{"id":17263,"date":"2025-08-25T16:34:11","date_gmt":"2025-08-25T14:34:11","guid":{"rendered":"https:\/\/orthopus.com\/?page_id=17263"},"modified":"2025-09-01T16:39:54","modified_gmt":"2025-09-01T14:39:54","slug":"dystrophie-musculaire-de-becker","status":"publish","type":"page","link":"https:\/\/orthopus.com\/fr\/maladies-neuromusculaires\/dystrophie-musculaire-de-becker\/","title":{"rendered":"Dystrophie musculaire de Becker &#8211; Traitements et Aide"},"content":{"rendered":"\t\t<div data-elementor-type=\"wp-page\" data-elementor-id=\"17263\" class=\"elementor elementor-17263\" data-elementor-post-type=\"page\">\n\t\t\t\t<div class=\"elementor-element elementor-element-0ce4b7f e-flex e-con-boxed e-con e-parent\" data-id=\"0ce4b7f\" data-element_type=\"container\" data-e-type=\"container\" data-settings=\"{&quot;jet_parallax_layout_list&quot;:[]}\">\n\t\t\t\t\t<div class=\"e-con-inner\">\n\t\t\t\t<div class=\"elementor-element elementor-element-4eebc39 elementor-widget elementor-widget-heading\" data-id=\"4eebc39\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"heading.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t<h1 class=\"elementor-heading-title elementor-size-default\">Dystrophie musculaire de Becker : comprendre, traiter et vivre avec la maladie<\/h1>\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t<div class=\"elementor-element elementor-element-f6a3e69 e-flex e-con-boxed e-con e-parent\" data-id=\"f6a3e69\" data-element_type=\"container\" data-e-type=\"container\" data-settings=\"{&quot;jet_parallax_layout_list&quot;:[]}\">\n\t\t\t\t\t<div class=\"e-con-inner\">\n\t\t\t\t<div class=\"elementor-element elementor-element-6c6ba62 elementor-widget elementor-widget-image\" data-id=\"6c6ba62\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"image.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t\t\t\t\t\t\t<img fetchpriority=\"high\" decoding=\"async\" width=\"800\" height=\"533\" src=\"https:\/\/orthopus.com\/wp-content\/uploads\/2025\/08\/orthopus-dystrophie-musculaire-de-duchenne.jpg\" class=\"attachment-full size-full wp-image-17402\" alt=\"\" srcset=\"https:\/\/orthopus.com\/wp-content\/uploads\/2025\/08\/orthopus-dystrophie-musculaire-de-duchenne.jpg 800w, https:\/\/orthopus.com\/wp-content\/uploads\/2025\/08\/orthopus-dystrophie-musculaire-de-duchenne-300x200.jpg 300w, https:\/\/orthopus.com\/wp-content\/uploads\/2025\/08\/orthopus-dystrophie-musculaire-de-duchenne-768x512.jpg 768w, https:\/\/orthopus.com\/wp-content\/uploads\/2025\/08\/orthopus-dystrophie-musculaire-de-duchenne-600x400.jpg 600w, https:\/\/orthopus.com\/wp-content\/uploads\/2025\/08\/orthopus-dystrophie-musculaire-de-duchenne-200x133.jpg 200w\" sizes=\"(max-width: 800px) 100vw, 800px\" \/>\t\t\t\t\t\t\t\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t<div class=\"elementor-element elementor-element-d86421b e-flex e-con-boxed e-con e-parent\" data-id=\"d86421b\" data-element_type=\"container\" data-e-type=\"container\" data-settings=\"{&quot;jet_parallax_layout_list&quot;:[]}\">\n\t\t\t\t\t<div class=\"e-con-inner\">\n\t\t\t\t<div class=\"elementor-element elementor-element-94ed8cb elementor-widget elementor-widget-text-editor\" data-id=\"94ed8cb\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<p data-block-id=\"00626b3d-0d22-411d-ad12-c78d16c897c2\" data-pm-slice=\"1 1 []\">La dystrophie musculaire de Becker (DMB) est une maladie g\u00e9n\u00e9tique rare touchant le plus souvent les muscles squelettiques et le c\u0153ur. Cette pathologie provoque une faiblesse musculaire progressive. Elle entra\u00eene ainsi une diminution de l\u2019autonomie et de la capacit\u00e9 \u00e0 se mouvoir. Les personnes touch\u00e9es ont alors un besoin d\u2019assistance technique ou m\u00e9dicale.<\/p><p data-block-id=\"962a67ce-f361-4e5d-8287-6e39aa4a8619\">La dystrophie musculaire de Becker est li\u00e9e \u00e0 une mutation de l\u2019ADN du g\u00e8ne DMD, responsable de la production d\u2019une prot\u00e9ine appel\u00e9e dystrophine. Des parties de la s\u00e9quence d&#8217;ADN du g\u00e8ne, appel\u00e9s nucl\u00e9otides, vont \u00eatre modifi\u00e9es. Cela va entra\u00eener une modification des s\u00e9quences codantes de l&#8217;ADN \u2014 appel\u00e9es exon. Le processus permettant de lire l&#8217;ADN et de synth\u00e9tiser la prot\u00e9ine ne reconnait plus certaines s\u00e9quences n\u00e9cessaires \u00e0 la production de la dystrophine. Dans le cas de la dystrophie de Becker, une version partiellement fonctionnelle de cette prot\u00e9ine est produite. Cela explique une progression plus lente que dans <a href=\"https:\/\/orthopus.com\/fr\/maladies-neuromusculaires\/dystrophie-musculaire-de-duchenne\/\">la dystrophie de Duchenne<\/a>, une forme plus grave de myopathie.<\/p><p data-block-id=\"efa22134-8f1e-4188-91c3-33167bc30a4e\">Les sympt\u00f4mes varient d&#8217;une personne \u00e0 l&#8217;autre. Toutefois, la DMB n\u00e9cessite une prise en charge multidisciplinaire. Cette derni\u00e8re va des traitements m\u00e9dicamenteux \u00e0 des solutions technologiques. Vivre avec cette pathologie, c&#8217;est aussi apprendre \u00e0 anticiper les besoins, \u00e0 s&#8217;adapter et \u00e0 s&#8217;appuyer sur les nombreuses solutions aujourd&#8217;hui disponibles.<\/p>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t<div class=\"elementor-element elementor-element-6896c65 e-flex e-con-boxed e-con e-parent\" data-id=\"6896c65\" data-element_type=\"container\" data-e-type=\"container\" data-settings=\"{&quot;jet_parallax_layout_list&quot;:[]}\">\n\t\t\t\t\t<div class=\"e-con-inner\">\n\t\t\t\t<div class=\"elementor-element elementor-element-9f368e7 elementor-widget elementor-widget-spacer\" data-id=\"9f368e7\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"spacer.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t<div class=\"elementor-spacer\">\n\t\t\t<div class=\"elementor-spacer-inner\"><\/div>\n\t\t<\/div>\n\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t<div class=\"elementor-element elementor-element-ba9f73a e-flex e-con-boxed e-con e-parent\" data-id=\"ba9f73a\" data-element_type=\"container\" data-e-type=\"container\" data-settings=\"{&quot;jet_parallax_layout_list&quot;:[]}\">\n\t\t\t\t\t<div class=\"e-con-inner\">\n\t\t\t\t<div class=\"elementor-element elementor-element-d145348 elementor-widget elementor-widget-heading\" data-id=\"d145348\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"heading.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t<h2 class=\"elementor-heading-title elementor-size-default\">Qu\u2019est-ce que la dystrophie musculaire de Becker ?<\/h2>\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t<div class=\"elementor-element elementor-element-384fa3b e-flex e-con-boxed e-con e-parent\" data-id=\"384fa3b\" data-element_type=\"container\" data-e-type=\"container\" data-settings=\"{&quot;jet_parallax_layout_list&quot;:[]}\">\n\t\t\t\t\t<div class=\"e-con-inner\">\n\t\t\t\t<div class=\"elementor-element elementor-element-aad9be0 elementor-widget elementor-widget-text-editor\" data-id=\"aad9be0\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<p data-block-id=\"f4e5b369-f9d1-4241-a1e8-42ad1a849a90\" data-pm-slice=\"1 1 []\">La dystrophie musculaire de Becker est une <strong><a href=\"https:\/\/orthopus.com\/fr\/maladies-neuromusculaires\/\">maladie neuromusculaire<\/a> g\u00e9n\u00e9tique rare qui touche environ 1 gar\u00e7on sur 18000 \u00e0 30000 naissances<\/strong>. Elle appartient au groupe des dystrophies musculaires dues \u00e0 une anomalie du g\u00e8ne DMD <strong>localis\u00e9 sur le chromosome X<\/strong>.<\/p><p data-block-id=\"7f56ea43-7b15-4c59-900d-f392d0653930\">La dystrophine est une prot\u00e9ine structurale qui maintient la stabilit\u00e9 des cellules musculaires. Elle voit alors sa structure ou sa quantit\u00e9 modifi\u00e9e.<\/p><p data-block-id=\"6ffe0be9-36cb-4f2d-a689-93c9065b68b9\">Ce g\u00e8ne produit pour la dystrophine, une prot\u00e9ine structurale qui maintient la stabilit\u00e9 des cellules musculaires. En cas de DMB, <strong>une forme tronqu\u00e9e mais encore partiellement fonctionnelle de cette prot\u00e9ine est produite<\/strong>. <a href=\"https:\/\/orthopus.com\/fr\/maladies-neuromusculaires\/dystrophie-musculaire-de-duchenne\/\">La Dystrophie musculaire de Duchenne<\/a>, quant \u00e0 elle, ne produit \u00e9galement pas ou peu de dystrophine. Les deux sont ce que l\u2019on appelle des <strong>dystrophinopathies<\/strong>.<\/p><p data-block-id=\"5dc39121-3f37-4983-a740-0d17b976fdf0\">Cette <strong>pathologie est transmise selon un mode r\u00e9cessif li\u00e9 au sexe<\/strong>, c\u2019est-\u00e0-dire qu\u2019il faut deux copies du g\u00e8ne pour que la maladie s\u2019exprime. Les femmes peuvent \u00eatre porteuses sans pr\u00e9senter de sympt\u00f4mes, car elles ne poss\u00e8dent qu\u2019un chromosome X et le chromosome Y est souvent dominant. \u00c0 l\u2019inverse, les gar\u00e7ons d\u00e9veloppent la maladie s\u2019ils h\u00e9ritent des chromosomes X mut\u00e9s.<\/p><p data-block-id=\"3ccc479b-bcc6-4184-b2f3-228fe57c10b4\"><strong>Le d\u00e9but des sympt\u00f4mes est variable :<\/strong> g\u00e9n\u00e9ralement entre 5 et 15 ans. Certains cas peuvent appara\u00eetre plus tard, \u00e0 l\u2019\u00e2ge adulte, ce qui peut rendre le diagnostic parfois difficile.<\/p><p data-block-id=\"af40b265-6eb4-4e04-b272-40450fc934a6\">L\u2019\u00e9volution de la maladie est lente mais continue. Au contraire, l&#8217;\u00e9volution de la <a href=\"https:\/\/orthopus.com\/fr\/maladies-neuromusculaires\/dystrophie-musculaire-de-duchenne\/\">dystrophie musculaire de Duchenne<\/a>, est beaucoup plus rapide. Tout d\u2019abord, <strong>les muscles du bassin et des membres inf\u00e9rieurs sont affect\u00e9s, puis ils sont suivis progressivement par d\u2019autres groupes musculaires<\/strong>. Le c\u0153ur est \u00e9galement concern\u00e9, ce qui peut entra\u00eener des complications cardiaques \u00e0 surveiller.<\/p>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t<div class=\"elementor-element elementor-element-01b2276 e-flex e-con-boxed e-con e-parent\" data-id=\"01b2276\" data-element_type=\"container\" data-e-type=\"container\" data-settings=\"{&quot;jet_parallax_layout_list&quot;:[]}\">\n\t\t\t\t\t<div class=\"e-con-inner\">\n\t\t\t\t<div class=\"elementor-element elementor-element-1fb58c3 elementor-widget elementor-widget-image\" data-id=\"1fb58c3\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"image.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t\t\t\t\t\t\t<img decoding=\"async\" width=\"800\" height=\"450\" src=\"https:\/\/orthopus.com\/wp-content\/uploads\/2025\/08\/Schema-dystrophies.jpg\" class=\"attachment-full size-full wp-image-17404\" alt=\"\" srcset=\"https:\/\/orthopus.com\/wp-content\/uploads\/2025\/08\/Schema-dystrophies.jpg 800w, https:\/\/orthopus.com\/wp-content\/uploads\/2025\/08\/Schema-dystrophies-300x169.jpg 300w, https:\/\/orthopus.com\/wp-content\/uploads\/2025\/08\/Schema-dystrophies-768x432.jpg 768w, https:\/\/orthopus.com\/wp-content\/uploads\/2025\/08\/Schema-dystrophies-150x85.jpg 150w, https:\/\/orthopus.com\/wp-content\/uploads\/2025\/08\/Schema-dystrophies-600x338.jpg 600w, https:\/\/orthopus.com\/wp-content\/uploads\/2025\/08\/Schema-dystrophies-200x113.jpg 200w\" sizes=\"(max-width: 800px) 100vw, 800px\" \/>\t\t\t\t\t\t\t\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t<div class=\"elementor-element elementor-element-9d1c1d1 e-flex e-con-boxed e-con e-parent\" data-id=\"9d1c1d1\" data-element_type=\"container\" data-e-type=\"container\" data-settings=\"{&quot;jet_parallax_layout_list&quot;:[]}\">\n\t\t\t\t\t<div class=\"e-con-inner\">\n\t\t\t\t<div class=\"elementor-element elementor-element-9dae209 elementor-widget elementor-widget-text-editor\" data-id=\"9dae209\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<p><em>Sch\u00e9ma explicatif comparant une cellule musculaire saine, une cellule atteinte de DMD et une cellule atteinte de DMB.<\/em><\/p>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t<div class=\"elementor-element elementor-element-4b26265 e-flex e-con-boxed e-con e-parent\" data-id=\"4b26265\" data-element_type=\"container\" data-e-type=\"container\" data-settings=\"{&quot;jet_parallax_layout_list&quot;:[]}\">\n\t\t\t\t\t<div class=\"e-con-inner\">\n\t\t\t\t<div class=\"elementor-element elementor-element-069e157 elementor-widget elementor-widget-text-editor\" data-id=\"069e157\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<p data-block-id=\"84c42f90-668f-4ed0-88d2-aa08fadad05b\" data-pm-slice=\"1 1 []\">La production de dystrophine est impossible \u00e0 cause de la mutation g\u00e9n\u00e9tique chez les personnes touch\u00e9es par la pathologie. Cela fragilise la membrane musculaire et provoque des d\u00e9g\u00e2ts plus importants \u00e0 chaque mouvement. Dans ce cas, la dystrophine est produite, mais en faible quantit\u00e9 ou de fa\u00e7on tronqu\u00e9e. Cela permet de maintenir la membrane musculaire partiellement intacte.<\/p>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t<div class=\"elementor-element elementor-element-f0b06cb e-flex e-con-boxed e-con e-parent\" data-id=\"f0b06cb\" data-element_type=\"container\" data-e-type=\"container\" data-settings=\"{&quot;jet_parallax_layout_list&quot;:[]}\">\n\t\t\t\t\t<div class=\"e-con-inner\">\n\t\t\t\t<div class=\"elementor-element elementor-element-aa2c698 elementor-widget elementor-widget-spacer\" data-id=\"aa2c698\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"spacer.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t<div class=\"elementor-spacer\">\n\t\t\t<div class=\"elementor-spacer-inner\"><\/div>\n\t\t<\/div>\n\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t<div class=\"elementor-element elementor-element-6b92e0a e-flex e-con-boxed e-con e-parent\" data-id=\"6b92e0a\" data-element_type=\"container\" data-e-type=\"container\" data-settings=\"{&quot;jet_parallax_layout_list&quot;:[]}\">\n\t\t\t\t\t<div class=\"e-con-inner\">\n\t\t\t\t<div class=\"elementor-element elementor-element-b8e83b5 elementor-widget elementor-widget-heading\" data-id=\"b8e83b5\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"heading.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t<h2 class=\"elementor-heading-title elementor-size-default\">Quels sont les sympt\u00f4mes et l\u2019\u00e9volution de la dystrophie musculaire de Becker ?<\/h2>\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t<div class=\"elementor-element elementor-element-5449255 e-flex e-con-boxed e-con e-parent\" data-id=\"5449255\" data-element_type=\"container\" data-e-type=\"container\" data-settings=\"{&quot;jet_parallax_layout_list&quot;:[]}\">\n\t\t\t\t\t<div class=\"e-con-inner\">\n\t\t<div class=\"elementor-element elementor-element-9eeb036 e-con-full e-flex e-con e-child\" data-id=\"9eeb036\" data-element_type=\"container\" data-e-type=\"container\" data-settings=\"{&quot;jet_parallax_layout_list&quot;:[]}\">\n\t\t\t\t<div class=\"elementor-element elementor-element-e24b1a9 elementor-widget elementor-widget-html\" data-id=\"e24b1a9\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"html.