-table__cell elementor-repeater-item-47e3bda jet-table__body-cell\"><div class=\"jet-table__cell-inner\"><div class=\"jet-table__cell-content\"><div class=\"jet-table__cell-text\">Rapide et s\u00e9v\u00e8re<\/div><\/div><\/div><\/td><\/tr><tr class=\"jet-table__body-row elementor-repeater-item-6a8a437\"><td class=\"jet-table__cell elementor-repeater-item-8edb09d jet-table__body-cell\"><div class=\"jet-table__cell-inner\"><div class=\"jet-table__cell-content\"><div class=\"jet-table__cell-text\">Traitement<\/div><\/div><\/div><\/td><td class=\"jet-table__cell elementor-repeater-item-927a984 jet-table__body-cell\"><div class=\"jet-table__cell-inner\"><div class=\"jet-table__cell-content\"><div class=\"jet-table__cell-text\">Pas de traitement curatif, prise en charge pluridisciplinaire (neurologue, kin\u00e9sith\u00e9rapeute, pneumologue, cardiologue, orthophoniste, ophtalmologue, conseiller g\u00e9n\u00e9tique, m\u00e9decin en m\u00e9decine physique et de r\u00e9adaptation)<\/div><\/div><\/div><\/td><td class=\"jet-table__cell elementor-repeater-item-61351fe jet-table__body-cell\"><div class=\"jet-table__cell-inner\"><div class=\"jet-table__cell-content\"><div class=\"jet-table__cell-text\">Pas de traitement curatif, prise en charge pluridisciplinaire (neurologue, kin\u00e9sith\u00e9rapeute, pneumologue, cardiologue, orthophoniste, ophtalmologue, conseiller g\u00e9n\u00e9tique, m\u00e9decin en m\u00e9decine physique et de r\u00e9adaptation) + recherche en cours (th\u00e9rapie g\u00e9nique, saut d\u2019exon, etc.)<\/div><\/div><\/div><\/td><\/tr><tr class=\"jet-table__body-row elementor-repeater-item-c182ffa\"><td class=\"jet-table__cell elementor-repeater-item-8c08171 jet-table__body-cell\"><div class=\"jet-table__cell-inner\"><div class=\"jet-table__cell-content\"><div class=\"jet-table__cell-text\">Particularit\u00e9s<\/div><\/div><\/div><\/td><td class=\"jet-table__cell elementor-repeater-item-ea3578e jet-table__body-cell\"><div class=\"jet-table__cell-inner\"><div class=\"jet-table__cell-content\"><div class=\"jet-table__cell-text\">Atteinte de plusieurs organes  et des muscles (multisyst\u00e9mique)<\/div><\/div><\/div><\/td><td class=\"jet-table__cell elementor-repeater-item-4646d61 jet-table__body-cell\"><div class=\"jet-table__cell-inner\"><div class=\"jet-table__cell-content\"><div class=\"jet-table__cell-text\">Forme la plus grave des dystrophies musculaires infantiles (handicap moteur pr\u00e9coce et esp\u00e9rance de vie r\u00e9duite)<\/div><\/div><\/div><\/td><\/tr><\/tbody>\n\t\t\t<\/table>\n\t\t<\/div>\n\n\t\t<\/div>\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t<div class=\"elementor-element elementor-element-683ac5c e-flex e-con-boxed e-con e-parent\" data-id=\"683ac5c\" data-element_type=\"container\" data-e-type=\"container\" data-settings=\"{&quot;jet_parallax_layout_list&quot;:[]}\">\n\t\t\t\t\t<div class=\"e-con-inner\">\n\t\t\t\t<div class=\"elementor-element elementor-element-11af463 elementor-widget elementor-widget-spacer\" data-id=\"11af463\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"spacer.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t<div class=\"elementor-spacer\">\n\t\t\t<div class=\"elementor-spacer-inner\"><\/div>\n\t\t<\/div>\n\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t<div class=\"elementor-element elementor-element-b375a14 e-flex e-con-boxed e-con e-parent\" data-id=\"b375a14\" data-element_type=\"container\" data-e-type=\"container\" data-settings=\"{&quot;jet_parallax_layout_list&quot;:[]}\">\n\t\t\t\t\t<div class=\"e-con-inner\">\n\t\t\t\t<div class=\"elementor-element elementor-element-a34608b elementor-widget elementor-widget-heading\" data-id=\"a34608b\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"heading.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t<h3 class=\"elementor-heading-title elementor-size-default\">Diagnostic et tests m\u00e9dicaux<\/h3>\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t<div class=\"elementor-element elementor-element-c2406ee e-flex e-con-boxed e-con e-parent\" data-id=\"c2406ee\" data-element_type=\"container\" data-e-type=\"container\" data-settings=\"{&quot;jet_parallax_layout_list&quot;:[]}\">\n\t\t\t\t\t<div class=\"e-con-inner\">\n\t\t\t\t<div class=\"elementor-element elementor-element-d078b3c elementor-widget elementor-widget-text-editor\" data-id=\"d078b3c\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<p>Le diagnostic des dystrophies musculaires repose sur de multiples examens cliniques et biologiques. Le.la m\u00e9decin neurologue commence g\u00e9n\u00e9ralement par une \u00e9valuation fonctionnelle de la force musculaire, du tonus, de la posture et de la marche. L\u2019examen clinique est compl\u00e9t\u00e9 par l\u2019analyse des ant\u00e9c\u00e9dents familiaux, souvent r\u00e9v\u00e9lateurs de la transmission g\u00e9n\u00e9tique.<\/p><p><strong>Des examens compl\u00e9mentaires permettent ensuite de confirmer l\u2019hypoth\u00e8se, tels que :<\/strong><\/p><p>\u00a0<\/p><ul><li><strong>Le dosage sanguin de la cr\u00e9atine kinase (CK) :<\/strong> une enzyme musculaire anormalement \u00e9lev\u00e9e en cas de l\u00e9sion.<\/li><li><strong>Les tests g\u00e9n\u00e9tiques :<\/strong> indissociables d\u2019un diagnostic pr\u00e9cis en relation avec la mutation recherch\u00e9e.<\/li><li><strong>La biopsie musculaire :<\/strong> parfois n\u00e9cessaire pour analyser la structure des fibres musculaires.<\/li><li><strong>L\u2019IRM (imagerie par r\u00e9sonance magn\u00e9tique) musculaire :<\/strong> pour observer le fonctionnement des muscles.<\/li><li><strong>L\u2019EMG (\u00e9lectromyographie) :<\/strong> pour \u00e9tudier les nerfs.<\/li><\/ul>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t<section class=\"elementor-section elementor-top-section elementor-element elementor-element-ffcb08b elementor-hidden-tablet elementor-hidden-mobile elementor-section-boxed elementor-section-height-default elementor-section-height-default\" data-id=\"ffcb08b\" data-element_type=\"section\" data-e-type=\"section\" data-settings=\"{&quot;jet_parallax_layout_list&quot;:[],&quot;background_background&quot;:&quot;classic&quot;}\">\n\t\t\t\t\t\t<div class=\"elementor-container elementor-column-gap-default\">\n\t\t\t\t\t<div class=\"elementor-column elementor-col-33 elementor-top-column elementor-element elementor-element-841c8fb\" data-id=\"841c8fb\" data-element_type=\"column\" data-e-type=\"column\" data-settings=\"{&quot;background_background&quot;:&quot;classic&quot;}\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-27509eb elementor-widget elementor-widget-text-editor\" data-id=\"27509eb\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<strong>Examen<\/strong>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t<div class=\"elementor-column elementor-col-33 elementor-top-column elementor-element elementor-element-f58596a\" data-id=\"f58596a\" data-element_type=\"column\" data-e-type=\"column\" data-settings=\"{&quot;background_background&quot;:&quot;classic&quot;}\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-4dcff13 elementor-widget elementor-widget-text-editor\" data-id=\"4dcff13\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<strong>Objectif<\/strong>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t<div class=\"elementor-column elementor-col-33 elementor-top-column elementor-element elementor-element-fda62a8\" data-id=\"fda62a8\" data-element_type=\"column\" data-e-type=\"column\" data-settings=\"{&quot;background_background&quot;:&quot;classic&quot;}\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-a6e8a82 elementor-widget elementor-widget-text-editor\" data-id=\"a6e8a82\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<p><strong>Pourquoi faire ?<\/strong><\/p>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/section>\n\t\t\t\t<section class=\"elementor-section elementor-top-section elementor-element elementor-element-daa9157 elementor-hidden-tablet elementor-hidden-mobile elementor-section-boxed elementor-section-height-default elementor-section-height-default\" data-id=\"daa9157\" data-element_type=\"section\" data-e-type=\"section\" data-settings=\"{&quot;jet_parallax_layout_list&quot;:[]}\">\n\t\t\t\t\t\t<div class=\"elementor-container elementor-column-gap-default\">\n\t\t\t\t\t<div class=\"elementor-column elementor-col-33 elementor-top-column elementor-element elementor-element-add2a0c\" data-id=\"add2a0c\" data-element_type=\"column\" data-e-type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-4112246 elementor-widget elementor-widget-text-editor\" data-id=\"4112246\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<strong>Analyse de sang pour mesurer le taux de cr\u00e9atine kinase<\/strong>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t<div class=\"elementor-column elementor-col-33 elementor-top-column elementor-element elementor-element-9d8d74e\" data-id=\"9d8d74e\" data-element_type=\"column\" data-e-type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-0e9d85a elementor-widget elementor-widget-text-editor\" data-id=\"0e9d85a\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\tObserver une anomalie dans un muscle\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t<div class=\"elementor-column elementor-col-33 elementor-top-column elementor-element elementor-element-bf96465\" data-id=\"bf96465\" data-element_type=\"column\" data-e-type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-7071c38 elementor-widget elementor-widget-text-editor\" data-id=\"7071c38\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t\u00c9l\u00e9vation marqu\u00e9e en cas de dystrophie\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/section>\n\t\t\t\t<section class=\"elementor-section elementor-top-section elementor-element elementor-element-17048d7 elementor-hidden-tablet elementor-hidden-mobile elementor-section-boxed elementor-section-height-default elementor-section-height-default\" data-id=\"17048d7\" data-element_type=\"section\" data-e-type=\"section\" data-settings=\"{&quot;jet_parallax_layout_list&quot;:[]}\">\n\t\t\t\t\t\t<div class=\"elementor-container elementor-column-gap-default\">\n\t\t\t\t\t<div class=\"elementor-column elementor-col-33 elementor-top-column elementor-element elementor-element-880488f\" data-id=\"880488f\" data-element_type=\"column\" data-e-type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-aef55a6 elementor-widget elementor-widget-text-editor\" data-id=\"aef55a6\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<strong>Tests g\u00e9n\u00e9tiques<\/strong>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t<div class=\"elementor-column elementor-col-33 elementor-top-column elementor-element elementor-element-2aecee1\" data-id=\"2aecee1\" data-element_type=\"column\" data-e-type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-27a4cb4 elementor-widget elementor-widget-text-editor\" data-id=\"27a4cb4\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\tIdentifier la mutation responsable\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t<div class=\"elementor-column elementor-col-33 elementor-top-column elementor-element elementor-element-629d94d\" data-id=\"629d94d\" data-element_type=\"column\" data-e-type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-144482a elementor-widget elementor-widget-text-editor\" data-id=\"144482a\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\tConfirmation du diagnostic et conseil g\u00e9n\u00e9tique\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/section>\n\t\t\t\t<section class=\"elementor-section elementor-top-section elementor-element elementor-element-7542cd5 elementor-hidden-tablet elementor-hidden-mobile elementor-section-boxed elementor-section-height-default elementor-section-height-default\" data-id=\"7542cd5\" data-element_type=\"section\" data-e-type=\"section\" data-settings=\"{&quot;jet_parallax_layout_list&quot;:[]}\">\n\t\t\t\t\t\t<div class=\"elementor-container elementor-column-gap-default\">\n\t\t\t\t\t<div class=\"elementor-column elementor-col-33 elementor-top-column elementor-element elementor-element-4f227ad\" data-id=\"4f227ad\" data-element_type=\"column\" data-e-type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-78896a8 elementor-widget elementor-widget-text-editor\" data-id=\"78896a8\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<strong>Biopsie musculaire<\/strong>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t<div class=\"elementor-column elementor-col-33 elementor-top-column elementor-element elementor-element-9247874\" data-id=\"9247874\" data-element_type=\"column\" data-e-type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-188487e elementor-widget elementor-widget-text-editor\" data-id=\"188487e\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\tObserver directement les fibres musculaires au microscope\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t<div class=\"elementor-column elementor-col-33 elementor-top-column elementor-element elementor-element-d44a74b\" data-id=\"d44a74b\" data-element_type=\"column\" data-e-type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-7777f77 elementor-widget elementor-widget-text-editor\" data-id=\"7777f77\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\tR\u00e9alisation seulement si les tests g\u00e9n\u00e9tiques ne sont pas concluants\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/section>\n\t\t<div class=\"elementor-element elementor-element-6087f58 elementor-hidden-desktop elementor-hidden-tablet e-flex e-con-boxed e-con e-parent\" data-id=\"6087f58\" data-element_type=\"container\" data-e-type=\"container\" data-settings=\"{&quot;jet_parallax_layout_list&quot;:[]}\">\n\t\t\t\t\t<div class=\"e-con-inner\">\n\t\t\t\t<div class=\"elementor-element elementor-element-20c38d3 elementor-widget elementor-widget-jet-table\" data-id=\"20c38d3\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"jet-table.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t<div class=\"elementor-jet-table jet-elements\">\n\t\t<div class=\"jet-table-wrapper jet-table-responsive-tablet jet-table-responsive-mobile\">\n\t\t\t<table class=\"jet-table jet-table--fa5-compat\">\n\t\t\t\t<thead class=\"jet-table__head\"><tr class=\"jet-table__head-row\"><th class=\"jet-table__cell elementor-repeater-item-83d94a3 jet-table__head-cell\" colspan=\"1\" scope=\"col\"><div class=\"jet-table__cell-inner\"><div class=\"jet-table__cell-content\"><div class=\"jet-table__cell-text\">Examen<\/div><\/div><\/div><\/th><th class=\"jet-table__cell elementor-repeater-item-493e60a jet-table__head-cell\" colspan=\"1\" scope=\"col\"><div class=\"jet-table__cell-inner\"><div class=\"jet-table__cell-content\"><div class=\"jet-table__cell-text\">Objectif<\/div><\/div><\/div><\/th><th class=\"jet-table__cell elementor-repeater-item-81ee20e jet-table__head-cell\" colspan=\"1\" scope=\"col\"><div class=\"jet-table__cell-inner\"><div class=\"jet-table__cell-content\"><div class=\"jet-table__cell-text\">Pourquoi faire ?