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t<blockquote class=\"tiktok-embed\" cite=\"https:\/\/www.tiktok.com\/@medecinsconnaisseurs\/video\/7264365188063841538\" data-video-id=\"7264365188063841538\" style=\"max-width: 605px;min-width: 325px;\" > <section> <a target=\"_blank\" title=\"@medecinsconnaisseurs\" href=\"https:\/\/www.tiktok.com\/@medecinsconnaisseurs?refer=embed\">@medecinsconnaisseurs<\/a> \ud83c\udfa5 Une vid\u00e9o sp\u00e9ciale sur la Dystrophie Musculaire de Becker vous attend ! \ud83d\udcaa\ud83d\udc99 Tags: <a title=\"medicalstudents\" target=\"_blank\" href=\"https:\/\/www.tiktok.com\/tag\/medicalstudents?refer=embed\">#medicalstudents<\/a> <a title=\"selfcare\" target=\"_blank\" href=\"https:\/\/www.tiktok.com\/tag\/selfcare?refer=embed\">#selfcare<\/a> <a title=\"lifestyle\" target=\"_blank\" href=\"https:\/\/www.tiktok.com\/tag\/lifestyle?refer=embed\">#lifestyle<\/a> <a title=\"healthy\" target=\"_blank\" href=\"https:\/\/www.tiktok.com\/tag\/healthy?refer=embed\">#healthy<\/a> <a title=\"etudiant\" target=\"_blank\" href=\"https:\/\/www.tiktok.com\/tag\/etudiant?refer=embed\">#etudiant<\/a> <a title=\"students\" target=\"_blank\" href=\"https:\/\/www.tiktok.com\/tag\/students?refer=embed\">#students<\/a> <a title=\"vlog\" target=\"_blank\" href=\"https:\/\/www.tiktok.com\/tag\/vlog?refer=embed\">#vlog<\/a> <a title=\"university\" target=\"_blank\" href=\"https:\/\/www.tiktok.com\/tag\/university?refer=embed\">#university<\/a> <a title=\"medco\" target=\"_blank\" href=\"https:\/\/www.tiktok.com\/tag\/medco?refer=embed\">#medco<\/a> <a title=\"hospital\" target=\"_blank\" href=\"https:\/\/www.tiktok.com\/tag\/hospital?refer=embed\">#hospital<\/a> <a title=\"medstudent\" target=\"_blank\" href=\"https:\/\/www.tiktok.com\/tag\/medstudent?refer=embed\">#medstudent<\/a> <a title=\"sensibilisation\" target=\"_blank\" href=\"https:\/\/www.tiktok.com\/tag\/sensibilisation?refer=embed\">#Sensibilisation<\/a> <a title=\"comprendreetsoutenir\" target=\"_blank\" href=\"https:\/\/www.tiktok.com\/tag\/comprendreetsoutenir?refer=embed\">#ComprendreEtSoutenir<\/a> <a title=\"viral\" target=\"_blank\" href=\"https:\/\/www.tiktok.com\/tag\/viral?refer=embed\">#viral<\/a> <a title=\"foryou\" target=\"_blank\" href=\"https:\/\/www.tiktok.com\/tag\/foryou?refer=embed\">#foryou<\/a> <a title=\"sensibilisation\" target=\"_blank\" href=\"https:\/\/www.tiktok.com\/tag\/sensibilisation?refer=embed\">#Sensibilisation<\/a> <a title=\"solidarit\u00e9\" target=\"_blank\" href=\"https:\/\/www.tiktok.com\/tag\/solidarit%C3%A9?refer=embed\">#Solidarit\u00e9<\/a> <a title=\"dystrophiemusculairedebecker\" target=\"_blank\" href=\"https:\/\/www.tiktok.com\/tag\/dystrophiemusculairedebecker?refer=embed\">#DystrophieMusculaireDeBecker<\/a> <a title=\"espoir\" target=\"_blank\" href=\"https:\/\/www.tiktok.com\/tag\/espoir?refer=embed\">#Espoir<\/a> <a title=\"foryou\" target=\"_blank\" href=\"https:\/\/www.tiktok.com\/tag\/foryou?refer=embed\">#foryou<\/a> <a title=\"pourtoi\" target=\"_blank\" href=\"https:\/\/www.tiktok.com\/tag\/pourtoi?refer=embed\">#pourtoi<\/a> <a target=\"_blank\" title=\"\u266c All Eyes On Me - Instrumental - Dj Belite\" href=\"https:\/\/www.tiktok.com\/music\/All-Eyes-On-Me-Instrumental-7182781797455890434?refer=embed\">\u266c All Eyes On Me - Instrumental - Dj Belite<\/a> <\/section> <\/blockquote> <script async src=\"https:\/\/www.tiktok.com\/embed.js\"><\/script>\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t<div class=\"elementor-element elementor-element-9994b80 e-con-full e-flex e-con e-child\" data-id=\"9994b80\" data-element_type=\"container\" data-e-type=\"container\" data-settings=\"{&quot;jet_parallax_layout_list&quot;:[]}\">\n\t\t\t\t<div class=\"elementor-element elementor-element-d30b7a0 elementor-widget elementor-widget-text-editor\" data-id=\"d30b7a0\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<p>Les premiers signes de la DMB sont souvent peu sp\u00e9cifiques. Les parents ou enseignants peuvent remarquer que l\u2019enfant se fatigue rapidement, court moins vite ou a du mal \u00e0 monter les escaliers.<\/p><p><strong>Principaux sympt\u00f4mes observ\u00e9s :<\/strong><\/p><ul><li>Fatigue musculaire anormale, surtout apr\u00e8s l\u2019effort<\/li><li>Crampes fr\u00e9quentes, souvent douloureuses<\/li><li>Faiblesse musculaire progressive<\/li><li>Difficult\u00e9s \u00e0 courir, sauter ou \u00e0 se relever du sol<\/li><li>Modifications de la d\u00e9marche ou chutes fr\u00e9quentes<\/li><\/ul><p><em>\u00ab Elle [la dystrophie musculaire de Becker] se manifeste par une faiblesse musculaire pr\u00e9dominant aux membres inf\u00e9rieurs (fatigue \u00e0 la marche, g\u00eane pour courir, sauter, monter des escaliers) qui appara\u00eet dans l&#8217;enfance ou l&#8217;adolescence, voire plus tard. S&#8217;y associent souvent des douleurs musculaires et des crampes. \u00bb<\/em><strong> \u2014 AFM-T\u00e9l\u00e9thon.\u00a0<\/strong><\/p>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t<div class=\"elementor-element elementor-element-01f12aa e-flex e-con-boxed e-con e-parent\" data-id=\"01f12aa\" data-element_type=\"container\" data-e-type=\"container\" data-settings=\"{&quot;jet_parallax_layout_list&quot;:[]}\">\n\t\t\t\t\t<div class=\"e-con-inner\">\n\t\t\t\t<div class=\"elementor-element elementor-element-9660aa0 elementor-widget elementor-widget-heading\" data-id=\"9660aa0\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"heading.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t<h3 class=\"elementor-heading-title elementor-size-default\">Impact sur la mobilit\u00e9 et les fonctions cardiaques<\/h3>\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t<div class=\"elementor-element elementor-element-4577979 e-flex e-con-boxed e-con e-parent\" data-id=\"4577979\" data-element_type=\"container\" data-e-type=\"container\" data-settings=\"{&quot;jet_parallax_layout_list&quot;:[]}\">\n\t\t\t\t\t<div class=\"e-con-inner\">\n\t\t\t\t<div class=\"elementor-element elementor-element-8eb2f72 elementor-widget elementor-widget-text-editor\" data-id=\"8eb2f72\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<p>Au fur et \u00e0 mesure que la myopathie progresse, la faiblesse musculaire entra\u00eene une perte d\u2019autonomie motrice. Ce sont d\u2019abord les muscles du bassin et des jambes qui sont affect\u00e9s, puis ils sont suivis par ceux des bras et du tronc.<br \/>L\u2019atteinte cardiaque est \u00e9galement fr\u00e9quente. On parle alors de cardiomyopathie, une pathologie qui fragilise les parois du c\u0153ur, pouvant entra\u00eener une insuffisance cardiaque si elle n\u2019est pas prise en charge.<\/p><p><strong>Les sympt\u00f4mes cardiaques peuvent inclure :<\/strong><\/p><p>\u00a0<\/p><ul><li>Essoufflement \u00e0 l\u2019effort<\/li><li>Palpitations<\/li><li>Baisse de la tol\u00e9rance \u00e0 l\u2019effort<\/li><li>Fatigue g\u00e9n\u00e9rale<\/li><\/ul>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t<div class=\"elementor-element elementor-element-ac712d6 e-flex e-con-boxed e-con e-parent\" data-id=\"ac712d6\" data-element_type=\"container\" data-e-type=\"container\" data-settings=\"{&quot;jet_parallax_layout_list&quot;:[]}\">\n\t\t\t\t\t<div class=\"e-con-inner\">\n\t\t\t\t<div class=\"elementor-element elementor-element-c895f75 elementor-widget elementor-widget-spacer\" data-id=\"c895f75\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"spacer.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t<div class=\"elementor-spacer\">\n\t\t\t<div class=\"elementor-spacer-inner\"><\/div>\n\t\t<\/div>\n\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t<div class=\"elementor-element elementor-element-c07eb01 e-flex e-con-boxed e-con e-parent\" data-id=\"c07eb01\" data-element_type=\"container\" data-e-type=\"container\" data-settings=\"{&quot;jet_parallax_layout_list&quot;:[]}\">\n\t\t\t\t\t<div class=\"e-con-inner\">\n\t\t\t\t<div class=\"elementor-element elementor-element-9172c1d elementor-widget elementor-widget-heading\" data-id=\"9172c1d\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"heading.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t<h3 class=\"elementor-heading-title elementor-size-default\">Dystrophie de Becker vs Dystrophie de Duchenne : quelles diff\u00e9rences ?<\/h3>\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t<section class=\"elementor-section elementor-top-section elementor-element elementor-element-ebfe071 elementor-hidden-tablet elementor-hidden-mobile elementor-section-boxed elementor-section-height-default elementor-section-height-default\" data-id=\"ebfe071\" data-element_type=\"section\" data-e-type=\"section\" data-settings=\"{&quot;jet_parallax_layout_list&quot;:[],&quot;background_background&quot;:&quot;classic&quot;}\">\n\t\t\t\t\t\t<div class=\"elementor-container elementor-column-gap-default\">\n\t\t\t\t\t<div class=\"elementor-column elementor-col-33 elementor-top-column elementor-element elementor-element-994223e\" data-id=\"994223e\" data-element_type=\"column\" data-e-type=\"column\" data-settings=\"{&quot;background_background&quot;:&quot;classic&quot;}\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-be60b79 elementor-widget elementor-widget-text-editor\" data-id=\"be60b79\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<strong>Noms<\/strong>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t<div class=\"elementor-column elementor-col-33 elementor-top-column elementor-element elementor-element-6cb88c9\" data-id=\"6cb88c9\" data-element_type=\"column\" data-e-type=\"column\" data-settings=\"{&quot;background_background&quot;:&quot;classic&quot;}\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-b26dbcc elementor-widget elementor-widget-text-editor\" data-id=\"b26dbcc\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<p><a href=\"https:\/\/orthopus.com\/fr\/maladies-neuromusculaires\/dystrophie-musculaire-de-duchenne\/\"><strong>Dystrophie Musculaire de Duchenne<\/strong><\/a><\/p>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t<div class=\"elementor-column elementor-col-33 elementor-top-column elementor-element elementor-element-64d0097\" data-id=\"64d0097\" data-element_type=\"column\" data-e-type=\"column\" data-settings=\"{&quot;background_background&quot;:&quot;classic&quot;}\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-01a11ba elementor-widget elementor-widget-text-editor\" data-id=\"01a11ba\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<strong>Dystrophie Musculaire de Becker<\/strong>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/section>\n\t\t\t\t<section class=\"elementor-section elementor-top-section elementor-element elementor-element-e53aa4b elementor-hidden-tablet elementor-hidden-mobile elementor-section-boxed elementor-section-height-default elementor-section-height-default\" data-id=\"e53aa4b\" data-element_type=\"section\" data-e-type=\"section\" data-settings=\"{&quot;jet_parallax_layout_list&quot;:[]}\">\n\t\t\t\t\t\t<div class=\"elementor-container elementor-column-gap-default\">\n\t\t\t\t\t<div class=\"elementor-column elementor-col-33 elementor-top-column elementor-element elementor-element-176fd39\" data-id=\"176fd39\" data-element_type=\"column\" data-e-type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-46fc576 elementor-widget elementor-widget-text-editor\" data-id=\"46fc576\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<p><strong>Apparition<\/strong><\/p>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t<div class=\"elementor-column elementor-col-33 elementor-top-column elementor-element elementor-element-e7408d6\" data-id=\"e7408d6\" data-element_type=\"column\" data-e-type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-7d991bb elementor-widget elementor-widget-text-editor\" data-id=\"7d991bb\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<a href=\"https:\/\/www.msdmanuals.com\/fr\/professional\/p%C3%A9diatrie\/troubles-musculaires-h%C3%A9r%C3%A9ditaires\/dystrophie-musculaire-de-duchenne-et-de-becker#Diagnostic_v12784698_fr\">Avant 5 ans<\/a>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t<div class=\"elementor-column elementor-col-33 elementor-top-column elementor-element elementor-element-32fb615\" data-id=\"32fb615\" data-element_type=\"column\" data-e-type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-95e90fb elementor-widget elementor-widget-text-editor\" data-id=\"95e90fb\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<p><a href=\"https:\/\/www.has-sante.fr\/upload\/docs\/application\/pdf\/2019-11\/pnds_becker_def.pdf\">G\u00e9n\u00e9ralement avant 12 ans<\/a><\/p>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/section>\n\t\t\t\t<section class=\"elementor-section elementor-top-section elementor-element elementor-element-2e74968 elementor-hidden-tablet elementor-hidden-mobile elementor-section-boxed elementor-section-height-default elementor-section-height-default\" data-id=\"2e74968\" data-element_type=\"section\" data-e-type=\"section\" data-settings=\"{&quot;jet_parallax_layout_list&quot;:[]}\">\n\t\t\t\t\t\t<div class=\"elementor-container elementor-column-gap-default\">\n\t\t\t\t\t<div class=\"elementor-column elementor-col-33 elementor-top-column elementor-element elementor-element-23e7d1a\" data-id=\"23e7d1a\" data-element_type=\"column\" data-e-type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-49c6288 elementor-widget elementor-widget-text-editor\" data-id=\"49c6288\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<p><a href=\"https:\/\/www.msdmanuals.com\/fr\/accueil\/probl%C3%A8mes-de-sant%C3%A9-infantiles\/dystrophies-musculaires-et-troubles-associ%C3%A9s\/dystrophie-musculaire-de-duchenne-et-dystrophie-musculaire-de-becker#Sympt%C3%B4mes_v732845_fr\"><strong>Mobilit\u00e9<\/strong><\/a><\/p>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t<div class=\"elementor-column elementor-col-33 elementor-top-column elementor-element elementor-element-2249149\" data-id=\"2249149\" data-element_type=\"column\" data-e-type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-5a79698 elementor-widget elementor-widget-text-editor\" data-id=\"5a79698\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\tPerte de la marche avant 12 ans\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t<div class=\"elementor-column elementor-col-33 elementor-top-column elementor-element elementor-element-de7674c\" data-id=\"de7674c\" data-element_type=\"column\" data-e-type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-571081a elementor-widget elementor-widget-text-editor\" data-id=\"571081a\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\tMarche pr\u00e9serv\u00e9e plus longtemps\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/section>\n\t\t\t\t<section class=\"elementor-section elementor-top-section elementor-element elementor-element-5f3386c elementor-hidden-tablet elementor-hidden-mobile elementor-section-boxed elementor-section-height-default elementor-section-height-default\" data-id=\"5f3386c\" data-element_type=\"section\" data-e-type=\"section\" data-settings=\"{&quot;jet_parallax_layout_list&quot;:[]}\">\n\t\t\t\t\t\t<div class=\"elementor-container elementor-column-gap-default\">\n\t\t\t\t\t<div class=\"elementor-column elementor-col-33 elementor-top-column elementor-element elementor-element-f5e2a22\" data-id=\"f5e2a22\" data-element_type=\"column\" data-e-type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-4be387c elementor-widget elementor-widget-text-editor\" data-id=\"4be387c\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<strong>Dystrophine<\/strong>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t<div class=\"elementor-column elementor-col-33 elementor-top-column elementor-element elementor-element-3694cd1\" data-id=\"3694cd1\" data-element_type=\"column\" data-e-type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-fd4db50 elementor-widget elementor-widget-text-editor\" data-id=\"fd4db50\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\tAbsente ou quasi-absente\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t<div class=\"elementor-column elementor-col-33 elementor-top-column elementor-element elementor-element-6cdced4\" data-id=\"6cdced4\" data-element_type=\"column\" data-e-type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-47659ba elementor-widget elementor-widget-text-editor\" data-id=\"47659ba\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\tPr\u00e9sente en faible quantit\u00e9\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/section>\n\t\t<div class=\"elementor-element elementor-element-afef774 elementor-hidden-desktop elementor-hidden-tablet e-flex e-con-boxed e-con e-parent\" data-id=\"afef774\" data-element_type=\"container\" data-e-type=\"container\" data-settings=\"{&quot;jet_parallax_layout_list&quot;:[]}\">\n\t\t\t\t\t<div class=\"e-con-inner\">\n\t\t\t\t<div class=\"elementor-element elementor-element-2daf4cf elementor-widget elementor-widget-jet-table\" data-id=\"2daf4cf\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"jet-table.