<\/div><\/div><\/div><\/th><\/tr><\/thead>\n\t\t\t\t\t\t\t\t<tbody class=\"jet-table__body\"><td class=\"jet-table__cell elementor-repeater-item-758ae34 jet-table__body-cell\" colspan=\"1\"><div class=\"jet-table__cell-inner\"><div class=\"jet-table__cell-content\"><div class=\"jet-table__cell-text\">Analyse de sang pour mesurer le taux de cr\u00e9atine kinase<\/div><\/div><\/div><\/td><td class=\"jet-table__cell elementor-repeater-item-7bfd3f6 jet-table__body-cell\"><div class=\"jet-table__cell-inner\"><div class=\"jet-table__cell-content\"><div class=\"jet-table__cell-text\">Observer une anomalie dans un muscle<\/div><\/div><\/div><\/td><td class=\"jet-table__cell elementor-repeater-item-53caccc jet-table__body-cell\"><div class=\"jet-table__cell-inner\"><div class=\"jet-table__cell-content\"><div class=\"jet-table__cell-text\">\u00c9l\u00e9vation marqu\u00e9e en cas de dystrophie<\/div><\/div><\/div><\/td><tr class=\"jet-table__body-row elementor-repeater-item-b832156\"><td class=\"jet-table__cell elementor-repeater-item-ea4dd97 jet-table__body-cell\"><div class=\"jet-table__cell-inner\"><div class=\"jet-table__cell-content\"><div class=\"jet-table__cell-text\">Tests g\u00e9n\u00e9tiques<\/div><\/div><\/div><\/td><td class=\"jet-table__cell elementor-repeater-item-7da20ee jet-table__body-cell\"><div class=\"jet-table__cell-inner\"><div class=\"jet-table__cell-content\"><div class=\"jet-table__cell-text\">Identifier la mutation responsable<\/div><\/div><\/div><\/td><td class=\"jet-table__cell elementor-repeater-item-fc93119 jet-table__body-cell\"><div class=\"jet-table__cell-inner\"><div class=\"jet-table__cell-content\"><div class=\"jet-table__cell-text\">Confirmation du diagnostic et conseil g\u00e9n\u00e9tique<\/div><\/div><\/div><\/td><\/tr><tr class=\"jet-table__body-row elementor-repeater-item-4c7a82b\"><td class=\"jet-table__cell elementor-repeater-item-7a286be jet-table__body-cell\"><div class=\"jet-table__cell-inner\"><div class=\"jet-table__cell-content\"><div class=\"jet-table__cell-text\">Biopsie musculaire<\/div><\/div><\/div><\/td><td class=\"jet-table__cell elementor-repeater-item-41d85bc jet-table__body-cell\"><div class=\"jet-table__cell-inner\"><div class=\"jet-table__cell-content\"><div class=\"jet-table__cell-text\">Observer directement les fibres musculaires au microscope<\/div><\/div><\/div><\/td><td class=\"jet-table__cell elementor-repeater-item-6f3049d jet-table__body-cell\"><div class=\"jet-table__cell-inner\"><div class=\"jet-table__cell-content\"><div class=\"jet-table__cell-text\">R\u00e9alisation seulement si les tests g\u00e9n\u00e9tiques ne sont pas concluants\n<\/div><\/div><\/div><\/td><\/tr><\/tbody>\n\t\t\t<\/table>\n\t\t<\/div>\n\n\t\t<\/div>\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t<div class=\"elementor-element elementor-element-627ae27 e-flex e-con-boxed e-con e-parent\" data-id=\"627ae27\" data-element_type=\"container\" data-e-type=\"container\" data-settings=\"{&quot;jet_parallax_layout_list&quot;:[]}\">\n\t\t\t\t\t<div class=\"e-con-inner\">\n\t\t\t\t<div class=\"elementor-element elementor-element-0265618 elementor-widget elementor-widget-spacer\" data-id=\"0265618\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"spacer.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t<div class=\"elementor-spacer\">\n\t\t\t<div class=\"elementor-spacer-inner\"><\/div>\n\t\t<\/div>\n\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t<div class=\"elementor-element elementor-element-d103518 e-flex e-con-boxed e-con e-parent\" data-id=\"d103518\" data-element_type=\"container\" data-e-type=\"container\" data-settings=\"{&quot;jet_parallax_layout_list&quot;:[]}\">\n\t\t\t\t\t<div class=\"e-con-inner\">\n\t\t\t\t<div class=\"elementor-element elementor-element-cbff0f0 elementor-widget elementor-widget-heading\" data-id=\"cbff0f0\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"heading.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t<h2 class=\"elementor-heading-title elementor-size-default\">Liste des principales dystrophies musculaires et leurs caract\u00e9ristiques<\/h2>\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t<div class=\"elementor-element elementor-element-7ac140a e-flex e-con-boxed e-con e-parent\" data-id=\"7ac140a\" data-element_type=\"container\" data-e-type=\"container\" data-settings=\"{&quot;jet_parallax_layout_list&quot;:[]}\">\n\t\t\t\t\t<div class=\"e-con-inner\">\n\t\t\t\t<div class=\"elementor-element elementor-element-d1b918e elementor-widget elementor-widget-text-editor\" data-id=\"d1b918e\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\tIl est crucial de distinguer correctement les diff\u00e9rentes formes de dystrophie musculaire, car chacune implique une \u00e9volution clinique et une prise en charge particuli\u00e8re. Voici un aper\u00e7u des principales formes connues :\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t<div class=\"elementor-element elementor-element-7532073 e-flex e-con-boxed e-con e-parent\" data-id=\"7532073\" data-element_type=\"container\" data-e-type=\"container\" data-settings=\"{&quot;jet_parallax_layout_list&quot;:[]}\">\n\t\t\t\t\t<div class=\"e-con-inner\">\n\t\t\t\t<div class=\"elementor-element elementor-element-d62fc7c elementor-widget elementor-widget-spacer\" data-id=\"d62fc7c\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"spacer.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t<div class=\"elementor-spacer\">\n\t\t\t<div class=\"elementor-spacer-inner\"><\/div>\n\t\t<\/div>\n\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t<div class=\"elementor-element elementor-element-3f526ef e-flex e-con-boxed e-con e-parent\" data-id=\"3f526ef\" data-element_type=\"container\" data-e-type=\"container\" data-settings=\"{&quot;jet_parallax_layout_list&quot;:[]}\">\n\t\t\t\t\t<div class=\"e-con-inner\">\n\t\t\t\t<div class=\"elementor-element elementor-element-c798325 elementor-widget elementor-widget-heading\" data-id=\"c798325\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"heading.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t<h3 class=\"elementor-heading-title elementor-size-default\">Les dystrophies musculaires les plus fr\u00e9quentes<\/h3>\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t<div class=\"elementor-element elementor-element-66aa2c1 e-flex e-con-boxed e-con e-parent\" data-id=\"66aa2c1\" data-element_type=\"container\" data-e-type=\"container\" data-settings=\"{&quot;jet_parallax_layout_list&quot;:[]}\">\n\t\t\t\t\t<div class=\"e-con-inner\">\n\t\t\t\t<div class=\"elementor-element elementor-element-9a291f7 elementor-widget elementor-widget-text-editor\" data-id=\"9a291f7\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<ul><li><strong><a href=\"https:\/\/orthopus.com\/fr\/maladies-neuromusculaires\/dystrophie-musculaire-de-duchenne\/\">Dystrophie musculaire de Duchenne<\/a> (DMD) :<\/strong> la forme la plus s\u00e9v\u00e8re et la plus pr\u00e9coce. Elle se transmet par le chromosome X et touche presque exclusivement les gar\u00e7ons. Elle entra\u00eene une perte de la marche avant 12 ans et des s\u00e9quelles respiratoires et cardiaques \u00e0 l\u2019adolescence.<\/li><li><strong><a href=\"https:\/\/orthopus.com\/fr\/maladies-neuromusculaires\/dystrophie-musculaire-de-becker\/\">Dystrophie musculaire de Becker (DMB)<\/a> :<\/strong> une forme plus mod\u00e9r\u00e9e que la maladie de Duchenne. Elle \u00e9volue plus lentement, et certain\u2022es personnes peuvent conserver la marche jusqu\u2019\u00e0 l\u2019\u00e2ge adulte.