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t<div class=\"elementor-jet-table jet-elements\">\n\t\t<div class=\"jet-table-wrapper jet-table-responsive-tablet jet-table-responsive-mobile\">\n\t\t\t<table class=\"jet-table jet-table--fa5-compat\">\n\t\t\t\t<thead class=\"jet-table__head\"><tr class=\"jet-table__head-row\"><th class=\"jet-table__cell elementor-repeater-item-83d94a3 jet-table__head-cell\" colspan=\"1\" scope=\"col\"><div class=\"jet-table__cell-inner\"><div class=\"jet-table__cell-content\"><div class=\"jet-table__cell-text\">Noms<\/div><\/div><\/div><\/th><th class=\"jet-table__cell elementor-repeater-item-493e60a jet-table__head-cell\" colspan=\"1\" scope=\"col\"><div class=\"jet-table__cell-inner\"><div class=\"jet-table__cell-content\"><div class=\"jet-table__cell-text\">Dystrophie Musculaire de Duchenne<\/div><\/div><\/div><\/th><th class=\"jet-table__cell elementor-repeater-item-81ee20e jet-table__head-cell\" colspan=\"1\" scope=\"col\"><div class=\"jet-table__cell-inner\"><div class=\"jet-table__cell-content\"><div class=\"jet-table__cell-text\">Dystrophie Musculaire de Becker<\/div><\/div><\/div><\/th><\/tr><\/thead>\n\t\t\t\t\t\t\t\t<tbody class=\"jet-table__body\"><td class=\"jet-table__cell elementor-repeater-item-758ae34 jet-table__body-cell\" colspan=\"1\"><div class=\"jet-table__cell-inner\"><div class=\"jet-table__cell-content\"><div class=\"jet-table__cell-text\">Apparition<\/div><\/div><\/div><\/td><td class=\"jet-table__cell elementor-repeater-item-7bfd3f6 jet-table__body-cell\"><div class=\"jet-table__cell-inner\"><div class=\"jet-table__cell-content\"><div class=\"jet-table__cell-text\">Avant 5 ans<\/div><\/div><\/div><\/td><td class=\"jet-table__cell elementor-repeater-item-53caccc jet-table__body-cell\"><div class=\"jet-table__cell-inner\"><div class=\"jet-table__cell-content\"><div class=\"jet-table__cell-text\">G\u00e9n\u00e9ralement vers l&#8217;\u00e2ge de 12 ans<\/div><\/div><\/div><\/td><tr class=\"jet-table__body-row elementor-repeater-item-b832156\"><td class=\"jet-table__cell elementor-repeater-item-ea4dd97 jet-table__body-cell\"><div class=\"jet-table__cell-inner\"><div class=\"jet-table__cell-content\"><div class=\"jet-table__cell-text\">Mobilit\u00e9<\/div><\/div><\/div><\/td><td class=\"jet-table__cell elementor-repeater-item-7da20ee jet-table__body-cell\"><div class=\"jet-table__cell-inner\"><div class=\"jet-table__cell-content\"><div class=\"jet-table__cell-text\">Perte de la marche avant 12 ans<\/div><\/div><\/div><\/td><td class=\"jet-table__cell elementor-repeater-item-fc93119 jet-table__body-cell\"><div class=\"jet-table__cell-inner\"><div class=\"jet-table__cell-content\"><div class=\"jet-table__cell-text\">Marche pr\u00e9serv\u00e9e plus longtemps<\/div><\/div><\/div><\/td><\/tr><tr class=\"jet-table__body-row elementor-repeater-item-4c7a82b\"><td class=\"jet-table__cell elementor-repeater-item-7a286be jet-table__body-cell\"><div class=\"jet-table__cell-inner\"><div class=\"jet-table__cell-content\"><div class=\"jet-table__cell-text\">Dystrophine<\/div><\/div><\/div><\/td><td class=\"jet-table__cell elementor-repeater-item-41d85bc jet-table__body-cell\"><div class=\"jet-table__cell-inner\"><div class=\"jet-table__cell-content\"><div class=\"jet-table__cell-text\">Absente ou quasi-absente<\/div><\/div><\/div><\/td><td class=\"jet-table__cell elementor-repeater-item-6f3049d jet-table__body-cell\"><div class=\"jet-table__cell-inner\"><div class=\"jet-table__cell-content\"><div class=\"jet-table__cell-text\">Pr\u00e9sente en faible quantit\u00e9\n\n<\/div><\/div><\/div><\/td><\/tr><\/tbody>\n\t\t\t<\/table>\n\t\t<\/div>\n\n\t\t<\/div>\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t<div class=\"elementor-element elementor-element-eeaa642 e-flex e-con-boxed e-con e-parent\" data-id=\"eeaa642\" data-element_type=\"container\" data-e-type=\"container\" data-settings=\"{&quot;jet_parallax_layout_list&quot;:[]}\">\n\t\t\t\t\t<div class=\"e-con-inner\">\n\t\t\t\t<div class=\"elementor-element elementor-element-49bc59c elementor-widget elementor-widget-spacer\" data-id=\"49bc59c\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"spacer.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t<div class=\"elementor-spacer\">\n\t\t\t<div class=\"elementor-spacer-inner\"><\/div>\n\t\t<\/div>\n\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t<div class=\"elementor-element elementor-element-b3cc9f3 e-flex e-con-boxed e-con e-parent\" data-id=\"b3cc9f3\" data-element_type=\"container\" data-e-type=\"container\" data-settings=\"{&quot;jet_parallax_layout_list&quot;:[]}\">\n\t\t\t\t\t<div class=\"e-con-inner\">\n\t\t\t\t<div class=\"elementor-element elementor-element-6a63c30 elementor-widget elementor-widget-heading\" data-id=\"6a63c30\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"heading.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t<h2 class=\"elementor-heading-title elementor-size-default\">Causes g\u00e9n\u00e9tiques et transmission<\/h2>\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t<div class=\"elementor-element elementor-element-c18f38d e-flex e-con-boxed e-con e-parent\" data-id=\"c18f38d\" data-element_type=\"container\" data-e-type=\"container\" data-settings=\"{&quot;jet_parallax_layout_list&quot;:[]}\">\n\t\t\t\t\t<div class=\"e-con-inner\">\n\t\t\t\t<div class=\"elementor-element elementor-element-1965123 elementor-widget elementor-widget-text-editor\" data-id=\"1965123\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<p>La <strong>dystrophie musculaire de Becker<\/strong> est caus\u00e9e par une mutation du <strong>g\u00e8ne DMD<\/strong>, situ\u00e9 sur le chromosome X. Ce g\u00e8ne est responsable de la production de <strong>dystrophine<\/strong>, une prot\u00e9ine impliqu\u00e9e dans la structure et la protection des fibres musculaires.<br \/>Chez les personnes concern\u00e9es, la mutation ne bloque pas totalement la fabrication de la dystrophine, mais elle la rend un peu moins efficace : elle n\u2019est pas totalement absente comme dans la <a href=\"https:\/\/orthopus.com\/fr\/maladies-neuromusculaires\/dystrophie-musculaire-de-duchenne\/\">dystrophie musculaire de Duchenne<\/a>. La dystrophie musculaire de Becker, elle, permet une production <strong>r\u00e9siduelle de dystrophine<\/strong>, d\u2019o\u00f9 une atteinte plus mod\u00e9r\u00e9e. C\u2019est-\u00e0-dire que plus il y a de dystrophine moins il y a de sympt\u00f4mes.<\/p>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t<div class=\"elementor-element elementor-element-c851a9e e-flex e-con-boxed e-con e-parent\" data-id=\"c851a9e\" data-element_type=\"container\" data-e-type=\"container\" data-settings=\"{&quot;jet_parallax_layout_list&quot;:[]}\">\n\t\t\t\t\t<div class=\"e-con-inner\">\n\t\t\t\t<div class=\"elementor-element elementor-element-4a50451 elementor-widget elementor-widget-spacer\" data-id=\"4a50451\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"spacer.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t<div class=\"elementor-spacer\">\n\t\t\t<div class=\"elementor-spacer-inner\"><\/div>\n\t\t<\/div>\n\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t<div class=\"elementor-element elementor-element-75705d7 e-flex e-con-boxed e-con e-parent\" data-id=\"75705d7\" data-element_type=\"container\" data-e-type=\"container\" data-settings=\"{&quot;jet_parallax_layout_list&quot;:[]}\">\n\t\t\t\t\t<div class=\"e-con-inner\">\n\t\t\t\t<div class=\"elementor-element elementor-element-31d3ecb elementor-widget elementor-widget-heading\" data-id=\"31d3ecb\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"heading.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t<h3 class=\"elementor-heading-title elementor-size-default\">Transmission g\u00e9n\u00e9tique<\/h3>\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t<div class=\"elementor-element elementor-element-64fddee e-flex e-con-boxed e-con e-parent\" data-id=\"64fddee\" data-element_type=\"container\" data-e-type=\"container\" data-settings=\"{&quot;jet_parallax_layout_list&quot;:[]}\">\n\t\t\t\t\t<div class=\"e-con-inner\">\n\t\t\t\t<div class=\"elementor-element elementor-element-458a9f4 elementor-widget elementor-widget-text-editor\" data-id=\"458a9f4\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<ul><li>La DMB suit un <strong>mode r\u00e9cessif li\u00e9 \u00e0 l\u2019X<\/strong><\/li><li>Les femmes porteuses peuvent transmettre le g\u00e8ne mut\u00e9 \u00e0 leurs enfants<\/li><li>Les gar\u00e7ons ayant h\u00e9rit\u00e9 du chromosome X mut\u00e9 seront atteints<\/li><\/ul><p>Un <a href=\"https:\/\/www.afm-telethon.fr\/fr\/vivre-avec-la-maladie\/je-m-informe-sur-les-maladies\/comprendre-les-maladies-genetiques\/consultation-genetique\"><strong>conseil g\u00e9n\u00e9tique<\/strong><\/a> est fortement souhaitable pour les familles concern\u00e9es. Il permet d\u2019\u00e9valuer les risques de transmission et de proposer un diagnostic pr\u00e9natal ou un d\u00e9pistage g\u00e9n\u00e9tique familial.<\/p>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t<section class=\"elementor-section elementor-top-section elementor-element elementor-element-cab2699 elementor-section-boxed elementor-section-height-default elementor-section-height-default\" data-id=\"cab2699\" data-element_type=\"section\" data-e-type=\"section\" data-settings=\"{&quot;jet_parallax_layout_list&quot;:[],&quot;background_background&quot;:&quot;classic&quot;}\">\n\t\t\t\t\t\t<div class=\"elementor-container elementor-column-gap-default\">\n\t\t\t\t\t<div class=\"elementor-column elementor-col-50 elementor-top-column elementor-element elementor-element-f0de1c7\" data-id=\"f0de1c7\" data-element_type=\"column\" data-e-type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-cdc321e elementor-widget elementor-widget-text-editor\" data-id=\"cdc321e\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<p>\ud83d\udc19<\/p>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t<div class=\"elementor-column elementor-col-50 elementor-top-column elementor-element elementor-element-ce3045e\" data-id=\"ce3045e\" data-element_type=\"column\" data-e-type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-3e66f27 elementor-widget elementor-widget-text-editor\" data-id=\"3e66f27\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<p><strong>Le point vocab\u2019 du poulpe : <\/strong><br \/>Un conseil g\u00e9n\u00e9tique est un accompagnement m\u00e9dical et psychologique propos\u00e9 aux personnes ou familles \u00e0 risque de d\u00e9velopper une maladie g\u00e9n\u00e9tique (par exemple, la dystrophie musculaire de Becker). Son objectif est d\u2019informer, d\u2019\u00e9valuer les risques de transmission, et d\u2019\u00eatre aid\u00e9 \u00e0 prendre des d\u00e9cisions \u00e9clair\u00e9es en mati\u00e8re de sant\u00e9 ou de reproduction.<\/p>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t<div class=\"elementor-element elementor-element-e5de86c elementor-widget elementor-widget-n-accordion\" data-id=\"e5de86c\" data-element_type=\"widget\" data-e-type=\"widget\" data-settings=\"{&quot;default_state&quot;:&quot;expanded&quot;,&quot;max_items_expended&quot;:&quot;one&quot;,&quot;n_accordion_animation_duration&quot;:{&quot;unit&quot;:&quot;ms&quot;,&quot;size&quot;:400,&quot;sizes&quot;:[]}}\" data-widget_type=\"nested-accordion.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t<div class=\"e-n-accordion\" aria-label=\"Accordion. Open links with Enter or Space, close with Escape, and navigate with Arrow Keys\">\n\t\t\t\t\t\t<details id=\"e-n-accordion-item-2410\" class=\"e-n-accordion-item\" open>\n\t\t\t\t<summary class=\"e-n-accordion-item-title\" data-accordion-index=\"1\" tabindex=\"0\" aria-expanded=\"true\" aria-controls=\"e-n-accordion-item-2410\" >\n\t\t\t\t\t<span class='e-n-accordion-item-title-header'><div class=\"e-n-accordion-item-title-text\"> Qu'est-ce que \u00e7a implique ? <\/div><\/span>\n\t\t\t\t\t\t\t<span class='e-n-accordion-item-title-icon'>\n\t\t\t<span class='e-opened' ><i aria-hidden=\"true\" class=\"fas fa-minus\"><\/i><\/span>\n\t\t\t<span class='e-closed'><i aria-hidden=\"true\" class=\"fas fa-plus\"><\/i><\/span>\n\t\t<\/span>\n\n\t\t\t\t\t\t<\/summary>\n\t\t\t\t<div role=\"region\" aria-labelledby=\"e-n-accordion-item-2410\" class=\"elementor-element elementor-element-57357e5 e-con-full e-flex e-con e-child\" data-id=\"57357e5\" data-element_type=\"container\" data-e-type=\"container\" data-settings=\"{&quot;jet_parallax_layout_list&quot;:[]}\">\n\t\t\t\t<div class=\"elementor-element elementor-element-da85572 elementor-widget elementor-widget-text-editor\" data-id=\"da85572\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<p><strong>Lors d\u2019un conseil g\u00e9n\u00e9tique, on peut :<br \/><br \/><\/strong><\/p><ul><li>\u00c9tudier l\u2019histoire familiale.<\/li><li>\u00c9valuer les risques de transmission de la maladie \u00e0 la descendance.<\/li><li>Expliquer les options disponibles, comme :<br \/>\u27a1\ufe0f Le diagnostic pr\u00e9natal (DPN) : test r\u00e9alis\u00e9 durant la grossesse afin de savoir si le f\u0153tus est atteint.<br \/>\u27a1\ufe0f Le diagnostic pr\u00e9implantatoire (DPI) : utilis\u00e9 lors d\u2019une f\u00e9condation in vitro (FIV), pour implanter uniquement des embryons non porteurs.<br \/>\u27a1\ufe0f Le d\u00e9pistage g\u00e9n\u00e9tique familial : tests propos\u00e9s \u00e0 d&#8217;autres membres de la famille pour savoir s\u2019ils sont porteurs.