<\/li><li><strong>Dystrophie facio-scapulo-hum\u00e9rale (FSH) :<\/strong> une forme relativement fr\u00e9quente, qui \u00e9volue lentement et qui touche principalement les muscles du visage, des omoplates et des bras. Elle touche les hommes comme les femmes et se pr\u00e9sente souvent avec des formes tr\u00e8s vari\u00e9es m\u00eame au sein d&#8217;une m\u00eame famille.<\/li><\/ul>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t<div class=\"elementor-element elementor-element-f4ac7d5 e-flex e-con-boxed e-con e-parent\" data-id=\"f4ac7d5\" data-element_type=\"container\" data-e-type=\"container\" data-settings=\"{&quot;jet_parallax_layout_list&quot;:[]}\">\n\t\t\t\t\t<div class=\"e-con-inner\">\n\t\t\t\t<div class=\"elementor-element elementor-element-2f696b0 elementor-widget elementor-widget-spacer\" data-id=\"2f696b0\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"spacer.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t<div class=\"elementor-spacer\">\n\t\t\t<div class=\"elementor-spacer-inner\"><\/div>\n\t\t<\/div>\n\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t<div class=\"elementor-element elementor-element-1ceb312 e-flex e-con-boxed e-con e-parent\" data-id=\"1ceb312\" data-element_type=\"container\" data-e-type=\"container\" data-settings=\"{&quot;jet_parallax_layout_list&quot;:[]}\">\n\t\t\t\t\t<div class=\"e-con-inner\">\n\t\t\t\t<div class=\"elementor-element elementor-element-ca3d801 elementor-widget elementor-widget-heading\" data-id=\"ca3d801\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"heading.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t<h3 class=\"elementor-heading-title elementor-size-default\">Dystrophies musculaires des ceintures et dystrophie musculaire cong\u00e9nitale<\/h3>\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t<div class=\"elementor-element elementor-element-e875365 e-flex e-con-boxed e-con e-parent\" data-id=\"e875365\" data-element_type=\"container\" data-e-type=\"container\" data-settings=\"{&quot;jet_parallax_layout_list&quot;:[]}\">\n\t\t\t\t\t<div class=\"e-con-inner\">\n\t\t\t\t<div class=\"elementor-element elementor-element-db9276c elementor-widget elementor-widget-text-editor\" data-id=\"db9276c\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<ul><li><strong>Dystrophies musculaires des ceintures (LGMD) :<\/strong> ensemble h\u00e9t\u00e9rog\u00e8ne de maladies atteignant les muscles de la ceinture pelvienne et scapulaire (omoplates). Elles se manifestent souvent \u00e0 l\u2019adolescence ou \u00e0 l\u2019\u00e2ge adulte et se traduisent en une perte progressive de la mobilit\u00e9.<\/li><li><strong>Dystrophies musculaires cong\u00e9nitales :<\/strong> formes rares, pr\u00e9sentes d\u00e8s la naissance. Elles sont responsables de troubles moteurs pr\u00e9coces, d\u2019un tonus musculaire bas, appel\u00e9 hypotonie, et parfois de malformations c\u00e9r\u00e9brales associ\u00e9es. Leur \u00e9volution est variable, quelques-unes entra\u00eenent un lourd handicap d\u00e8s l\u2019enfance.<\/li><\/ul>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t<div class=\"elementor-element elementor-element-ebc4f05 e-flex e-con-boxed e-con e-parent\" data-id=\"ebc4f05\" data-element_type=\"container\" data-e-type=\"container\" data-settings=\"{&quot;jet_parallax_layout_list&quot;:[]}\">\n\t\t\t\t\t<div class=\"e-con-inner\">\n\t\t\t\t<div class=\"elementor-element elementor-element-9b5bcc1 elementor-widget elementor-widget-spacer\" data-id=\"9b5bcc1\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"spacer.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t<div class=\"elementor-spacer\">\n\t\t\t<div class=\"elementor-spacer-inner\"><\/div>\n\t\t<\/div>\n\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t<div class=\"elementor-element elementor-element-a709001 e-flex e-con-boxed e-con e-parent\" data-id=\"a709001\" data-element_type=\"container\" data-e-type=\"container\" data-settings=\"{&quot;jet_parallax_layout_list&quot;:[]}\">\n\t\t\t\t\t<div class=\"e-con-inner\">\n\t\t\t\t<div class=\"elementor-element elementor-element-7c96630 elementor-widget elementor-widget-heading\" data-id=\"7c96630\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"heading.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t<h2 class=\"elementor-heading-title elementor-size-default\">Suivi m\u00e9dical et param\u00e9dical : am\u00e9liorer la qualit\u00e9 de vie des personnes en situation de handicap<\/h2>\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t<div class=\"elementor-element elementor-element-5d78750 e-flex e-con-boxed e-con e-parent\" data-id=\"5d78750\" data-element_type=\"container\" data-e-type=\"container\" data-settings=\"{&quot;jet_parallax_layout_list&quot;:[]}\">\n\t\t\t\t\t<div class=\"e-con-inner\">\n\t\t\t\t<div class=\"elementor-element elementor-element-5eee0d7 elementor-widget elementor-widget-text-editor\" data-id=\"5eee0d7\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<p>Il n\u2019existe pas de traitement curatif pour les dystrophies musculaires, mais leur prise en charge repose sur des <a href=\"https:\/\/orthopus.com\/fr\/maladies-neuromusculaires\/traitement-maladie-neuromusculaire\/\">strat\u00e9gies m\u00e9dicales et param\u00e9dicales rigoureuses<\/a>. Elles permettent de ralentir l\u2019\u00e9volution de la maladie, d\u2019\u00e9viter quelques complications et surtout d\u2019<strong>am\u00e9liorer la qualit\u00e9 de vie des personnes en situation de handicap<\/strong>.<\/p><p>Ce suivi doit \u00eatre adapt\u00e9 \u00e0 chaque individu\u2022e. Il \u00e9volue en fonction du type de dystrophie, de l\u2019\u00e2ge, de la vitesse de progression et des atteintes sp\u00e9cifiques. Il est essentiel d\u2019impliquer une \u00e9quipe soignante vari\u00e9e, coordonn\u00e9e autour de la personne qui vit avec une dystrophie musculaire.<\/p>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t<div class=\"elementor-element elementor-element-c3b65ad e-flex e-con-boxed e-con e-parent\" data-id=\"c3b65ad\" data-element_type=\"container\" data-e-type=\"container\" data-settings=\"{&quot;jet_parallax_layout_list&quot;:[]}\">\n\t\t\t\t\t<div class=\"e-con-inner\">\n\t\t\t\t<div class=\"elementor-element elementor-element-a333202 elementor-widget elementor-widget-spacer\" data-id=\"a333202\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"spacer.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t<div class=\"elementor-spacer\">\n\t\t\t<div class=\"elementor-spacer-inner\"><\/div>\n\t\t<\/div>\n\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t<div class=\"elementor-element elementor-element-9b09f55 e-flex e-con-boxed e-con e-parent\" data-id=\"9b09f55\" data-element_type=\"container\" data-e-type=\"container\" data-settings=\"{&quot;jet_parallax_layout_list&quot;:[]}\">\n\t\t\t\t\t<div class=\"e-con-inner\">\n\t\t\t\t<div class=\"elementor-element elementor-element-84f5865 elementor-widget elementor-widget-heading\" data-id=\"84f5865\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"heading.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t<h3 class=\"elementor-heading-title elementor-size-default\">Une prise en charge pluridisciplinaire<\/h3>\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t<div class=\"elementor-element elementor-element-0464b6d e-flex e-con-boxed e-con e-parent\" data-id=\"0464b6d\" data-element_type=\"container\" data-e-type=\"container\" data-settings=\"{&quot;jet_parallax_layout_list&quot;:[]}\">\n\t\t\t\t\t<div class=\"e-con-inner\">\n\t\t\t\t<div class=\"elementor-element elementor-element-5679f6c elementor-widget elementor-widget-text-editor\" data-id=\"5679f6c\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<p>Pour assurer la prise en charge, l\u2019organisation des soins s\u2019effectue en consultations pluridisciplinaires. Elles sont r\u00e9alis\u00e9es dans des centres sp\u00e9cialis\u00e9s en pathologies neuromusculaires, o\u00f9 diff\u00e9rent\u2022es professionnel\u2022les de sant\u00e9 travaillent ensemble pour proposer un suivi global et personnalis\u00e9.<\/p><p><strong>Les sp\u00e9cialistes impliqu\u00e9\u2022es incluent g\u00e9n\u00e9ralement :<\/strong><\/p><ul><li><strong>M\u00e9decins neurologues :<\/strong> en charge du diagnostic, du suivi fonctionnel et de la coordination m\u00e9dicale.<\/li><li><strong>Chirurgien\u2022nes orthop\u00e9distes :<\/strong> pour pr\u00e9venir ou corriger les d\u00e9formations articulaires (scoliose, r\u00e9tractions).<\/li><li><strong>Pneumologues :<\/strong> pour surveiller la capacit\u00e9 respiratoire et interviennent en cas d\u2019insuffisance ventilatoire.<\/li><li><strong>Cardiologues : <\/strong>indispensables dans certaines dystrophies comme Duchenne, o\u00f9 le muscle cardiaque est touch\u00e9.<\/li><li><strong>Gastro-ent\u00e9rologues et nutritionnistes :<\/strong> pour s\u2019occuper des troubles de la d\u00e9glutition, de la digestion et de la gestion pond\u00e9rale.<\/li><li><strong><a href=\"https:\/\/orthopus.com\/fr\/professionnels-de-sante\/kine-pour-neuropathie\/\">Kin\u00e9sith\u00e9rapeutes<\/a>, <a href=\"https:\/\/orthopus.com\/fr\/ergotherapeute-neuromusculaire-une-assistance-indispensable\/\">ergoth\u00e9rapeutes<\/a>, psychomotricien\u2022nes et orthophonistes :<\/strong> pour soutenir la fonction motrice, l\u2019autonomie, et la communication.<\/li><\/ul><p>Cette prise en charge int\u00e9gr\u00e9e vise \u00e0 pr\u00e9venir les complications, favoriser la qualit\u00e9 de vie et soutenir psychologiquement les personnes concern\u00e9es et leurs familles.<\/p>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t<div class=\"elementor-element elementor-element-b2e65ab e-flex e-con-boxed e-con e-parent\" data-id=\"b2e65ab\" data-element_type=\"container\" data-e-type=\"container\" data-settings=\"{&quot;jet_parallax_layout_list&quot;:[]}\">\n\t\t\t\t\t<div class=\"e-con-inner\">\n\t\t\t\t<div class=\"elementor-element elementor-element-257d3a0 elementor-widget elementor-widget-spacer\" data-id=\"257d3a0\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"spacer.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t<div class=\"elementor-spacer\">\n\t\t\t<div class=\"elementor-spacer-inner\"><\/div>\n\t\t<\/div>\n\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t<div class=\"elementor-element elementor-element-f472626 e-flex e-con-boxed e-con e-parent\" data-id=\"f472626\" data-element_type=\"container\" data-e-type=\"container\" data-settings=\"{&quot;jet_parallax_layout_list&quot;:[]}\">\n\t\t\t\t\t<div class=\"e-con-inner\">\n\t\t\t\t<div class=\"elementor-element elementor-element-751d718 elementor-widget elementor-widget-heading\" data-id=\"751d718\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"heading.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t<h3 class=\"elementor-heading-title elementor-size-default\">Approche m\u00e9dicamenteuse et essais cliniques<\/h3>\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t<div class=\"elementor-element elementor-element-9f8e430 e-flex e-con-boxed e-con e-parent\" data-id=\"9f8e430\" data-element_type=\"container\" data-e-type=\"container\" data-settings=\"{&quot;jet_parallax_layout_list&quot;:[]}\">\n\t\t\t\t\t<div class=\"e-con-inner\">\n\t\t\t\t<div class=\"elementor-element elementor-element-eb4137f elementor-widget elementor-widget-text-editor\" data-id=\"eb4137f\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<p data-block-id=\"f6229a59-b54e-4dd5-b317-3dd60eb62c7b\" data-pm-slice=\"1 1 []\">Il n\u2019existe \u00e0 ce jour <strong>aucun traitement pouvant gu\u00e9rir les dystrophies musculaires<\/strong>. Plusieurs m\u00e9dicaments font ralentir l\u2019\u00e9volution de la maladie et contribuent \u00e0 pr\u00e9server la force musculaire plus longtemps.<\/p><p data-block-id=\"91818bb0-3199-4641-9259-35f8023d15d4\">Les plus utilis\u00e9s sont les <a href=\"https:\/\/www.msdmanuals.com\/fr\/accueil\/multimedia\/table\/cortico%C3%AFdes-utilisations-et-effets-secondaires\" target=\"_blank\" rel=\"noopener noreferrer nofollow\">corticost\u00e9ro\u00efdes<\/a>, comme la prednisone ou le deflazacort. Ils sont particuli\u00e8rement efficaces puisqu&#8217;ils permettent de prolonger la capacit\u00e9 de marche de plusieurs ann\u00e9es. Ils agissent en r\u00e9duisant l\u2019inflammation musculaire et en limitant la perte des fibres musculaires. Cependant, ils sont associ\u00e9s \u00e0 des effets secondaires importants (prise de poids, hypertension, fragilit\u00e9 osseuse) qui n\u00e9cessitent une surveillance attentive.<\/p><p data-block-id=\"6a6f18cd-825f-4634-accc-bc67c6ca0750\">D\u2019autres pistes th\u00e9rapeutiques sont actuellement en cours de d\u00e9veloppement :<\/p><ul data-block-id=\"cf6539a2-8579-4aea-a5e2-51f0df8060c1\"><li><p data-block-id=\"ca5dd490-c22b-4871-940b-703089d0bf74\"><strong>La th\u00e9rapie g\u00e9nique<\/strong>, qui vise \u00e0 ins\u00e9rer une copie saine du g\u00e8ne d\u00e9ficient dans les cellules musculaires.<\/p><\/li><li><p data-block-id=\"01779554-9132-47f7-8bdf-469dec330707\"><strong>La th\u00e9rapie antisens<\/strong>, comme le saut d\u2019exon, qui permet de contourner certaines mutations g\u00e9n\u00e9tiques.<\/p><\/li><li><p data-block-id=\"79513914-eb84-4c4c-b57b-25361e4d988b\"><strong>Les cellules souches musculaires<\/strong>, \u00e9tudi\u00e9es pour leur potentiel \u00e0 r\u00e9g\u00e9n\u00e9rer les fibres musculaires endommag\u00e9es.<\/p><\/li><\/ul><p data-block-id=\"3fd16a0f-0f42-42b2-8ead-abfec27038c6\">Ces avanc\u00e9es font l\u2019objet d\u2019essais cliniques en France et \u00e0 l\u2019\u00e9tranger. De nombreuses personnes y participent sur la base du volontariat, dans l\u2019espoir d\u2019acc\u00e9der plus rapidement \u00e0 de nouveaux traitements. L\u2019implication de structures comme l\u2019<a href=\"https:\/\/www.afm-telethon.fr\/fr\" target=\"_blank\" rel=\"noopener noreferrer nofollow\">AFM-T\u00e9l\u00e9thon<\/a> (association de militants, personnes concern\u00e9es par des maladies g\u00e9n\u00e9tiques et leur entourage, rares, \u00e9volutives et les maladies neuromusculaires) et l\u2019<a href=\"https:\/\/www.inserm.fr\/\" target=\"_blank\" rel=\"noopener noreferrer nofollow\">INSERM <\/a>(Institut National de la Sant\u00e9 et de la Recherche M\u00e9dicale) permet de gagner du temps dans la mise \u00e0 disposition de ces innovations.<\/p>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t<div class=\"elementor-element elementor-element-928a822 e-flex e-con-boxed e-con e-parent\" data-id=\"928a822\" data-element_type=\"container\" data-e-type=\"container\" data-settings=\"{&quot;jet_parallax_layout_list&quot;:[]}\">\n\t\t\t\t\t<div class=\"e-con-inner\">\n\t\t\t\t<div class=\"elementor-element elementor-element-d4b893a elementor-widget elementor-widget-spacer\" data-id=\"d4b893a\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"spacer.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t<div class=\"elementor-spacer\">\n\t\t\t<div class=\"elementor-spacer-inner\"><\/div>\n\t\t<\/div>\n\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t<div class=\"elementor-element elementor-element-0aceeda e-flex e-con-boxed e-con e-parent\" data-id=\"0aceeda\" data-element_type=\"container\" data-e-type=\"container\" data-settings=\"{&quot;jet_parallax_layout_list&quot;:[]}\">\n\t\t\t\t\t<div class=\"e-con-inner\">\n\t\t\t\t<div class=\"elementor-element elementor-element-9fcb4c9 elementor-widget elementor-widget-heading\" data-id=\"9fcb4c9\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"heading.