<\/li><\/ul>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/details>\n\t\t\t\t\t\t<details id=\"e-n-accordion-item-2411\" class=\"e-n-accordion-item\" >\n\t\t\t\t<summary class=\"e-n-accordion-item-title\" data-accordion-index=\"2\" tabindex=\"-1\" aria-expanded=\"false\" aria-controls=\"e-n-accordion-item-2411\" >\n\t\t\t\t\t<span class='e-n-accordion-item-title-header'><div class=\"e-n-accordion-item-title-text\"> Qui r\u00e9alise \u00e7a en France ? <\/div><\/span>\n\t\t\t\t\t\t\t<span class='e-n-accordion-item-title-icon'>\n\t\t\t<span class='e-opened' ><i aria-hidden=\"true\" class=\"fas fa-minus\"><\/i><\/span>\n\t\t\t<span class='e-closed'><i aria-hidden=\"true\" class=\"fas fa-plus\"><\/i><\/span>\n\t\t<\/span>\n\n\t\t\t\t\t\t<\/summary>\n\t\t\t\t<div role=\"region\" aria-labelledby=\"e-n-accordion-item-2411\" class=\"elementor-element elementor-element-9d690c5 e-con-full e-flex e-con e-child\" data-id=\"9d690c5\" data-element_type=\"container\" data-e-type=\"container\" data-settings=\"{&quot;jet_parallax_layout_list&quot;:[]}\">\n\t\t\t\t<div class=\"elementor-element elementor-element-43187eb elementor-widget elementor-widget-text-editor\" data-id=\"43187eb\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<p>Ce sont les centres de g\u00e9n\u00e9tique m\u00e9dicale ou centres de r\u00e9f\u00e9rence des maladies rares qui s\u2019en occupent. Ils regroupent :<br \/><br \/><\/p><ul><li>Des g\u00e9n\u00e9ticiens m\u00e9dicaux<\/li><li>Des conseillers en g\u00e9n\u00e9tique<\/li><li>Des psychologues, pour accompagner l\u2019annonce et les d\u00e9cisions<\/li><\/ul><p>En r\u00e8gle g\u00e9n\u00e9rale, ils sont rattach\u00e9s \u00e0 des h\u00f4pitaux universitaires (CHU) ou \u00e0 des \u00e9tablissements sp\u00e9cialis\u00e9s. L\u2019<a href=\"https:\/\/www.afm-telethon.fr\/fr\">AFM-T\u00e9l\u00e9thon<\/a> peut \u00e9galement orienter les familles vers les bons services ou les accompagner dans leurs d\u00e9marches.<\/p>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/details>\n\t\t\t\t\t<\/div>\n\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/section>\n\t\t<div class=\"elementor-element elementor-element-30f4757 e-flex e-con-boxed e-con e-parent\" data-id=\"30f4757\" data-element_type=\"container\" data-e-type=\"container\" data-settings=\"{&quot;jet_parallax_layout_list&quot;:[]}\">\n\t\t\t\t\t<div class=\"e-con-inner\">\n\t\t\t\t<div class=\"elementor-element elementor-element-0302abb elementor-widget elementor-widget-spacer\" data-id=\"0302abb\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"spacer.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t<div class=\"elementor-spacer\">\n\t\t\t<div class=\"elementor-spacer-inner\"><\/div>\n\t\t<\/div>\n\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t<div class=\"elementor-element elementor-element-b9471d1 e-flex e-con-boxed e-con e-parent\" data-id=\"b9471d1\" data-element_type=\"container\" data-e-type=\"container\" data-settings=\"{&quot;jet_parallax_layout_list&quot;:[]}\">\n\t\t\t\t\t<div class=\"e-con-inner\">\n\t\t\t\t<div class=\"elementor-element elementor-element-a5b8bc4 elementor-widget elementor-widget-heading\" data-id=\"a5b8bc4\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"heading.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t<h2 class=\"elementor-heading-title elementor-size-default\">Quels sont les traitements existants pour la dystrophie musculaire de Becker ?<\/h2>\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t<div class=\"elementor-element elementor-element-b806862 e-flex e-con-boxed e-con e-parent\" data-id=\"b806862\" data-element_type=\"container\" data-e-type=\"container\" data-settings=\"{&quot;jet_parallax_layout_list&quot;:[]}\">\n\t\t\t\t\t<div class=\"e-con-inner\">\n\t\t\t\t<div class=\"elementor-element elementor-element-fb177e3 elementor-widget elementor-widget-text-editor\" data-id=\"fb177e3\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<p>\u00c0 ce jour, <strong>aucun traitement ne permet de gu\u00e9rir la dystrophie musculaire de Becker<\/strong>. Toutefois, des <a href=\"https:\/\/orthopus.com\/fr\/maladies-neuromusculaires\/traitement-maladie-neuromusculaire\/\">approches combin\u00e9es<\/a> permettent de ralentir l\u2019\u00e9volution de la maladie, de pr\u00e9server la mobilit\u00e9, et d&#8217;am\u00e9liorer la qualit\u00e9 de vie.<br \/>La prise en charge repose sur une approche pluridisciplinaire, associant traitements m\u00e9dicamenteux, r\u00e9\u00e9ducation, surveillance cardiaque, et <a href=\"https:\/\/orthopus.com\/fr\/aide-technique\/robot-assistance-compensation\/\">aides techniques<\/a>.<\/p>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t<div class=\"elementor-element elementor-element-0fc7635 e-flex e-con-boxed e-con e-parent\" data-id=\"0fc7635\" data-element_type=\"container\" data-e-type=\"container\" data-settings=\"{&quot;jet_parallax_layout_list&quot;:[]}\">\n\t\t\t\t\t<div class=\"e-con-inner\">\n\t\t\t\t<div class=\"elementor-element elementor-element-9be9432 elementor-widget elementor-widget-spacer\" data-id=\"9be9432\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"spacer.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t<div class=\"elementor-spacer\">\n\t\t\t<div class=\"elementor-spacer-inner\"><\/div>\n\t\t<\/div>\n\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t<div class=\"elementor-element elementor-element-f081845 e-flex e-con-boxed e-con e-parent\" data-id=\"f081845\" data-element_type=\"container\" data-e-type=\"container\" data-settings=\"{&quot;jet_parallax_layout_list&quot;:[]}\">\n\t\t\t\t\t<div class=\"e-con-inner\">\n\t\t\t\t<div class=\"elementor-element elementor-element-49f8960 elementor-widget elementor-widget-heading\" data-id=\"49f8960\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"heading.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t<h3 class=\"elementor-heading-title elementor-size-default\">Approche m\u00e9dicamenteuse et traitements actuels<\/h3>\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t<section class=\"elementor-section elementor-top-section elementor-element elementor-element-00683e3 elementor-hidden-tablet elementor-hidden-mobile elementor-section-boxed elementor-section-height-default elementor-section-height-default\" data-id=\"00683e3\" data-element_type=\"section\" data-e-type=\"section\" data-settings=\"{&quot;jet_parallax_layout_list&quot;:[],&quot;background_background&quot;:&quot;classic&quot;}\">\n\t\t\t\t\t\t<div class=\"elementor-container elementor-column-gap-default\">\n\t\t\t\t\t<div class=\"elementor-column elementor-col-33 elementor-top-column elementor-element elementor-element-9377ac3\" data-id=\"9377ac3\" data-element_type=\"column\" data-e-type=\"column\" data-settings=\"{&quot;background_background&quot;:&quot;classic&quot;}\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-0df5ad3 elementor-widget elementor-widget-text-editor\" data-id=\"0df5ad3\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<strong>Traitement<\/strong>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t<div class=\"elementor-column elementor-col-33 elementor-top-column elementor-element elementor-element-47cc85b\" data-id=\"47cc85b\" data-element_type=\"column\" data-e-type=\"column\" data-settings=\"{&quot;background_background&quot;:&quot;classic&quot;}\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-2654c0d elementor-widget elementor-widget-text-editor\" data-id=\"2654c0d\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<strong>Objectif principal<\/strong>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t<div class=\"elementor-column elementor-col-33 elementor-top-column elementor-element elementor-element-101ec0e\" data-id=\"101ec0e\" data-element_type=\"column\" data-e-type=\"column\" data-settings=\"{&quot;background_background&quot;:&quot;classic&quot;}\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-e58cfda elementor-widget elementor-widget-text-editor\" data-id=\"e58cfda\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<strong>Statut actuel<\/strong>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/section>\n\t\t\t\t<section class=\"elementor-section elementor-top-section elementor-element elementor-element-2aad8df elementor-hidden-tablet elementor-hidden-mobile elementor-section-boxed elementor-section-height-default elementor-section-height-default\" data-id=\"2aad8df\" data-element_type=\"section\" data-e-type=\"section\" data-settings=\"{&quot;jet_parallax_layout_list&quot;:[]}\">\n\t\t\t\t\t\t<div class=\"elementor-container elementor-column-gap-default\">\n\t\t\t\t\t<div class=\"elementor-column elementor-col-33 elementor-top-column elementor-element elementor-element-6fcf42c\" data-id=\"6fcf42c\" data-element_type=\"column\" data-e-type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-fe1c426 elementor-widget elementor-widget-text-editor\" data-id=\"fe1c426\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<p><a href=\"https:\/\/www.msdmanuals.com\/fr\/accueil\/multimedia\/table\/cortico%C3%AFdes-utilisations-et-effets-secondaires\"><strong>Corticost\u00e9ro\u00efdes<\/strong><\/a><\/p>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t<div class=\"elementor-column elementor-col-33 elementor-top-column elementor-element elementor-element-caa38b4\" data-id=\"caa38b4\" data-element_type=\"column\" data-e-type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-5e9fcef elementor-widget elementor-widget-text-editor\" data-id=\"5e9fcef\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<p>Ralentir la perte de force musculaire<\/p>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t<div class=\"elementor-column elementor-col-33 elementor-top-column elementor-element elementor-element-d91859d\" data-id=\"d91859d\" data-element_type=\"column\" data-e-type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-06646a8 elementor-widget elementor-widget-text-editor\" data-id=\"06646a8\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\tUtilis\u00e9s couramment\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/section>\n\t\t\t\t<section class=\"elementor-section elementor-top-section elementor-element elementor-element-c05650e elementor-hidden-tablet elementor-hidden-mobile elementor-section-boxed elementor-section-height-default elementor-section-height-default\" data-id=\"c05650e\" data-element_type=\"section\" data-e-type=\"section\" data-settings=\"{&quot;jet_parallax_layout_list&quot;:[]}\">\n\t\t\t\t\t\t<div class=\"elementor-container elementor-column-gap-default\">\n\t\t\t\t\t<div class=\"elementor-column elementor-col-33 elementor-top-column elementor-element elementor-element-0c802f0\" data-id=\"0c802f0\" data-element_type=\"column\" data-e-type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-9c8f20a elementor-widget elementor-widget-text-editor\" data-id=\"9c8f20a\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<p><a href=\"https:\/\/fr.wikipedia.org\/wiki\/Inhibiteur_de_l%27enzyme_de_conversion\"><strong>Inhibiteurs de l&#8217;enzyme de conversion (IEC)<\/strong><\/a><\/p>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t<div class=\"elementor-column elementor-col-33 elementor-top-column elementor-element elementor-element-a9abec7\" data-id=\"a9abec7\" data-element_type=\"column\" data-e-type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-d486e3c elementor-widget elementor-widget-text-editor\" data-id=\"d486e3c\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\tPr\u00e9server la fonction cardiaque\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t<div class=\"elementor-column elementor-col-33 elementor-top-column elementor-element elementor-element-962777d\" data-id=\"962777d\" data-element_type=\"column\" data-e-type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-393f70f elementor-widget elementor-widget-text-editor\" data-id=\"393f70f\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\tPrescrits en cas de cardiomyopathie\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/section>\n\t\t\t\t<section class=\"elementor-section elementor-top-section elementor-element elementor-element-15220af elementor-hidden-tablet elementor-hidden-mobile elementor-section-boxed elementor-section-height-default elementor-section-height-default\" data-id=\"15220af\" data-element_type=\"section\" data-e-type=\"section\" data-settings=\"{&quot;jet_parallax_layout_list&quot;:[]}\">\n\t\t\t\t\t\t<div class=\"elementor-container elementor-column-gap-default\">\n\t\t\t\t\t<div class=\"elementor-column elementor-col-33 elementor-top-column elementor-element elementor-element-6d60383\" data-id=\"6d60383\" data-element_type=\"column\" data-e-type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-05de3ef elementor-widget elementor-widget-text-editor\" data-id=\"05de3ef\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<p><a href=\"https:\/\/www.cbip.be\/fr\/chapters\/2?frag=570\"><strong>B\u00eata-bloquants<\/strong><\/a><\/p>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t<div class=\"elementor-column elementor-col-33 elementor-top-column elementor-element elementor-element-fcf7f32\" data-id=\"fcf7f32\" data-element_type=\"column\" data-e-type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-a5f5a0b elementor-widget elementor-widget-text-editor\" data-id=\"a5f5a0b\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\tR\u00e9duire les risques cardiaques\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t<div class=\"elementor-column elementor-col-33 elementor-top-column elementor-element elementor-element-dd23550\" data-id=\"dd23550\" data-element_type=\"column\" data-e-type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-9c1da3c elementor-widget elementor-widget-text-editor\" data-id=\"9c1da3c\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\tUtilis\u00e9s selon le profil\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/section>\n\t\t\t\t<section class=\"elementor-section elementor-top-section elementor-element elementor-element-280d0ce elementor-hidden-tablet elementor-hidden-mobile elementor-section-boxed elementor-section-height-default elementor-section-height-default\" data-id=\"280d0ce\" data-element_type=\"section\" data-e-type=\"section\" data-settings=\"{&quot;jet_parallax_layout_list&quot;:[]}\">\n\t\t\t\t\t\t<div class=\"elementor-container elementor-column-gap-default\">\n\t\t\t\t\t<div class=\"elementor-column elementor-col-33 elementor-top-column elementor-element elementor-element-b91176f\" data-id=\"b91176f\" data-element_type=\"column\" data-e-type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-7f68add elementor-widget elementor-widget-text-editor\" data-id=\"7f68add\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<p><a href=\"https:\/\/www.medecinesciences.org\/en\/articles\/medsci\/full_html\/2004\/10\/medsci20042012p1163\/medsci20042012p1163.html\"><strong>Saut d&#8217;exon<\/strong><\/a><\/p>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t<div class=\"elementor-column elementor-col-33 elementor-top-column elementor-element elementor-element-bdbe8ef\" data-id=\"bdbe8ef\" data-element_type=\"column\" data-e-type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-35c021e elementor-widget elementor-widget-text-editor\" data-id=\"35c021e\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\tCorriger la lecture du g\u00e8ne DMD\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t<div class=\"elementor-column elementor-col-33 elementor-top-column elementor-element elementor-element-c9b3708\" data-id=\"c9b3708\" data-element_type=\"column\" data-e-type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-9a63a0c elementor-widget elementor-widget-text-editor\" data-id=\"9a63a0c\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\tEn d\u00e9veloppement\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/section>\n\t\t\t\t<section class=\"elementor-section elementor-top-section elementor-element elementor-element-c832619 elementor-hidden-tablet elementor-hidden-mobile elementor-section-boxed elementor-section-height-default elementor-section-height-default\" data-id=\"c832619\" data-element_type=\"section\" data-e-type=\"section\" data-settings=\"{&quot;jet_parallax_layout_list&quot;:[]}\">\n\t\t\t\t\t\t<div class=\"elementor-container elementor-column-gap-default\">\n\t\t\t\t\t<div class=\"elementor-column elementor-col-33 elementor-top-column elementor-element elementor-element-83e2253\" data-id=\"83e2253\" data-element_type=\"column\" data-e-type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-0d12908 elementor-widget elementor-widget-text-editor\" data-id=\"0d12908\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<p><a href=\"https:\/\/www.afm-telethon.fr\/fr\/termes\/therapie-genique#:~:text=La%20th%C3%A9rapie%20g%C3%A9nique%20repose%20sur,plus%20fr%C3%A9quentes%20comme%20les%20cancers.