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t<h3 class=\"elementor-heading-title elementor-size-default\">R\u00e9\u00e9ducation et dispositifs d\u2019assistance<\/h3>\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t<div class=\"elementor-element elementor-element-cddc048 e-flex e-con-boxed e-con e-parent\" data-id=\"cddc048\" data-element_type=\"container\" data-e-type=\"container\" data-settings=\"{&quot;jet_parallax_layout_list&quot;:[]}\">\n\t\t\t\t\t<div class=\"e-con-inner\">\n\t\t\t\t<div class=\"elementor-element elementor-element-e244a5d elementor-widget elementor-widget-text-editor\" data-id=\"e244a5d\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<p>La r\u00e9\u00e9ducation est la pierre angulaire de la prise en charge. <strong>Elle permet de maintenir les capacit\u00e9s fonctionnelles, d\u2019\u00e9viter les r\u00e9tractions musculaires et d\u2019am\u00e9liorer la posture.<\/strong> Elle est pratiqu\u00e9e par une \u00e9quipe pluridisciplinaire en collaboration avec la personne concern\u00e9e et ses proches.<\/p><p>La <a href=\"https:\/\/orthopus.com\/fr\/professionnels-de-sante\/kine-pour-neuropathie\/\"><strong>kin\u00e9sith\u00e9rapie<\/strong> <\/a>est effectu\u00e9e de mani\u00e8re r\u00e9guli\u00e8re et adapt\u00e9e \u00e0 chaque stade de la maladie. Elle comprend des exercices passifs, des \u00e9tirements et parfois l\u2019utilisation de machines pour mobiliser les membres sans effort.<\/p><p>Les <strong>orth\u00e8ses<\/strong> jouent \u00e9galement un r\u00f4le important. Elles soutiennent les articulations affaiblies, permettent de stabiliser certaines postures et d\u2019\u00e9viter les complications orthop\u00e9diques. Elles peuvent \u00eatre port\u00e9es la journ\u00e9e ou la nuit, selon les besoins.<\/p><p>Plusieurs types d\u2019orth\u00e8ses existent, en voici quelques-unes :<\/p>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t<div class=\"elementor-element elementor-element-01588ac e-flex e-con-boxed e-con e-parent\" data-id=\"01588ac\" data-element_type=\"container\" data-e-type=\"container\" data-settings=\"{&quot;jet_parallax_layout_list&quot;:[]}\">\n\t\t\t\t\t<div class=\"e-con-inner\">\n\t\t<div class=\"elementor-element elementor-element-ed209f1 e-con-full e-flex e-con e-child\" data-id=\"ed209f1\" data-element_type=\"container\" data-e-type=\"container\" data-settings=\"{&quot;jet_parallax_layout_list&quot;:[]}\">\n\t\t\t\t<div class=\"elementor-element elementor-element-a94726c elementor-widget elementor-widget-image\" data-id=\"a94726c\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"image.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t\t\t\t\t\t\t<img decoding=\"async\" width=\"1000\" height=\"1000\" src=\"https:\/\/orthopus.com\/wp-content\/uploads\/2025\/08\/orthese-dorsale-bauefeind.webp\" class=\"attachment-large size-large wp-image-17326\" alt=\"\" srcset=\"https:\/\/orthopus.com\/wp-content\/uploads\/2025\/08\/orthese-dorsale-bauefeind.webp 1000w, https:\/\/orthopus.com\/wp-content\/uploads\/2025\/08\/orthese-dorsale-bauefeind-300x300.webp 300w, https:\/\/orthopus.com\/wp-content\/uploads\/2025\/08\/orthese-dorsale-bauefeind-150x150.webp 150w, https:\/\/orthopus.com\/wp-content\/uploads\/2025\/08\/orthese-dorsale-bauefeind-768x768.webp 768w, https:\/\/orthopus.com\/wp-content\/uploads\/2025\/08\/orthese-dorsale-bauefeind-230x230.webp 230w, https:\/\/orthopus.com\/wp-content\/uploads\/2025\/08\/orthese-dorsale-bauefeind-400x400.webp 400w, https:\/\/orthopus.com\/wp-content\/uploads\/2025\/08\/orthese-dorsale-bauefeind-600x600.webp 600w, https:\/\/orthopus.com\/wp-content\/uploads\/2025\/08\/orthese-dorsale-bauefeind-640x640.webp 640w, https:\/\/orthopus.com\/wp-content\/uploads\/2025\/08\/orthese-dorsale-bauefeind-200x200.webp 200w\" sizes=\"(max-width: 1000px) 100vw, 1000px\" \/>\t\t\t\t\t\t\t\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t<div class=\"elementor-element elementor-element-ba61a64 e-con-full e-flex e-con e-child\" data-id=\"ba61a64\" data-element_type=\"container\" data-e-type=\"container\" data-settings=\"{&quot;jet_parallax_layout_list&quot;:[]}\">\n\t\t\t\t<div class=\"elementor-element elementor-element-bc86c0c elementor-widget elementor-widget-image\" data-id=\"bc86c0c\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"image.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t\t\t\t\t\t\t<img loading=\"lazy\" decoding=\"async\" width=\"1001\" height=\"1001\" src=\"https:\/\/orthopus.com\/wp-content\/uploads\/2025\/08\/orthese-dorsale.webp\" class=\"attachment-large size-large wp-image-17329\" alt=\"\" srcset=\"https:\/\/orthopus.com\/wp-content\/uploads\/2025\/08\/orthese-dorsale.webp 1001w, https:\/\/orthopus.com\/wp-content\/uploads\/2025\/08\/orthese-dorsale-300x300.webp 300w, https:\/\/orthopus.com\/wp-content\/uploads\/2025\/08\/orthese-dorsale-150x150.webp 150w, https:\/\/orthopus.com\/wp-content\/uploads\/2025\/08\/orthese-dorsale-768x768.webp 768w, https:\/\/orthopus.com\/wp-content\/uploads\/2025\/08\/orthese-dorsale-230x230.webp 230w, https:\/\/orthopus.com\/wp-content\/uploads\/2025\/08\/orthese-dorsale-400x400.webp 400w, https:\/\/orthopus.com\/wp-content\/uploads\/2025\/08\/orthese-dorsale-600x600.webp 600w, https:\/\/orthopus.com\/wp-content\/uploads\/2025\/08\/orthese-dorsale-640x640.webp 640w, https:\/\/orthopus.com\/wp-content\/uploads\/2025\/08\/orthese-dorsale-200x200.webp 200w\" sizes=\"(max-width: 1001px) 100vw, 1001px\" \/>\t\t\t\t\t\t\t\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t<div class=\"elementor-element elementor-element-db35cdc e-con-full e-flex e-con e-child\" data-id=\"db35cdc\" data-element_type=\"container\" data-e-type=\"container\" data-settings=\"{&quot;jet_parallax_layout_list&quot;:[]}\">\n\t\t\t\t<div class=\"elementor-element elementor-element-7cbd9b2 elementor-widget elementor-widget-text-editor\" data-id=\"7cbd9b2\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\tOrth\u00e8se dorsale\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t<div class=\"elementor-element elementor-element-bef4f18 e-con-full e-flex e-con e-child\" data-id=\"bef4f18\" data-element_type=\"container\" data-e-type=\"container\" data-settings=\"{&quot;jet_parallax_layout_list&quot;:[]}\">\n\t\t\t\t<div class=\"elementor-element elementor-element-20133da elementor-widget elementor-widget-text-editor\" data-id=\"20133da\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\tOrth\u00e8se d\u2019articulation de l\u2019\u00e9paule\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t<div class=\"elementor-element elementor-element-b259219 e-flex e-con-boxed e-con e-parent\" data-id=\"b259219\" data-element_type=\"container\" data-e-type=\"container\" data-settings=\"{&quot;jet_parallax_layout_list&quot;:[]}\">\n\t\t\t\t\t<div class=\"e-con-inner\">\n\t\t\t\t<div class=\"elementor-element elementor-element-c7c310d elementor-widget elementor-widget-text-editor\" data-id=\"c7c310d\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<p data-block-id=\"bb9032cf-5444-4189-abe5-7ae06a60b02f\" data-pm-slice=\"1 1 []\">Les technologies d\u2019assistance jouent \u00e9galement un r\u00f4le essentiel dans la vie des personnes atteintes de dystrophies musculaires. Elles permettent de compenser la perte de force et de mobilit\u00e9, tout en aidant chacun\u2022e \u00e0 garder un maximum d\u2019autonomie. Parmi ces solutions, on retrouve des dispositifs robotiques et des aides techniques con\u00e7us pour s\u2019adapter aux besoins du quotidien.<\/p><ul data-block-id=\"0517f21a-1b0c-4f29-8964-a1737653d3bd\"><li><p data-block-id=\"c33d9c5c-8111-4f0c-a9b6-dedaef98b977\">Les <a href=\"https:\/\/orthopus.com\/fr\/gamme-assistants-robotiques-pour-la-mobilite-du-bras\/\" target=\"_blank\" rel=\"noopener noreferrer nofollow\">bras robotis\u00e9s<\/a> peuvent saisir des objets.<\/p><\/li><li><p data-block-id=\"c8fd7b11-0411-45b5-83b7-39d44670d1ce\">Les supports de bras articul\u00e9s soulagent le poids du bras et facilitent les mouvements du quotidien, comme manger ou se coiffer.<\/p><\/li><li><p data-block-id=\"2db9044d-39bc-412d-a8a8-f928b10ec700\">Les <a href=\"https:\/\/orthopus.com\/fr\/aide-technique\/robot-assistance-compensation\/\">exosquelettes<\/a> passifs accompagnent le corps dans ses gestes sans avoir besoin d\u2019\u00e9nergie \u00e9lectrique. Ils all\u00e8gent les mouvements et laissent la personne actrice de ses actions.<\/p><\/li><\/ul><p data-block-id=\"2433383e-61bc-45e8-8588-8b5067be8bae\">Ces dispositifs ne remplacent pas les capacit\u00e9s humaines. Ils les soutiennent et les accompagnent dans une autonomie relative. C\u2019est gr\u00e2ce \u00e0 eux que de nombreuses personnes peuvent continuer \u00e0 vivre de fa\u00e7on plus autonome.<\/p><p data-block-id=\"209edcbd-6173-435b-902c-9df2f8355ab7\">Vivre avec une dystrophie musculaire, c\u2019est faire face \u00e0 de nombreux d\u00e9fis. Que ce soit pour les personnes elles-m\u00eames, mais aussi pour leurs proches et les soignant\u2022es. M\u00eame si ces maladies ne gu\u00e9rissent pas encore, les choses ont beaucoup \u00e9volu\u00e9. Gr\u00e2ce \u00e0 un suivi m\u00e9dical complet, aux progr\u00e8s comme la th\u00e9rapie g\u00e9nique et \u00e0 la technologie d\u2019assistance, on peut aujourd\u2019hui accompagner au mieux les personnes vivant avec des dystrophies musculaires.<\/p>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t<div class=\"elementor-element elementor-element-96fd740 e-flex e-con-boxed e-con e-parent\" data-id=\"96fd740\" data-element_type=\"container\" data-e-type=\"container\" data-settings=\"{&quot;jet_parallax_layout_list&quot;:[]}\">\n\t\t\t\t\t<div class=\"e-con-inner\">\n\t\t\t\t<div class=\"elementor-element elementor-element-04b4ca6 elementor-widget elementor-widget-html\" data-id=\"04b4ca6\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"html.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t<script type=\"application\/ld+json\">\r\n{\r\n  \"@context\": \"https:\/\/schema.org\",\r\n  \"@type\": 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une perte de force et une r\u00e9duction de l\u2019autonomie.\",\r\n    \"cause\": \"Anomalies g\u00e9n\u00e9tiques affectant la production ou la structure de prot\u00e9ines n\u00e9cessaires au bon fonctionnement musculaire.\",\r\n    \"symptoms\": [\r\n      \"Faiblesse musculaire progressive\",\r\n      \"Chutes fr\u00e9quentes\",\r\n      \"Crampes et douleurs musculaires\",\r\n      \"Troubles respiratoires\",\r\n      \"Complications cardiaques\"\r\n    ],\r\n    \"possibleTreatment\": [\r\n      \"Corticost\u00e9ro\u00efdes (prednisone, deflazacort)\",\r\n      \"Prise en charge pluridisciplinaire\",\r\n      \"R\u00e9\u00e9ducation fonctionnelle et kin\u00e9sith\u00e9rapie\",\r\n      \"Orth\u00e8ses et dispositifs d\u2019assistance (bras robotis\u00e9s, exosquelettes passifs)\",\r\n      \"Essais cliniques (th\u00e9rapie g\u00e9nique, saut d\u2019exon, cellules souches)\"\r\n    ]\r\n  },\r\n  \"about\": [\r\n    {\r\n      \"@type\": \"MedicalCondition\",\r\n      \"name\": \"Dystrophie musculaire de Duchenne\",\r\n      \"description\": \"Forme la plus s\u00e9v\u00e8re et pr\u00e9coce des dystrophies musculaires, li\u00e9e au chromosome X et touchant quasi exclusivement les gar\u00e7ons.\"\r\n    },\r\n    {\r\n      \"@type\": \"MedicalCondition\",\r\n      \"name\": \"Dystrophie musculaire de Becker\",\r\n      \"description\": \"Forme plus mod\u00e9r\u00e9e et lente que la dystrophie de Duchenne, certains patients conservent la marche \u00e0 l\u2019\u00e2ge adulte.\"\r\n    },\r\n    {\r\n      \"@type\": \"MedicalCondition\",\r\n      \"name\": \"Dystrophie facio-scapulo-hum\u00e9rale (FSH)\",\r\n      \"description\": \"Atteint principalement les muscles du visage, des omoplates et des bras. \u00c9volution lente et formes vari\u00e9es.\"\r\n    },\r\n    {\r\n      \"@type\": \"MedicalCondition\",\r\n      \"name\": \"Dystrophie myotonique\",\r\n      \"description\": \"Caract\u00e9ris\u00e9e par une difficult\u00e9 de rel\u00e2chement des muscles apr\u00e8s contraction (myotonie), associ\u00e9e \u00e0 des troubles cardiaques et respiratoires.\"\r\n    }\r\n  ],\r\n  \"publisher\": {\r\n    \"@type\": \"Organization\",\r\n    \"name\": \"Orthopus\",\r\n    \"url\": \"https:\/\/orthopus.com\/fr\/\"\r\n  },\r\n  \"author\": {\r\n    \"@type\": \"Person\",\r\n    \"name\": \"Pierre Murzeau\",\r\n    \"jobTitle\": \"Content manager\",\r\n    \"url\": \"https:\/\/orthopus.com\/fr\/equipage\/\"\r\n  }\r\n}\r\n<\/script>\r\n\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t<div class=\"elementor-element elementor-element-3f466dc elementor-widget elementor-widget-spacer\" data-id=\"3f466dc\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"spacer.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t<div class=\"elementor-spacer\">\n\t\t\t<div class=\"elementor-spacer-inner\"><\/div>\n\t\t<\/div>\n\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t<div class=\"elementor-element elementor-element-1c74b3b e-flex e-con-boxed e-con e-parent\" data-id=\"1c74b3b\" data-element_type=\"container\" data-e-type=\"container\" data-settings=\"{&quot;jet_parallax_layout_list&quot;:[]}\">\n\t\t\t\t\t<div class=\"e-con-inner\">\n\t\t\t\t<div class=\"elementor-element elementor-element-d9b401c elementor-widget elementor-widget-heading\" data-id=\"d9b401c\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"heading.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t<h2 class=\"elementor-heading-title elementor-size-default\">Sources : <\/h2>\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t<div class=\"elementor-element elementor-element-c2adb93 e-flex e-con-boxed e-con e-parent\" data-id=\"c2adb93\" data-element_type=\"container\" data-e-type=\"container\" data-settings=\"{&quot;jet_parallax_layout_list&quot;:[]}\">\n\t\t\t\t\t<div class=\"e-con-inner\">\n\t\t\t\t<div class=\"elementor-element elementor-element-31b5ab7 elementor-widget elementor-widget-text-editor\" data-id=\"31b5ab7\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<ol>\n  <li>Dystrophies musculaires cong\u00e9nitales | AFM T\u00e9l\u00e9thon [Internet]. 