\"><strong>Th\u00e9rapie g\u00e9nique<\/strong><\/a><\/p>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t<div class=\"elementor-column elementor-col-33 elementor-top-column elementor-element elementor-element-e5cb30d\" data-id=\"e5cb30d\" data-element_type=\"column\" data-e-type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-d2aa427 elementor-widget elementor-widget-text-editor\" data-id=\"d2aa427\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\tRestaurer la production de dystrophine\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t<div class=\"elementor-column elementor-col-33 elementor-top-column elementor-element elementor-element-61413ca\" data-id=\"61413ca\" data-element_type=\"column\" data-e-type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-b7368e0 elementor-widget elementor-widget-text-editor\" data-id=\"b7368e0\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\tEn phase d&#8217;essais\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/section>\n\t\t<div class=\"elementor-element elementor-element-5e940d8 elementor-hidden-desktop elementor-hidden-tablet e-flex e-con-boxed e-con e-parent\" data-id=\"5e940d8\" data-element_type=\"container\" data-e-type=\"container\" data-settings=\"{&quot;jet_parallax_layout_list&quot;:[]}\">\n\t\t\t\t\t<div class=\"e-con-inner\">\n\t\t\t\t<div class=\"elementor-element elementor-element-76fe860 elementor-widget elementor-widget-jet-table\" data-id=\"76fe860\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"jet-table.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t<div class=\"elementor-jet-table jet-elements\">\n\t\t<div class=\"jet-table-wrapper jet-table-responsive-tablet jet-table-responsive-mobile\">\n\t\t\t<table class=\"jet-table jet-table--fa5-compat\">\n\t\t\t\t<thead class=\"jet-table__head\"><tr class=\"jet-table__head-row\"><th class=\"jet-table__cell elementor-repeater-item-83d94a3 jet-table__head-cell\" colspan=\"1\" scope=\"col\"><div class=\"jet-table__cell-inner\"><div class=\"jet-table__cell-content\"><div class=\"jet-table__cell-text\">Traitement<\/div><\/div><\/div><\/th><th class=\"jet-table__cell elementor-repeater-item-493e60a jet-table__head-cell\" colspan=\"1\" scope=\"col\"><div class=\"jet-table__cell-inner\"><div class=\"jet-table__cell-content\"><div class=\"jet-table__cell-text\">Objectif principal<\/div><\/div><\/div><\/th><th class=\"jet-table__cell elementor-repeater-item-81ee20e jet-table__head-cell\" colspan=\"1\" scope=\"col\"><div class=\"jet-table__cell-inner\"><div class=\"jet-table__cell-content\"><div class=\"jet-table__cell-text\">Statut actuel<\/div><\/div><\/div><\/th><\/tr><\/thead>\n\t\t\t\t\t\t\t\t<tbody class=\"jet-table__body\"><td class=\"jet-table__cell elementor-repeater-item-758ae34 jet-table__body-cell\" colspan=\"1\"><div class=\"jet-table__cell-inner\"><div class=\"jet-table__cell-content\"><div class=\"jet-table__cell-text\">Corticost\u00e9ro\u00efdes<\/div><\/div><\/div><\/td><td class=\"jet-table__cell elementor-repeater-item-7bfd3f6 jet-table__body-cell\"><div class=\"jet-table__cell-inner\"><div class=\"jet-table__cell-content\"><div class=\"jet-table__cell-text\">Ralentir la perte de force musculaire<\/div><\/div><\/div><\/td><td class=\"jet-table__cell elementor-repeater-item-53caccc jet-table__body-cell\"><div class=\"jet-table__cell-inner\"><div class=\"jet-table__cell-content\"><div class=\"jet-table__cell-text\">Utilis\u00e9s couramment<\/div><\/div><\/div><\/td><tr class=\"jet-table__body-row elementor-repeater-item-b832156\"><td class=\"jet-table__cell elementor-repeater-item-ea4dd97 jet-table__body-cell\"><div class=\"jet-table__cell-inner\"><div class=\"jet-table__cell-content\"><div class=\"jet-table__cell-text\">Inhibiteurs de l&#8217;enzyme de conversion (IEC)<\/div><\/div><\/div><\/td><td class=\"jet-table__cell elementor-repeater-item-7da20ee jet-table__body-cell\"><div class=\"jet-table__cell-inner\"><div class=\"jet-table__cell-content\"><div class=\"jet-table__cell-text\">Pr\u00e9server la fonction cardiaque<\/div><\/div><\/div><\/td><td class=\"jet-table__cell elementor-repeater-item-fc93119 jet-table__body-cell\"><div class=\"jet-table__cell-inner\"><div class=\"jet-table__cell-content\"><div class=\"jet-table__cell-text\">Prescrits en cas de cardiomyopathie<\/div><\/div><\/div><\/td><\/tr><tr class=\"jet-table__body-row elementor-repeater-item-4c7a82b\"><td class=\"jet-table__cell elementor-repeater-item-7a286be jet-table__body-cell\"><div class=\"jet-table__cell-inner\"><div class=\"jet-table__cell-content\"><div class=\"jet-table__cell-text\">B\u00eata-bloquants<\/div><\/div><\/div><\/td><td class=\"jet-table__cell elementor-repeater-item-41d85bc jet-table__body-cell\"><div class=\"jet-table__cell-inner\"><div class=\"jet-table__cell-content\"><div class=\"jet-table__cell-text\">R\u00e9duire les risques cardiaques<\/div><\/div><\/div><\/td><td class=\"jet-table__cell elementor-repeater-item-6f3049d jet-table__body-cell\"><div class=\"jet-table__cell-inner\"><div class=\"jet-table__cell-content\"><div class=\"jet-table__cell-text\">Utilis\u00e9s selon le profil<\/div><\/div><\/div><\/td><\/tr><tr class=\"jet-table__body-row elementor-repeater-item-0d8a535\"><td class=\"jet-table__cell elementor-repeater-item-2d80336 jet-table__body-cell\"><div class=\"jet-table__cell-inner\"><div class=\"jet-table__cell-content\"><div class=\"jet-table__cell-text\">Saut d&#8217;exon<\/div><\/div><\/div><\/td><td class=\"jet-table__cell elementor-repeater-item-8238817 jet-table__body-cell\"><div class=\"jet-table__cell-inner\"><div class=\"jet-table__cell-content\"><div class=\"jet-table__cell-text\">Corriger la lecture du g\u00e8ne DMD<\/div><\/div><\/div><\/td><td class=\"jet-table__cell elementor-repeater-item-0879855 jet-table__body-cell\"><div class=\"jet-table__cell-inner\"><div class=\"jet-table__cell-content\"><div class=\"jet-table__cell-text\">En d\u00e9veloppement<\/div><\/div><\/div><\/td><\/tr><tr class=\"jet-table__body-row elementor-repeater-item-9a65f3e\"><td class=\"jet-table__cell elementor-repeater-item-302c583 jet-table__body-cell\"><div class=\"jet-table__cell-inner\"><div class=\"jet-table__cell-content\"><div class=\"jet-table__cell-text\">Th\u00e9rapie g\u00e9nique<\/div><\/div><\/div><\/td><td class=\"jet-table__cell elementor-repeater-item-8ff36d8 jet-table__body-cell\"><div class=\"jet-table__cell-inner\"><div class=\"jet-table__cell-content\"><div class=\"jet-table__cell-text\">Restaurer la production de dystrophine<\/div><\/div><\/div><\/td><td class=\"jet-table__cell elementor-repeater-item-aead8d4 jet-table__body-cell\"><div class=\"jet-table__cell-inner\"><div class=\"jet-table__cell-content\"><div class=\"jet-table__cell-text\">En phase d&#8217;essais<\/div><\/div><\/div><\/td><\/tr><\/tbody>\n\t\t\t<\/table>\n\t\t<\/div>\n\n\t\t<\/div>\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t<div class=\"elementor-element elementor-element-ed9bdb5 e-flex e-con-boxed e-con e-parent\" data-id=\"ed9bdb5\" data-element_type=\"container\" data-e-type=\"container\" data-settings=\"{&quot;jet_parallax_layout_list&quot;:[]}\">\n\t\t\t\t\t<div class=\"e-con-inner\">\n\t\t\t\t<div class=\"elementor-element elementor-element-6a32b60 elementor-widget elementor-widget-text-editor\" data-id=\"6a32b60\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<p>Ces traitements permettent, dans certains cas, de stabiliser les fonctions musculaires ou cardiaques sur plusieurs ann\u00e9es. Leur efficacit\u00e9 d\u00e9pend du stade de la maladie et des caract\u00e9ristiques g\u00e9n\u00e9tiques de la personne ayant un handicap.<\/p>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t<div class=\"elementor-element elementor-element-f44bd94 e-flex e-con-boxed e-con e-parent\" data-id=\"f44bd94\" data-element_type=\"container\" data-e-type=\"container\" data-settings=\"{&quot;jet_parallax_layout_list&quot;:[]}\">\n\t\t\t\t\t<div class=\"e-con-inner\">\n\t\t\t\t<div class=\"elementor-element elementor-element-509e8a2 elementor-widget elementor-widget-spacer\" data-id=\"509e8a2\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"spacer.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t<div class=\"elementor-spacer\">\n\t\t\t<div class=\"elementor-spacer-inner\"><\/div>\n\t\t<\/div>\n\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t<div class=\"elementor-element elementor-element-d6db1df e-flex e-con-boxed e-con e-parent\" data-id=\"d6db1df\" data-element_type=\"container\" data-e-type=\"container\" data-settings=\"{&quot;jet_parallax_layout_list&quot;:[]}\">\n\t\t\t\t\t<div class=\"e-con-inner\">\n\t\t\t\t<div class=\"elementor-element elementor-element-b2457b2 elementor-widget elementor-widget-heading\" data-id=\"b2457b2\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"heading.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t<h3 class=\"elementor-heading-title elementor-size-default\">Suivi m\u00e9dical et prise en charge pluridisciplinaire<\/h3>\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t<div class=\"elementor-element elementor-element-91d9578 e-flex e-con-boxed e-con e-parent\" data-id=\"91d9578\" data-element_type=\"container\" data-e-type=\"container\" data-settings=\"{&quot;jet_parallax_layout_list&quot;:[]}\">\n\t\t\t\t\t<div class=\"e-con-inner\">\n\t\t\t\t<div class=\"elementor-element elementor-element-f4dfb69 elementor-widget elementor-widget-text-editor\" data-id=\"f4dfb69\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<p>Le suivi de la DMB repose sur une \u00e9quipe m\u00e9dicale coordonn\u00e9e, qui adapte au mieux le parcours en fonction de l\u2019\u00e9volution<a href=\"https:\/\/www.afm-telethon.fr\/fr\/fiches-maladies\/dystrophie-musculaire-de-becker\">(1)<\/a>. Cela comprend :<\/p><ul><li><a href=\"https:\/\/orthopus.com\/fr\/professionnels-de-sante\/kine-pour-neuropathie\/\">Kin\u00e9sith\u00e9rapie<\/a> r\u00e9guli\u00e8re<\/li><li>Orthophonie<\/li><li>Cardiologie<\/li><li>Pneumologie<\/li><\/ul><p>La fr\u00e9quence et l\u2019intensit\u00e9 des soins sont ajust\u00e9es \u00e0 chaque \u00e9tape de la maladie.<\/p>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t<div class=\"elementor-element elementor-element-135d544 e-con-full e-flex e-con e-parent\" data-id=\"135d544\" data-element_type=\"container\" data-e-type=\"container\" data-settings=\"{&quot;jet_parallax_layout_list&quot;:[]}\">\n\t\t\t\t<div class=\"elementor-element elementor-element-1ead9f9 elementor-widget elementor-widget-image\" data-id=\"1ead9f9\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"image.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t\t\t\t\t\t\t<img decoding=\"async\" width=\"800\" height=\"450\" src=\"https:\/\/orthopus.com\/wp-content\/uploads\/2025\/08\/parcours-de-soins-dystrophie-musculaire-becker-1.jpg\" class=\"attachment-full size-full wp-image-17406\" alt=\"\" srcset=\"https:\/\/orthopus.com\/wp-content\/uploads\/2025\/08\/parcours-de-soins-dystrophie-musculaire-becker-1.jpg 800w, https:\/\/orthopus.com\/wp-content\/uploads\/2025\/08\/parcours-de-soins-dystrophie-musculaire-becker-1-300x169.jpg 300w, https:\/\/orthopus.com\/wp-content\/uploads\/2025\/08\/parcours-de-soins-dystrophie-musculaire-becker-1-768x432.jpg 768w, https:\/\/orthopus.com\/wp-content\/uploads\/2025\/08\/parcours-de-soins-dystrophie-musculaire-becker-1-150x85.jpg 150w, https:\/\/orthopus.com\/wp-content\/uploads\/2025\/08\/parcours-de-soins-dystrophie-musculaire-becker-1-600x338.jpg 600w, https:\/\/orthopus.com\/wp-content\/uploads\/2025\/08\/parcours-de-soins-dystrophie-musculaire-becker-1-200x113.jpg 200w\" sizes=\"(max-width: 800px) 100vw, 800px\" \/>\t\t\t\t\t\t\t\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t<div class=\"elementor-element elementor-element-ff8f87d e-flex e-con-boxed e-con e-parent\" data-id=\"ff8f87d\" data-element_type=\"container\" data-e-type=\"container\" data-settings=\"{&quot;jet_parallax_layout_list&quot;:[]}\">\n\t\t\t\t\t<div class=\"e-con-inner\">\n\t\t\t\t<div class=\"elementor-element elementor-element-d21f402 elementor-widget elementor-widget-spacer\" data-id=\"d21f402\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"spacer.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t<div class=\"elementor-spacer\">\n\t\t\t<div class=\"elementor-spacer-inner\"><\/div>\n\t\t<\/div>\n\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t<div class=\"elementor-element elementor-element-b3ad26b e-flex e-con-boxed e-con e-parent\" data-id=\"b3ad26b\" data-element_type=\"container\" data-e-type=\"container\" data-settings=\"{&quot;jet_parallax_layout_list&quot;:[]}\">\n\t\t\t\t\t<div class=\"e-con-inner\">\n\t\t\t\t<div class=\"elementor-element elementor-element-0155a4c elementor-widget elementor-widget-heading\" data-id=\"0155a4c\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"heading.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t<h3 class=\"elementor-heading-title elementor-size-default\">Innovations technologiques dans le traitement<\/h3>\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t<div class=\"elementor-element elementor-element-631213f e-flex e-con-boxed e-con e-parent\" data-id=\"631213f\" data-element_type=\"container\" data-e-type=\"container\" data-settings=\"{&quot;jet_parallax_layout_list&quot;:[]}\">\n\t\t\t\t\t<div class=\"e-con-inner\">\n\t\t\t\t<div class=\"elementor-element elementor-element-a6db215 elementor-widget elementor-widget-text-editor\" data-id=\"a6db215\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<p>Les solutions technologiques prennent une place importante dans la prise en charge de la Dystrophie musculaire de Becker. Plusieurs <a href=\"https:\/\/orthopus.com\/fr\/aide-technique\/robot-assistance-compensation\/\">innovations<\/a> facilitent le quotidien :<\/p><ul><li><a href=\"https:\/\/orthopus.com\/fr\/gamme-assistants-robotiques-pour-la-mobilite-du-bras\/\">Dispositifs robotiques d\u2019assistance<\/a><\/li><li>Exosquelettes<\/li><li>Interfaces num\u00e9riques<\/li><\/ul><p><strong>Avantages des technologies d\u2019assistance :<\/strong><\/p><p>\u00a0<\/p><ul><li>Compensation des pertes fonctionnelles<\/li><li>R\u00e9duction de l\u2019effort musculaire<\/li><li>Maintien de l\u2019autonomie dans les gestes du quotidien<\/li><li>Adaptation \u00e9volutive selon le stade de la maladie<\/li><\/ul><p>Ces innovations ne remplacent pas les traitements m\u00e9dicaux, mais elles les compl\u00e8tent efficacement et am\u00e9liorent consid\u00e9rablement la qualit\u00e9 de vie.