2024 [cit\u00e9 5 mai 2025]. Disponible sur: <a href=\"https:\/\/www.afm-telethon.fr\/fr\/fiches-maladies\/dystrophies-musculaires-congenitales\" rel=\"nofollow\">https:\/\/www.afm-telethon.fr\/fr\/fiches-maladies\/dystrophies-musculaires-congenitales<\/a><\/li>\n  <li>Inserm [Internet]. [cit\u00e9 2 mai 2025]. Myopathie de Duchenne \u00b7 Inserm, La science pour la sant\u00e9. Disponible sur: <a href=\"https:\/\/www.inserm.fr\/dossier\/myopathie-duchenne\/\" rel=\"nofollow\">https:\/\/www.inserm.fr\/dossier\/myopathie-duchenne\/<\/a><\/li>\n  <li>Qu\u2019est-ce que la dystrophie musculaire \u2013 Dystrophie Musculaire Canada [Internet]. [cit\u00e9 5 mai 2025]. Disponible sur: <a href=\"https:\/\/muscle.ca\/fr\/decouvrir-la-dystrophie-musculaire\/quest-ce-que-la-dystrophie-musculaire\/\" rel=\"nofollow\">https:\/\/muscle.ca\/fr\/decouvrir-la-dystrophie-musculaire\/quest-ce-que-la-dystrophie-musculaire\/<\/a><\/li>\n  <li>DMDB G. Groupe d\u2019Int\u00e9r\u00eat DMDB de l\u2019AFM-T\u00e9l\u00e9thon. 2020 [cit\u00e9 2 mai 2025]. La Dystrophie Musculaire de Becker. Disponible sur: <a href=\"https:\/\/dmdb.afm-telethon.fr\/la-dystrophie-musculaire-de-becker\/\" rel=\"nofollow\">https:\/\/dmdb.afm-telethon.fr\/la-dystrophie-musculaire-de-becker\/<\/a><\/li>\n  <li>Protocole National de Diagnostic et de Soins, (PNDS). Dystrophie musculaire de Duchenne [Internet]. Disponible sur: <a href=\"https:\/\/www.has-sante.fr\/upload\/docs\/application\/pdf\/2019-11\/pnds_duchenne_raccourci_18_pages_final_nov_2019_.pdf\" rel=\"nofollow\">https:\/\/www.has-sante.fr\/upload\/docs\/application\/pdf\/2019-11\/pnds_duchenne_raccourci_18_pages_final_nov_2019_.pdf<\/a><\/li>\n  <li>Myopathie de Duchenne [Internet]. G\u00e9n\u00e9thon. [cit\u00e9 2 mai 2025]. Disponible sur: <a href=\"https:\/\/www.genethon.fr\/notre-pipeline\/myopathie-de-duchenne\/\" rel=\"nofollow\">https:\/\/www.genethon.fr\/notre-pipeline\/myopathie-de-duchenne\/<\/a><\/li>\n  <li>Orphanet: Dystrophie musculaire de Duchenne et Becker [Internet]. [cit\u00e9 2 mai 2025]. Disponible sur: <a href=\"http:\/\/www.orpha.net\/fr\/disease\/detail\/262\" rel=\"nofollow\">http:\/\/www.orpha.net\/fr\/disease\/detail\/262<\/a><\/li>\n  <li>Dystrophie musculaire de Duchenne | AFM T\u00e9l\u00e9thon [Internet]. 2024 [cit\u00e9 2 mai 2025]. Disponible sur: <a href=\"https:\/\/www.afm-telethon.fr\/fr\/fiches-maladies\/dystrophie-musculaire-de-duchenne\" rel=\"nofollow\">https:\/\/www.afm-telethon.fr\/fr\/fiches-maladies\/dystrophie-musculaire-de-duchenne<\/a><\/li>\n  <li>Dystrophie musculaire de Becker | AFM T\u00e9l\u00e9thon [Internet]. 2024 [cit\u00e9 2 mai 2025]. Disponible sur: <a href=\"https:\/\/www.afm-telethon.fr\/fr\/fiches-maladies\/dystrophie-musculaire-de-becker\" rel=\"nofollow\">https:\/\/www.afm-telethon.fr\/fr\/fiches-maladies\/dystrophie-musculaire-de-becker<\/a><\/li>\n  <li>Maladie de Steinert | AFM T\u00e9l\u00e9thon [Internet]. 2020 [cit\u00e9 2 mai 2025]. Disponible sur: <a href=\"https:\/\/www.afm-telethon.fr\/fr\/fiches-maladies\/maladie-de-steinert\" rel=\"nofollow\">https:\/\/www.afm-telethon.fr\/fr\/fiches-maladies\/maladie-de-steinert<\/a><\/li>\n  <li>Manuels MSD pour le grand public [Internet]. [cit\u00e9 5 mai 2025]. Dystrophie musculaire de Duchenne et dystrophie musculaire de Becker &#8211; Probl\u00e8mes de sant\u00e9 infantiles. Disponible sur: <a href=\"https:\/\/www.msdmanuals.com\/fr\/accueil\/probl\u00e8mes-de-sant\u00e9-infantiles\/dystrophies-musculaires-et-troubles-associ\u00e9s\/dystrophie-musculaire-de-duchenne-et-dystrophie-musculaire-de-becker\" rel=\"nofollow\">https:\/\/www.msdmanuals.com\/fr\/accueil\/probl\u00e8mes-de-sant\u00e9-infantiles\/dystrophies-musculaires-et-troubles-associ\u00e9s\/dystrophie-musculaire-de-duchenne-et-dystrophie-musculaire-de-becker<\/a><\/li>\n  <li>Myopathie facio-scapulo-hum\u00e9rale | AFM T\u00e9l\u00e9thon [Internet]. 2024 [cit\u00e9 2 mai 2025]. Disponible sur: <a href=\"https:\/\/www.afm-telethon.fr\/fr\/fiches-maladies\/myopathie-facio-scapulo-humerale\" rel=\"nofollow\">https:\/\/www.afm-telethon.fr\/fr\/fiches-maladies\/myopathie-facio-scapulo-humerale<\/a><\/li>\n  <li>Manuels MSD pour le grand public [Internet]. [cit\u00e9 5 mai 2025]. Dystrophie des ceintures &#8211; Probl\u00e8mes de sant\u00e9 infantiles. Disponible sur: <a href=\"https:\/\/www.msdmanuals.com\/fr\/accueil\/probl\u00e8mes-de-sant\u00e9-infantiles\/dystrophies-musculaires-et-troubles-associ\u00e9s\/dystrophie-des-ceintures\" rel=\"nofollow\">https:\/\/www.msdmanuals.com\/fr\/accueil\/probl\u00e8mes-de-sant\u00e9-infantiles\/dystrophies-musculaires-et-troubles-associ\u00e9s\/dystrophie-des-ceintures<\/a><\/li>\n  <li>Manuels MSD pour le grand public [Internet]. [cit\u00e9 2 mai 2025]. Table:Cortico\u00efdes\u202f: Utilisations et effets secondaires. Disponible sur: <a href=\"https:\/\/www.msdmanuals.com\/fr\/accueil\/multimedia\/table\/cortico\u00efdes-utilisations-et-effets-secondaires\" rel=\"nofollow\">https:\/\/www.msdmanuals.com\/fr\/accueil\/multimedia\/table\/cortico\u00efdes-utilisations-et-effets-secondaires<\/a><\/li>\n  <li>Th\u00e9rapie g\u00e9nique | AFM T\u00e9l\u00e9thon [Internet]. 2024 [cit\u00e9 2 mai 2025]. Disponible sur: <a href=\"https:\/\/www.afm-telethon.fr\/fr\/termes\/therapie-genique\" rel=\"nofollow\">https:\/\/www.afm-telethon.fr\/fr\/termes\/therapie-genique<\/a><\/li>\n  <li>Th\u00e9rapie antisens. In: Wikip\u00e9dia [Internet]. 2025 [cit\u00e9 5 mai 2025]. Disponible sur: <a href=\"https:\/\/fr.wikipedia.org\/w\/index.php?title=Th%C3%A9rapie_antisens&amp;oldid=221839535\" rel=\"nofollow\">https:\/\/fr.wikipedia.org\/w\/index.php?title=Th%C3%A9rapie_antisens&amp;oldid=221839535<\/a><\/li>\n  <li>Goyenvalle A, Vulin A, Fougerousse F, Leturcq F, Kaplan JC, Garcia L, et al. Le saut d\u2019exon th\u00e9rapeutique\u202f: un espoir pour les dystrophinopathies. m\u00e9decine\/sciences. 1 d\u00e9c 2004;20(12):1163\u20115. <a href=\"https:\/\/www.researchgate.net\/publication\/238082244_Le_saut_d'exon_therapeutique_un_espoir_pour_les_dystrophinopathies\" rel=\"nofollow\">https:\/\/www.researchgate.net\/publication\/238082244_Le_saut_d&#8217;exon_therapeutique_un_espoir_pour_les_dystrophinopathies<\/a><\/li>\n  <li>Pann\u00e9rec A, Sassoon D. Identification d\u2019une nouvelle population de cellules souches musculaires. m\u00e9decine\/sciences. 1 oct 2010;26(10):797\u2011800. <a href=\"https:\/\/www.medecinesciences.org\/en\/articles\/medsci\/full_html\/2010\/09\/medsci20102610p797\/medsci20102610p797.html\" rel=\"nofollow\">https:\/\/www.medecinesciences.org\/en\/articles\/medsci\/full_html\/2010\/09\/medsci20102610p797\/medsci20102610p797.html<\/a><\/li>\n<\/ol>\n\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t","protected":false},"excerpt":{"rendered":"<p>Dystrophies musculaires : d\u00e9finition et solutions pour am\u00e9liorer le quotidien Les dystrophies musculaires repr\u00e9sentent un ensemble de maladies g\u00e9n\u00e9tiques rares qui \u00e9voluent avec le temps. Dans la plupart des cas, elles sont souvent h\u00e9r\u00e9ditaires et atteignent les muscles squelettiques. Ce sont ceux que l\u2019on contr\u00f4le pour bouger, parler ou respirer. Ces maladies provoquent une d\u00e9t\u00e9rioration [&hellip;]<\/p>\n","protected":false},"author":15,"featured_media":0,"parent":17468,"menu_order":0,"comment_status":"closed","ping_status":"closed","template":"","meta":{"_jet_sm_ready_style":"","_jet_sm_style":"","_jet_sm_controls_values":"","_jet_sm_fonts_collection":"","_jet_sm_fonts_links":"","footnotes":""},"class_list":["post-17304","page","type-page","status-publish","hentry"],"yoast_head":"<!-- This site is optimized with the Yoast SEO plugin v27.4 - https:\/\/yoast.com\/product\/yoast-seo-wordpress\/ -->\n<title>Dystrophies musculaires : Traitement et Technologie<\/title>\n<meta name=\"description\" content=\"D\u00e9couvrez comment la technologie am\u00e9liore la vie des personnes atteintes de dystrophies musculaires gr\u00e2ce aux solutions robotiques avanc\u00e9es.\" \/>\n<meta name=\"robots\" content=\"index, follow, max-snippet:-1, max-image-preview:large, max-video-preview:-1\" \/>\n<link rel=\"canonical\" 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