<\/p><p>Chez ORTHOPUS, nous concevons des solutions robotiques qui permettent aux personnes en situation de handicap de retrouver une certaine partie de leur autonomie : manger seul, travailler sur un ordinateur ou interagir plus facilement avec leur environnement et leur entourage.<\/p>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t<div class=\"elementor-element elementor-element-b236e2c e-flex e-con-boxed e-con e-parent\" data-id=\"b236e2c\" data-element_type=\"container\" data-e-type=\"container\" data-settings=\"{&quot;jet_parallax_layout_list&quot;:[]}\">\n\t\t\t\t\t<div class=\"e-con-inner\">\n\t\t\t\t<div class=\"elementor-element elementor-element-0c3e72e elementor-widget elementor-widget-spacer\" data-id=\"0c3e72e\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"spacer.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t<div class=\"elementor-spacer\">\n\t\t\t<div class=\"elementor-spacer-inner\"><\/div>\n\t\t<\/div>\n\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t<div class=\"elementor-element elementor-element-db56cf3 e-flex e-con-boxed e-con e-parent\" data-id=\"db56cf3\" data-element_type=\"container\" data-e-type=\"container\" data-settings=\"{&quot;jet_parallax_layout_list&quot;:[]}\">\n\t\t\t\t\t<div class=\"e-con-inner\">\n\t\t\t\t<div class=\"elementor-element elementor-element-e9c2380 elementor-widget elementor-widget-heading\" data-id=\"e9c2380\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"heading.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t<h2 class=\"elementor-heading-title elementor-size-default\">Perspectives futures et recherche sur la dystrophie musculaire de Becker<\/h2>\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t<div class=\"elementor-element elementor-element-375179d e-flex e-con-boxed e-con e-parent\" data-id=\"375179d\" data-element_type=\"container\" data-e-type=\"container\" data-settings=\"{&quot;jet_parallax_layout_list&quot;:[]}\">\n\t\t\t\t\t<div class=\"e-con-inner\">\n\t\t\t\t<div class=\"elementor-element elementor-element-eec367a elementor-widget elementor-widget-text-editor\" data-id=\"eec367a\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<p data-block-id=\"ed527323-a12d-4b36-bc8c-56cbb0035707\" data-pm-slice=\"1 1 []\">La <strong><a href=\"https:\/\/orthopus.com\/fr\/maladies-neuromusculaires\/traitement-maladie-neuromusculaire\/\">recherche<\/a> sur la dystrophie musculaire de Becker a fait des avanc\u00e9es consid\u00e9rables<\/strong>. Actuellement, on parvient \u00e0 freiner l&#8217;\u00e9volution de la maladie avec les traitements disponibles. N\u00e9anmoins, l&#8217;objectif des \u00e9quipes de chercheur\u2022euses est de corriger la cause g\u00e9n\u00e9tique, afin de restaurer la fonction du muscle.<\/p><p data-block-id=\"08a259eb-c894-436f-8939-0168d0d14dbd\">Les progr\u00e8s des derni\u00e8res ann\u00e9es sont remarquables, comme le montre le travail sur la g\u00e9nomique (\u00e9tude du patrimoine g\u00e9n\u00e9tique d\u2019un organisme), la biotechnologie (qui consiste \u00e0 exploiter des cellules pour la fabrication de produits m\u00e9dicaux utiles \u00e0 l\u2019Homme) ou encore l\u2019intelligence artificielle.<\/p>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t<div class=\"elementor-element elementor-element-d847856 e-flex e-con-boxed e-con e-parent\" data-id=\"d847856\" data-element_type=\"container\" data-e-type=\"container\" data-settings=\"{&quot;jet_parallax_layout_list&quot;:[]}\">\n\t\t\t\t\t<div class=\"e-con-inner\">\n\t\t\t\t<div class=\"elementor-element elementor-element-4eee242 elementor-widget elementor-widget-image\" data-id=\"4eee242\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"image.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t\t\t\t\t\t\t<img loading=\"lazy\" decoding=\"async\" width=\"768\" height=\"432\" src=\"https:\/\/orthopus.com\/wp-content\/uploads\/2025\/08\/Progres-des-dernieres-annees-768x432.webp\" class=\"attachment-medium_large size-medium_large wp-image-17279\" alt=\"\" srcset=\"https:\/\/orthopus.com\/wp-content\/uploads\/2025\/08\/Progres-des-dernieres-annees-768x432.webp 768w, https:\/\/orthopus.com\/wp-content\/uploads\/2025\/08\/Progres-des-dernieres-annees-300x169.webp 300w, https:\/\/orthopus.com\/wp-content\/uploads\/2025\/08\/Progres-des-dernieres-annees-1024x576.webp 1024w, https:\/\/orthopus.com\/wp-content\/uploads\/2025\/08\/Progres-des-dernieres-annees-1536x864.webp 1536w, https:\/\/orthopus.com\/wp-content\/uploads\/2025\/08\/Progres-des-dernieres-annees-2048x1152.webp 2048w, https:\/\/orthopus.com\/wp-content\/uploads\/2025\/08\/Progres-des-dernieres-annees-150x85.webp 150w, https:\/\/orthopus.com\/wp-content\/uploads\/2025\/08\/Progres-des-dernieres-annees-1920x1080.webp 1920w, https:\/\/orthopus.com\/wp-content\/uploads\/2025\/08\/Progres-des-dernieres-annees-600x338.webp 600w, https:\/\/orthopus.com\/wp-content\/uploads\/2025\/08\/Progres-des-dernieres-annees-200x113.webp 200w\" sizes=\"(max-width: 768px) 100vw, 768px\" \/>\t\t\t\t\t\t\t\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t<div class=\"elementor-element elementor-element-c1b87a6 e-flex e-con-boxed e-con e-parent\" data-id=\"c1b87a6\" data-element_type=\"container\" data-e-type=\"container\" data-settings=\"{&quot;jet_parallax_layout_list&quot;:[]}\">\n\t\t\t\t\t<div class=\"e-con-inner\">\n\t\t\t\t<div class=\"elementor-element elementor-element-ac593fe elementor-widget elementor-widget-spacer\" data-id=\"ac593fe\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"spacer.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t<div class=\"elementor-spacer\">\n\t\t\t<div class=\"elementor-spacer-inner\"><\/div>\n\t\t<\/div>\n\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t<div class=\"elementor-element elementor-element-5ab4cdb e-flex e-con-boxed e-con e-parent\" data-id=\"5ab4cdb\" data-element_type=\"container\" data-e-type=\"container\" data-settings=\"{&quot;jet_parallax_layout_list&quot;:[]}\">\n\t\t\t\t\t<div class=\"e-con-inner\">\n\t\t\t\t<div class=\"elementor-element elementor-element-a55ae13 elementor-widget elementor-widget-heading\" data-id=\"a55ae13\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"heading.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t<h3 class=\"elementor-heading-title elementor-size-default\">Avanc\u00e9es en recherche g\u00e9n\u00e9tique et m\u00e9dicamenteuse<\/h3>\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t<div class=\"elementor-element elementor-element-8c85bd2 e-flex e-con-boxed e-con e-parent\" data-id=\"8c85bd2\" data-element_type=\"container\" data-e-type=\"container\" data-settings=\"{&quot;jet_parallax_layout_list&quot;:[]}\">\n\t\t\t\t\t<div class=\"e-con-inner\">\n\t\t\t\t<div class=\"elementor-element elementor-element-fd2ef5a elementor-widget elementor-widget-text-editor\" data-id=\"fd2ef5a\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<p>Les laboratoires sp\u00e9cialis\u00e9s dans les maladies neuromusculaires travaillent sur diff\u00e9rentes approches innovantes :<\/p><ul><li><strong>Th\u00e9rapie g\u00e9nique :<\/strong> introduire une copie fonctionnelle du g\u00e8ne DMD dans les cellules musculaires par l\u2019interm\u00e9diaire d\u2019un vecteur viral (virus modifi\u00e9, servant \u00e0 transporter un g\u00e8ne \u00e0 l\u2019int\u00e9rieur des cellules). Cela permet la production d\u2019une dystrophine miniature, mais fonctionnelle.<\/li><li><strong>Exon skipping :<\/strong> technique qui masque une partie d\u2019un g\u00e8ne mut\u00e9 pour r\u00e9tablir une lecture partielle correcte du g\u00e8ne. Cela permet la synth\u00e8se d\u2019une dystrophine plus stable.<\/li><li><strong>\u00c9dition du g\u00e9nome (CRISPR-Cas9) :<\/strong> modification directe de l\u2019ADN d\u00e9fectueux. Bien que prometteuse, cette technique n\u00e9cessite des validations suppl\u00e9mentaires pour garantir sa s\u00e9curit\u00e9. En effet, parfois, CRISPR coupe au mauvais endroit dans l\u2019ADN, ce qui pourrait provoquer d\u2019autres probl\u00e8mes (ou mutations non voulues : effets &#8220;hors cible&#8221;). De plus, une fois l\u2019ADN sectionn\u00e9, le corps doit le r\u00e9parer, mais cette \u00e9tape peut \u00eatre impr\u00e9visible et ne pas toujours bien fonctionner. On ne sait pas encore comment les cellules modifi\u00e9es vont r\u00e9agir avec le temps. Il faut s\u2019assurer qu\u2019il n\u2019y ait ni inflammation, ni cancer, ni autres complications des ann\u00e9es plus tard. Sur un registre similaire, on ne sait pas si la modification touche des cellules reproductrices (spermatozo\u00efdes ou ovules), les changements pourraient \u00eatre transmis aux enfants, ce qui pose des questions \u00e9thiques importantes.<\/li><li><strong>Mol\u00e9cules pharmacologiques cibl\u00e9es :<\/strong> certains m\u00e9dicaments visent \u00e0 stimuler la production naturelle de dystrophine ou \u00e0 prot\u00e9ger les muscles des processus d\u00e9g\u00e9n\u00e9ratifs.<\/li><\/ul><p>Ces recherches ouvrent de r\u00e9elles perspectives, malgr\u00e9 l\u2019absence actuelle de traitements curatifs disponibles sur le march\u00e9.<\/p>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t<div class=\"elementor-element elementor-element-59717cc e-flex e-con-boxed e-con e-parent\" data-id=\"59717cc\" data-element_type=\"container\" data-e-type=\"container\" data-settings=\"{&quot;jet_parallax_layout_list&quot;:[]}\">\n\t\t\t\t\t<div class=\"e-con-inner\">\n\t\t\t\t<div class=\"elementor-element elementor-element-62f36c8 elementor-widget elementor-widget-spacer\" data-id=\"62f36c8\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"spacer.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t<div class=\"elementor-spacer\">\n\t\t\t<div class=\"elementor-spacer-inner\"><\/div>\n\t\t<\/div>\n\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t<div class=\"elementor-element elementor-element-2eaffaa e-flex e-con-boxed e-con e-parent\" data-id=\"2eaffaa\" data-element_type=\"container\" data-e-type=\"container\" data-settings=\"{&quot;jet_parallax_layout_list&quot;:[]}\">\n\t\t\t\t\t<div class=\"e-con-inner\">\n\t\t\t\t<div class=\"elementor-element elementor-element-83f9fa0 elementor-widget elementor-widget-heading\" data-id=\"83f9fa0\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"heading.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t<h2 class=\"elementor-heading-title elementor-size-default\">Quelles aides financi\u00e8res pour les personnes atteintes de la DMB ?<\/h2>\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t<div class=\"elementor-element elementor-element-2e56c11 e-flex e-con-boxed e-con e-parent\" data-id=\"2e56c11\" data-element_type=\"container\" data-e-type=\"container\" data-settings=\"{&quot;jet_parallax_layout_list&quot;:[]}\">\n\t\t\t\t\t<div class=\"e-con-inner\">\n\t\t\t\t<div class=\"elementor-element elementor-element-560531b elementor-widget elementor-widget-text-editor\" data-id=\"560531b\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<p>Les co\u00fbts des soins, des \u00e9quipements sp\u00e9cialis\u00e9s ou encore des adaptations du logement ou du v\u00e9hicule peuvent \u00eatre \u00e9lev\u00e9s. Plusieurs <a href=\"https:\/\/orthopus.com\/fr\/aides-financieres\/aides-financieres-handicap\/\">dispositifs<\/a> existent pour accompagner les familles dans cette gestion financi\u00e8re.<\/p>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t<div class=\"elementor-element elementor-element-07653fc e-flex e-con-boxed e-con e-parent\" data-id=\"07653fc\" data-element_type=\"container\" data-e-type=\"container\" data-settings=\"{&quot;jet_parallax_layout_list&quot;:[]}\">\n\t\t\t\t\t<div class=\"e-con-inner\">\n\t\t\t\t<div class=\"elementor-element elementor-element-123d65c elementor-widget elementor-widget-spacer\" data-id=\"123d65c\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"spacer.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t<div class=\"elementor-spacer\">\n\t\t\t<div class=\"elementor-spacer-inner\"><\/div>\n\t\t<\/div>\n\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t<div class=\"elementor-element elementor-element-999393f e-flex e-con-boxed e-con e-parent\" data-id=\"999393f\" data-element_type=\"container\" data-e-type=\"container\" data-settings=\"{&quot;jet_parallax_layout_list&quot;:[]}\">\n\t\t\t\t\t<div class=\"e-con-inner\">\n\t\t\t\t<div class=\"elementor-element elementor-element-b57384e elementor-widget elementor-widget-heading\" data-id=\"b57384e\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"heading.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t<h3 class=\"elementor-heading-title elementor-size-default\">Prise en charge m\u00e9dicale et allocations<\/h3>\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t<div class=\"elementor-element elementor-element-dc5c487 e-flex e-con-boxed e-con e-parent\" data-id=\"dc5c487\" data-element_type=\"container\" data-e-type=\"container\" data-settings=\"{&quot;jet_parallax_layout_list&quot;:[]}\">\n\t\t\t\t\t<div class=\"e-con-inner\">\n\t\t\t\t<div class=\"elementor-element elementor-element-bbf682f elementor-widget elementor-widget-text-editor\" data-id=\"bbf682f\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\tLes personnes vivant avec une Dystrophie musculaire de Becker peuvent b\u00e9n\u00e9ficier d\u2019aides sp\u00e9cifiques :\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t<section class=\"elementor-section elementor-top-section elementor-element elementor-element-a1d2c25 elementor-hidden-tablet elementor-hidden-mobile elementor-section-boxed elementor-section-height-default elementor-section-height-default\" data-id=\"a1d2c25\" data-element_type=\"section\" data-e-type=\"section\" data-settings=\"{&quot;jet_parallax_layout_list&quot;:[],&quot;background_background&quot;:&quot;classic&quot;}\">\n\t\t\t\t\t\t<div class=\"elementor-container elementor-column-gap-default\">\n\t\t\t\t\t<div class=\"elementor-column elementor-col-33 elementor-top-column elementor-element elementor-element-6274fc0\" data-id=\"6274fc0\" data-element_type=\"column\" data-e-type=\"column\" data-settings=\"{&quot;background_background&quot;:&quot;classic&quot;}\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-45e0310 elementor-widget elementor-widget-text-editor\" data-id=\"45e0310\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<strong>Aide \/ dispositif<\/strong>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t<div class=\"elementor-column elementor-col-33 elementor-top-column elementor-element elementor-element-0641204\" data-id=\"0641204\" data-element_type=\"column\" data-e-type=\"column\" data-settings=\"{&quot;background_background&quot;:&quot;classic&quot;}\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-c835e31 elementor-widget elementor-widget-text-editor\" data-id=\"c835e31\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<strong>D\u00e9tail<\/strong>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t<div class=\"elementor-column elementor-col-33 elementor-top-column elementor-element elementor-element-c668621\" data-id=\"c668621\" data-element_type=\"column\" data-e-type=\"column\" data-settings=\"{&quot;background_background&quot;:&quot;classic&quot;}\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-c8ac598 elementor-widget elementor-widget-text-editor\" data-id=\"c8ac598\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<strong>Organisme concern\u00e9<\/strong>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/section>\n\t\t\t\t<section class=\"elementor-section elementor-top-section elementor-element elementor-element-5944b30 elementor-hidden-tablet elementor-hidden-mobile elementor-section-boxed elementor-section-height-default elementor-section-height-default\" data-id=\"5944b30\" data-element_type=\"section\" data-e-type=\"section\" data-settings=\"{&quot;jet_parallax_layout_list&quot;:[]}\">\n\t\t\t\t\t\t<div class=\"elementor-container elementor-column-gap-default\">\n\t\t\t\t\t<div class=\"elementor-column elementor-col-33 elementor-top-column elementor-element elementor-element-05600d5\" data-id=\"05600d5\" data-element_type=\"column\" data-e-type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-416c09d elementor-widget elementor-widget-text-editor\" data-id=\"416c09d\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<p><a href=\"https:\/\/www.ameli.fr\/assure\">ALD<\/a> (Affection Longue Dur\u00e9e)<\/p>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t<div class=\"elementor-column elementor-col-33 elementor-top-column elementor-element elementor-element-d578b95\" data-id=\"d578b95\" data-element_type=\"column\" data-e-type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-878ccf2 elementor-widget elementor-widget-text-editor\" data-id=\"878ccf2\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<p>Remboursement \u00e0 100% des soins li\u00e9s \u00e0 la DMB<\/p>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t<div class=\"elementor-column elementor-col-33 elementor-top-column elementor-element elementor-element-57c0738\" data-id=\"57c0738\" data-element_type=\"column\" data-e-type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-7abed84 elementor-widget elementor-widget-text-editor\" data-id=\"7abed84\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<p><a href=\"https:\/\/www.ameli.fr\/assure\">S\u00e9curit\u00e9 Sociale<\/a><\/p>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/section>\n\t\t\t\t<section class=\"elementor-section elementor-top-section elementor-element elementor-element-fb69448 elementor-hidden-tablet elementor-hidden-mobile elementor-section-boxed elementor-section-height-default elementor-section-height-default\" data-id=\"fb69448\" data-element_type=\"section\" data-e-type=\"section\" data-settings=\"{&quot;jet_parallax_layout_list&quot;:[]}\">\n\t\t\t\t\t\t<div class=\"elementor-container elementor-column-gap-default\">\n\t\t\t\t\t<div class=\"elementor-column elementor-col-33 elementor-top-column elementor-element elementor-element-1050905\" data-id=\"1050905\" data-element_type=\"column\" data-e-type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-8d51e2c elementor-widget elementor-widget-text-editor\" data-id=\"8d51e2c\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<p><a href=\"https:\/\/caf.fr\/\">AAH<\/a> (Allocation Adulte Handicap\u00e9)<\/p>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t<div class=\"elementor-column elementor-col-33 elementor-top-column elementor-element elementor-element-a757e07\" data-id=\"a757e07\" data-element_type=\"column\" data-e-type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-54ed10f elementor-widget elementor-widget-text-editor\" data-id=\"54ed10f\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\tSoutien mensuel pour les adultes avec perte d&#8217;autonomie\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t<div class=\"elementor-column elementor-col-33 elementor-top-column elementor-element elementor-element-ec5aa03\" data-id=\"ec5aa03\" data-element_type=\"column\" data-e-type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-bc3cbe0 elementor-widget elementor-widget-text-editor\" data-id=\"bc3cbe0\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<p><a href=\"https:\/\/caf.fr\/\">CAF<\/a><\/p>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/section>\n\t\t\t\t<section class=\"elementor-section elementor-top-section elementor-element elementor-element-874279d elementor-hidden-tablet elementor-hidden-mobile elementor-section-boxed elementor-section-height-default elementor-section-height-default\" data-id=\"874279d\" data-element_type=\"section\" data-e-type=\"section\" data-settings=\"{&quot;jet_parallax_layout_list&quot;:[]}\">\n\t\t\t\t\t\t<div class=\"elementor-container elementor-column-gap-default\">\n\t\t\t\t\t<div class=\"elementor-column elementor-col-33 elementor-top-column elementor-element elementor-element-27980b7\" data-id=\"27980b7\" data-element_type=\"column\" data-e-type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-a629320 elementor-widget elementor-widget-text-editor\" data-id=\"a629320\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<p><a href=\"https:\/\/mdphenligne.cnsa.fr\/\">PCH<\/a> (Prestation de Compensation du Handicap)<\/p>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t<div class=\"elementor-column elementor-col-33 elementor-top-column elementor-element elementor-element-68cc8dd\" data-id=\"68cc8dd\" data-element_type=\"column\" data-e-type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-fc17006 elementor-widget elementor-widget-text-editor\" data-id=\"fc17006\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\tAide pour financer les \u00e9quipements, aides humaines, logements\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t<div class=\"elementor-column elementor-col-33 elementor-top-column elementor-element elementor-element-9fa6321\" data-id=\"9fa6321\" data-element_type=\"column\" data-e-type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-9ab5cbf elementor-widget elementor-widget-text-editor\" data-id=\"9ab5cbf\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<p><a href=\"https:\/\/mdphenligne.cnsa.fr\/\">MDPH<\/a><\/p>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/section>\n\t\t\t\t<section class=\"elementor-section elementor-top-section elementor-element elementor-element-cbd4082 elementor-hidden-tablet elementor-hidden-mobile elementor-section-boxed elementor-section-height-default elementor-section-height-default\" data-id=\"cbd4082\" data-element_type=\"section\" data-e-type=\"section\" data-settings=\"{&quot;jet_parallax_layout_list&quot;:[]}\">\n\t\t\t\t\t\t<div class=\"elementor-container elementor-column-gap-default\">\n\t\t\t\t\t<div class=\"elementor-column elementor-col-33 elementor-top-column elementor-element elementor-element-3e382f1\" data-id=\"3e382f1\" data-element_type=\"column\" data-e-type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-cf28467 elementor-widget elementor-widget-text-editor\" data-id=\"cf28467\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\tCarte Mobilit\u00e9 Inclusion\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t<div class=\"elementor-column elementor-col-33 elementor-top-column elementor-element elementor-element-139053c\" data-id=\"139053c\" data-element_type=\"column\" data-e-type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-ca57922 elementor-widget elementor-widget-text-editor\" data-id=\"ca57922\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\tPriorit\u00e9 dans les transports stationnement facilit\u00e9\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t<div class=\"elementor-column elementor-col-33 elementor-top-column elementor-element elementor-element-b8a3bac\" data-id=\"b8a3bac\" data-element_type=\"column\" data-e-type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-7ad7f61 elementor-widget elementor-widget-text-editor\" data-id=\"7ad7f61\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\tConseil D\u00e9partemental\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/section>\n\t\t<div class=\"elementor-element elementor-element-fa74cb2 elementor-hidden-desktop elementor-hidden-tablet e-flex e-con-boxed e-con e-parent\" data-id=\"fa74cb2\" data-element_type=\"container\" data-e-type=\"container\" data-settings=\"{&quot;jet_parallax_layout_list&quot;:[]}\">\n\t\t\t\t\t<div class=\"e-con-inner\">\n\t\t\t\t<div class=\"elementor-element elementor-element-0a9edaa elementor-widget elementor-widget-jet-table\" data-id=\"0a9edaa\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"jet-table.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t<div class=\"elementor-jet-table jet-elements\">\n\t\t<div class=\"jet-table-wrapper jet-table-responsive-tablet jet-table-responsive-mobile\">\n\t\t\t<table class=\"jet-table jet-table--fa5-compat\">\n\t\t\t\t<thead class=\"jet-table__head\"><tr class=\"jet-table__head-row\"><th class=\"jet-table__cell elementor-repeater-item-83d94a3 jet-table__head-cell\" colspan=\"1\" scope=\"col\"><div class=\"jet-table__cell-inner\"><div class=\"jet-table__cell-content\"><div class=\"jet-table__cell-text\">Aide \/ dispositif <\/div><\/div><\/div><\/th><th class=\"jet-table__cell elementor-repeater-item-493e60a jet-table__head-cell\" colspan=\"1\" scope=\"col\"><div class=\"jet-table__cell-inner\"><div class=\"jet-table__cell-content\"><div class=\"jet-table__cell-text\">D\u00e9tail<\/div><\/div><\/div><\/th><th class=\"jet-table__cell elementor-repeater-item-81ee20e jet-table__head-cell\" colspan=\"1\" scope=\"col\"><div class=\"jet-table__cell-inner\"><div class=\"jet-table__cell-content\"><div class=\"jet-table__cell-text\">Organisme concern\u00e9<\/div><\/div><\/div><\/th><\/tr><\/thead>\n\t\t\t\t\t\t\t\t<tbody class=\"jet-table__body\"><td class=\"jet-table__cell elementor-repeater-item-758ae34 jet-table__body-cell\" colspan=\"1\"><div class=\"jet-table__cell-inner\"><div class=\"jet-table__cell-content\"><div class=\"jet-table__cell-text\">ALD (Affection Longue Dur\u00e9e)<\/div><\/div><\/div><\/td><td class=\"jet-table__cell elementor-repeater-item-7bfd3f6 jet-table__body-cell\"><div class=\"jet-table__cell-inner\"><div class=\"jet-table__cell-content\"><div class=\"jet-table__cell-text\">Remboursement \u00e0 100% des soins li\u00e9s \u00e0 la DMB<\/div><\/div><\/div><\/td><td class=\"jet-table__cell elementor-repeater-item-53caccc jet-table__body-cell\"><div class=\"jet-table__cell-inner\"><div class=\"jet-table__cell-content\"><div class=\"jet-table__cell-text\">S\u00e9curit\u00e9 Sociale<\/div><\/div><\/div><\/td><tr class=\"jet-table__body-row elementor-repeater-item-b832156\"><td class=\"jet-table__cell elementor-repeater-item-ea4dd97 jet-table__body-cell\"><div class=\"jet-table__cell-inner\"><div class=\"jet-table__cell-content\"><div class=\"jet-table__cell-text\">AAH (Allocation Adulte Handicap\u00e9)<\/div><\/div><\/div><\/td><td class=\"jet-table__cell elementor-repeater-item-7da20ee jet-table__body-cell\"><div class=\"jet-table__cell-inner\"><div class=\"jet-table__cell-content\"><div class=\"jet-table__cell-text\">Soutien mensuel pour les adultes avec perte d&#8217;autonomie<\/div><\/div><\/div><\/td><td class=\"jet-table__cell elementor-repeater-item-fc93119 jet-table__body-cell\"><div class=\"jet-table__cell-inner\"><div class=\"jet-table__cell-content\"><div class=\"jet-table__cell-text\">CAF<\/div><\/div><\/div><\/td><\/tr><tr class=\"jet-table__body-row elementor-repeater-item-4c7a82b\"><td class=\"jet-table__cell elementor-repeater-item-7a286be jet-table__body-cell\"><div class=\"jet-table__cell-inner\"><div class=\"jet-table__cell-content\"><div class=\"jet-table__cell-text\">PCH (Prestation de Compensation du Handicap)<\/div><\/div><\/div><\/td><td class=\"jet-table__cell elementor-repeater-item-41d85bc jet-table__body-cell\"><div class=\"jet-table__cell-inner\"><div class=\"jet-table__cell-content\"><div class=\"jet-table__cell-text\">Aide pour financer les \u00e9quipements, aides humaines, logements<\/div><\/div><\/div><\/td><td class=\"jet-table__cell elementor-repeater-item-6f3049d jet-table__body-cell\"><div class=\"jet-table__cell-inner\"><div class=\"jet-table__cell-content\"><div class=\"jet-table__cell-text\">MDPH<\/div><\/div><\/div><\/td><\/tr><tr class=\"jet-table__body-row elementor-repeater-item-0d8a535\"><td class=\"jet-table__cell elementor-repeater-item-2d80336 jet-table__body-cell\"><div class=\"jet-table__cell-inner\"><div class=\"jet-table__cell-content\"><div class=\"jet-table__cell-text\">Carte Mobilit\u00e9 Inclusion<\/div><\/div><\/div><\/td><td class=\"jet-table__cell elementor-repeater-item-8238817 jet-table__body-cell\"><div class=\"jet-table__cell-inner\"><div class=\"jet-table__cell-content\"><div class=\"jet-table__cell-text\">Priorit\u00e9 dans les transports, stationnement facilit\u00e9<\/div><\/div><\/div><\/td><td class=\"jet-table__cell elementor-repeater-item-0879855 jet-table__body-cell\"><div class=\"jet-table__cell-inner\"><div class=\"jet-table__cell-content\"><div class=\"jet-table__cell-text\">Conseil D\u00e9partemental<\/div><\/div><\/div><\/td><\/tr><\/tbody>\n\t\t\t<\/table>\n\t\t<\/div>\n\n\t\t<\/div>\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t<div class=\"elementor-element elementor-element-bd35d35 e-flex e-con-boxed e-con e-parent\" data-id=\"bd35d35\" data-element_type=\"container\" data-e-type=\"container\" data-settings=\"{&quot;jet_parallax_layout_list&quot;:[]}\">\n\t\t\t\t\t<div class=\"e-con-inner\">\n\t\t\t\t<div class=\"elementor-element elementor-element-0899cc0 elementor-widget elementor-widget-text-editor\" data-id=\"0899cc0\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\tCes dispositifs sont soumis \u00e0 conditions d\u2019\u00e9ligibilit\u00e9, bas\u00e9es sur le niveau de handicap, l\u2019\u00e2ge et sa situation familiale.\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t<div class=\"elementor-element elementor-element-ca92f14 e-flex e-con-boxed e-con e-parent\" data-id=\"ca92f14\" data-element_type=\"container\" data-e-type=\"container\" data-settings=\"{&quot;jet_parallax_layout_list&quot;:[]}\">\n\t\t\t\t\t<div class=\"e-con-inner\">\n\t\t\t\t<div class=\"elementor-element elementor-element-0f48ae6 elementor-widget elementor-widget-spacer\" data-id=\"0f48ae6\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"spacer.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t<div class=\"elementor-spacer\">\n\t\t\t<div class=\"elementor-spacer-inner\"><\/div>\n\t\t<\/div>\n\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t<div class=\"elementor-element elementor-element-1403dae e-flex e-con-boxed e-con e-parent\" data-id=\"1403dae\" data-element_type=\"container\" data-e-type=\"container\" data-settings=\"{&quot;jet_parallax_layout_list&quot;:[]}\">\n\t\t\t\t\t<div class=\"e-con-inner\">\n\t\t\t\t<div class=\"elementor-element elementor-element-8f84392 elementor-widget elementor-widget-heading\" data-id=\"8f84392\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"heading.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t<h3 class=\"elementor-heading-title elementor-size-default\">Financement des \u00e9quipements et aides techniques<\/h3>\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t<div class=\"elementor-element elementor-element-8d6ea92 e-flex e-con-boxed e-con e-parent\" data-id=\"8d6ea92\" data-element_type=\"container\" data-e-type=\"container\" data-settings=\"{&quot;jet_parallax_layout_list&quot;:[]}\">\n\t\t\t\t\t<div class=\"e-con-inner\">\n\t\t\t\t<div class=\"elementor-element elementor-element-64d1652 elementor-widget elementor-widget-text-editor\" data-id=\"64d1652\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<p>Les dispositifs d\u2019\u00e9quipements tels que <strong>les <a href=\"https:\/\/orthopus.com\/fr\/aides-financieres\/aide-pour-fauteuil-roulant\/\">fauteuils roulants<\/a> \u00e9lectriques, les lits m\u00e9dicalis\u00e9s, <a href=\"https:\/\/orthopus.com\/fr\/aide-technique\/bras-robotique-handicap-orthopus\/\">les bras robotiques<\/a> ou les logiciels de commande vocale<\/strong> peuvent b\u00e9n\u00e9ficier d\u2019une prise en charge partielle.<\/p><p>Sources de financement possibles :<\/p><ul><li>Compl\u00e9mentaire sant\u00e9 \/ mutuelle<\/li><li>Fonds d\u00e9partementaux (dans le cadre de la MDPH)<\/li><li>Associations : comme l\u2019<a href=\"https:\/\/www.afm-telethon.fr\/fr\">AFM-T\u00e9l\u00e9thon<\/a>, <a href=\"https:\/\/www.apf-francehandicap.org\/\">APF France Handicap<\/a>, etc.<\/li><li>Crowdfunding solidaire : plateformes comme <a href=\"http:\/\/leetchi.com\/?utm_source=google&amp;utm_medium=cpc&amp;utm_campaign=lca_marque_leetchi&amp;utm_term=search_brand&amp;gad_source=1&amp;gbraid=0AAAAADxO86qWVNFm7ph7KSY3S3BuJstB4&amp;gclid=Cj0KCQjw_JzABhC2ARIsAPe3ynrpR-sH87-3D3yTZ7FXYcQkiUl_ZFmidfjksS32xOk2_B3mr0IGhBoaAlRIEALw_wcB\">Leetchi<\/a> ou <a href=\"https:\/\/www.gofundme.com\/fr-fr\">GoFundMe<\/a><\/li><\/ul>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t<div class=\"elementor-element elementor-element-ca8d10e e-flex e-con-boxed e-con e-parent\" data-id=\"ca8d10e\" data-element_type=\"container\" data-e-type=\"container\" data-settings=\"{&quot;jet_parallax_layout_list&quot;:[]}\">\n\t\t\t\t\t<div class=\"e-con-inner\">\n\t\t\t\t<div class=\"elementor-element elementor-element-d55fd04 elementor-align-center elementor-widget elementor-widget-button\" data-id=\"d55fd04\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"button.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<div class=\"elementor-button-wrapper\">\n\t\t\t\t\t<a class=\"elementor-button elementor-button-link elementor-size-sm elementor-animation-float\" href=\"https:\/\/orthopus.com\/fr\/financer-une-aide-technique-a-la-mobilite-du-bras\/\">\n\t\t\t\t\t\t<span class=\"elementor-button-content-wrapper\">\n\t\t\t\t\t\t\t\t\t<span class=\"elementor-button-text\">FINANCER UNE AIDE TECHNIQUE POUR LE BRAS<\/span>\n\t\t\t\t\t<\/span>\n\t\t\t\t\t<\/a>\n\t\t\t\t<\/div>\n\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t<div class=\"elementor-element elementor-element-19dee2c e-flex e-con-boxed e-con e-parent\" data-id=\"19dee2c\" data-element_type=\"container\" data-e-type=\"container\" data-settings=\"{&quot;jet_parallax_layout_list&quot;:[]}\">\n\t\t\t\t\t<div class=\"e-con-inner\">\n\t\t\t\t<div class=\"elementor-element elementor-element-28bef2f elementor-widget elementor-widget-text-editor\" data-id=\"28bef2f\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<p data-block-id=\"a4d46ce2-4adf-4a01-9a4e-2c6d9729f547\" data-pm-slice=\"1 1 []\">La dystrophie musculaire de Becker est une condition musculaire sp\u00e9cifique. Cependant, les progr\u00e8s scientifiques et technologiques ouvrent de nouvelles perspectives. Une prise en charge globale, un accompagnement personnalis\u00e9 et l\u2019acc\u00e8s \u00e0 des aides techniques et financi\u00e8res, am\u00e9liorent concr\u00e8tement la qualit\u00e9 de vie.<\/p><p data-block-id=\"6e876c03-7cf2-406a-baa2-a84f7249d6ce\">Les recherches en cours sur la dystrophine, la th\u00e9rapie g\u00e9nique et la robotique sont prometteuses. Elles laissent entrevoir un avenir plus autonome, plus confortable et plus apais\u00e9.<\/p><p data-block-id=\"211f7f5f-2e9b-4c96-9973-97dc1073e694\">Vivre avec la dystrophie musculaire de Becker ne consiste pas seulement \u00e0 s&#8217;adapter \u00e0 une pathologie \u00e9volutive. C\u2019est aussi pouvoir compter sur une cha\u00eene de soins, d\u2019innovations et de soutiens humains pour avancer jour apr\u00e8s jour.<\/p>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t<div class=\"elementor-element elementor-element-bb2d724 e-flex e-con-boxed e-con e-parent\" data-id=\"bb2d724\" data-element_type=\"container\" data-e-type=\"container\" data-settings=\"{&quot;jet_parallax_layout_list&quot;:[]}\">\n\t\t\t\t\t<div class=\"e-con-inner\">\n\t\t\t\t<div class=\"elementor-element elementor-element-3d9e2eb elementor-widget elementor-widget-spacer\" data-id=\"3d9e2eb\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"spacer.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t<div class=\"elementor-spacer\">\n\t\t\t<div class=\"elementor-spacer-inner\"><\/div>\n\t\t<\/div>\n\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t<div class=\"elementor-element elementor-element-537235e e-flex e-con-boxed e-con e-parent\" data-id=\"537235e\" data-element_type=\"container\" data-e-type=\"container\" data-settings=\"{&quot;jet_parallax_layout_list&quot;:[]}\">\n\t\t\t\t\t<div class=\"e-con-inner\">\n\t\t\t\t<div class=\"elementor-element elementor-element-38e4d1b elementor-widget elementor-widget-heading\" data-id=\"38e4d1b\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"heading.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t<h2 class=\"elementor-heading-title elementor-size-default\">FAQ<\/h2>\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t<div class=\"elementor-element elementor-element-d77046d e-flex e-con-boxed e-con e-parent\" data-id=\"d77046d\" data-element_type=\"container\" data-e-type=\"container\" data-settings=\"{&quot;jet_parallax_layout_list&quot;:[]}\">\n\t\t\t\t\t<div class=\"e-con-inner\">\n\t\t\t\t<div class=\"elementor-element elementor-element-1048570 elementor-widget elementor-widget-text-editor\" data-id=\"1048570\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<p><strong>Comment la myopathie de Becker affecte-t-elle la qualit\u00e9 de vie ?<\/strong><br \/>La maladie entra\u00eene une perte progressive de la force musculaire et de la mobilit\u00e9. Toutefois, avec une prise en charge adapt\u00e9e, les personnes peuvent pr\u00e9server une bonne qualit\u00e9 de vie et une autonomie pendant plusieurs ann\u00e9es.<\/p><p><strong><br \/>Quelles sont les options de traitement pour la myopathie de Becker ?<\/strong><br \/>Les traitements incluent des m\u00e9dicaments comme les corticost\u00e9ro\u00efdes, un suivi cardiologique, la r\u00e9\u00e9ducation fonctionnelle, ainsi que des dispositifs d\u2019assistance robotique.<\/p><p><strong><br \/>Existe-t-il des th\u00e9rapies innovantes pour la myopathie de Becker ?<\/strong><br \/>Oui. La th\u00e9rapie g\u00e9nique, l\u2019exon skipping, et l\u2019\u00e9dition du g\u00e9nome font partie des pistes actuellement en cours de d\u00e9veloppement.<\/p><p><strong><br \/>Comment diff\u00e9rencier la myopathie de Becker de <a href=\"https:\/\/orthopus.com\/fr\/maladies-neuromusculaires\/dystrophie-musculaire-de-duchenne\/\">la dystrophie musculaire de Duchenne<\/a> (DMD) ?<\/strong><br \/>La dystrophie musculaire de Becker \u00e9volue plus lentement et la dystrophine est partiellement pr\u00e9sente, ce qui retarde l\u2019apparition des sympt\u00f4mes. La DMD, en revanche, est plus s\u00e9v\u00e8re et d\u00e9bute plus t\u00f4t.<\/p><p><strong><br \/>Quels sont les premiers signes de la dystrophie musculaire de Becker ?<\/strong><br \/>Fatigue musculaire, crampes, difficult\u00e9s \u00e0 courir ou \u00e0 monter les escaliers sont les sympt\u00f4mes les plus fr\u00e9quents au d\u00e9but.<\/p>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t<div class=\"elementor-element elementor-element-988e1a9 e-flex e-con-boxed e-con e-parent\" data-id=\"988e1a9\" data-element_type=\"container\" data-e-type=\"container\" data-settings=\"{&quot;jet_parallax_layout_list&quot;:[]}\">\n\t\t\t\t\t<div class=\"e-con-inner\">\n\t\t\t\t<div class=\"elementor-element elementor-element-43d5198 elementor-widget elementor-widget-spacer\" data-id=\"43d5198\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"spacer.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t<div class=\"elementor-spacer\">\n\t\t\t<div class=\"elementor-spacer-inner\"><\/div>\n\t\t<\/div>\n\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t<div class=\"elementor-element elementor-element-22961ee elementor-widget elementor-widget-html\" data-id=\"22961ee\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"html.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t<script type=\"application\/ld+json\">\r\n{\r\n  \"@context\": \"https:\/\/schema.org\",\r\n  \"@graph\": [\r\n    {\r\n      \"@type\": \"MedicalWebPage\",\r\n      \"@id\": \"https:\/\/orthopus.com\/fr\/maladies-neuromusculaires\/dystrophie-musculaire-de-becker\/\",\r\n      \"url\": \"https:\/\/orthopus.com\/fr\/maladies-neuromusculaires\/dystrophie-musculaire-de-becker\/\",\r\n      \"name\": \"Dystrophie musculaire de Becker : comprendre, traiter et vivre avec la maladie\",\r\n      \"inLanguage\": \"fr-FR\",\r\n      \"about\": { \"@id\": \"https:\/\/orthopus.com\/fr\/maladies-neuromusculaires\/dystrophie-musculaire-de-becker\/\" },\r\n      \"description\": \"Guide sur la dystrophie musculaire de Becker (DMB) : d\u00e9finition, g\u00e9n\u00e9tique (g\u00e8ne DMD), sympt\u00f4mes, \u00e9volution, atteinte cardiaque, prises en charge (m\u00e9dicamenteuse, r\u00e9\u00e9ducation, suivi pluridisciplinaire), innovations (th\u00e9rapie g\u00e9nique, saut d\u2019exon), aides et financements.\",\r\n      \"isPartOf\": {\r\n        \"@type\": \"WebSite\",\r\n        \"name\": \"Orthopus\",\r\n        \"url\": \"https:\/\/orthopus.com\/fr\/\"\r\n      },\r\n      \"author\": { \"@id\": \"https:\/\/orthopus.com\/fr\/equipage\/\" },\r\n      \"medicalAudience\": [\"Patient\",\"Caregiver\"],\r\n      \"medicalSpecialty\": [\"Neurology\",\"Physiotherapy\",\"Cardiovascular\"]\r\n    },\r\n    {\r\n      \"@type\": \"Person\",\r\n      \"@id\": \"https:\/\/orthopus.com\/fr\/equipage\/\",\r\n      \"name\": \"Pierre Murzeau\",\r\n      \"jobTitle\": \"Content manager\"\r\n    },\r\n    {\r\n      \"@type\": \"MedicalCondition\",\r\n      \"@id\": \"https:\/\/orthopus.com\/fr\/maladies-neuromusculaires\/dystrophie-musculaire-de-becker\/\",\r\n      \"name\": \"Dystrophie musculaire de Becker\",\r\n      \"alternateName\": [\"DMB\", \"Becker muscular dystrophy\"],\r\n      \"identifier\": [\r\n        { \"@type\": \"PropertyValue\", \"propertyID\": \"ICD-10\", \"value\": \"G71.0\" }\r\n      ],\r\n      \"description\": \"Maladie neuromusculaire g\u00e9n\u00e9tique rare li\u00e9e \u00e0 une mutation du g\u00e8ne DMD (chromosome X) entra\u00eenant une production partielle de dystrophine, une faiblesse musculaire progressive et une atteinte cardiaque possible. 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Avec un suivi adapt\u00e9 (r\u00e9\u00e9ducation, surveillance cardiaque, aides techniques), une bonne qualit\u00e9 de vie et une autonomie peuvent \u00eatre pr\u00e9serv\u00e9es plusieurs ann\u00e9es.\"\r\n          }\r\n        },\r\n        {\r\n          \"@type\": \"Question\",\r\n          \"name\": \"Quelles sont les options de traitement pour la myopathie de Becker ?\",\r\n          \"acceptedAnswer\": {\r\n            \"@type\": \"Answer\",\r\n            \"text\": \"Corticost\u00e9ro\u00efdes, prise en charge cardiologique (IEC, b\u00eata-bloquants selon besoins), kin\u00e9sith\u00e9rapie\/r\u00e9\u00e9ducation, suivi pluridisciplinaire et aides techniques (exosquelettes, dispositifs robotiques).\"\r\n          }\r\n        },\r\n        {\r\n          \"@type\": \"Question\",\r\n          \"name\": \"Existe-t-il des th\u00e9rapies innovantes pour la myopathie de Becker ?\",\r\n          \"acceptedAnswer\": {\r\n            \"@type\": \"Answer\",\r\n            \"text\": \"Oui : th\u00e9rapie g\u00e9nique, exon skipping et \u00e9dition du g\u00e9nome (CRISPR-Cas9) sont \u00e0 l\u2019\u00e9tude. 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Disponible sur: <a href=\"https:\/\/www.afm-telethon.fr\/fr\/fiches-maladies\/dystrophie-musculaire-de-becker\" rel=\"nofollow\">https:\/\/www.afm-telethon.fr\/fr\/fiches-maladies\/dystrophie-musculaire-de-becker<\/a><\/li>\n  <li>Manuels MSD pour le grand public [Internet]. [cit\u00e9 2 mai 2025]. Dystrophie musculaire de Duchenne et dystrophie musculaire de Becker &#8211; Probl\u00e8mes de sant\u00e9 infantiles. Disponible sur: <a href=\"https:\/\/www.msdmanuals.com\/fr\/accueil\/probl\u00e8mes-de-sant\u00e9-infantiles\/dystrophies-musculaires-et-troubles-associ\u00e9s\/dystrophie-musculaire-de-duchenne-et-dystrophie-musculaire-de-becker\" rel=\"nofollow\">https:\/\/www.msdmanuals.com\/fr\/accueil\/probl\u00e8mes-de-sant\u00e9-infantiles\/dystrophies-musculaires-et-troubles-associ\u00e9s\/dystrophie-musculaire-de-duchenne-et-dystrophie-musculaire-de-becker<\/a><\/li>\n  <li>DMDB G. Groupe d\u2019Int\u00e9r\u00eat DMDB de l\u2019AFM-T\u00e9l\u00e9thon. 2020 [cit\u00e9 2 mai 2025]. La Dystrophie Musculaire de Becker. Disponible sur: <a href=\"https:\/\/dmdb.afm-telethon.fr\/la-dystrophie-musculaire-de-becker\/\" rel=\"nofollow\">https:\/\/dmdb.afm-telethon.fr\/la-dystrophie-musculaire-de-becker\/<\/a><\/li>\n  <li>\u00c9dition professionnelle du Manuel MSD [Internet]. [cit\u00e9 2 mai 2025]. Dystrophie musculaire de Duchenne et de Becker &#8211; P\u00e9diatrie. Disponible sur: <a href=\"https:\/\/www.msdmanuals.com\/fr\/professional\/p\u00e9diatrie\/troubles-musculaires-h\u00e9r\u00e9ditaires\/dystrophie-musculaire-de-duchenne-et-de-becker\" rel=\"nofollow\">https:\/\/www.msdmanuals.com\/fr\/professional\/p\u00e9diatrie\/troubles-musculaires-h\u00e9r\u00e9ditaires\/dystrophie-musculaire-de-duchenne-et-de-becker<\/a><\/li>\n  <li>Orphanet: Dystrophie musculaire de Duchenne et Becker [Internet]. [cit\u00e9 2 mai 2025]. Disponible sur: <a href=\"http:\/\/www.orpha.net\/fr\/disease\/detail\/262\" rel=\"nofollow\">http:\/\/www.orpha.net\/fr\/disease\/detail\/262<\/a><\/li>\n  <li>La consultation de conseil g\u00e9n\u00e9tique | AFM T\u00e9l\u00e9thon [Internet]. 2014 [cit\u00e9 2 mai 2025]. Disponible sur: <a href=\"https:\/\/www.afm-telethon.fr\/fr\/vivre-avec-la-maladie\/je-m-informe-sur-les-maladies\/comprendre-les-maladies-genetiques\/consultation-genetique\" rel=\"nofollow\">https:\/\/www.afm-telethon.fr\/fr\/vivre-avec-la-maladie\/je-m-informe-sur-les-maladies\/comprendre-les-maladies-genetiques\/consultation-genetique<\/a><\/li>\n  <li>CBIP [Internet]. [cit\u00e9 2 mai 2025]. CBIP. Disponible sur: <a href=\"https:\/\/www.cbip.be\/fr\/chapters\/2?frag=570\" rel=\"nofollow\">https:\/\/www.cbip.be\/fr\/chapters\/2?frag=570<\/a><\/li>\n  <li>Goyenvalle A, Vulin A, Fougerousse F, Leturcq F, Kaplan JC, Garcia L, et al. Le saut d\u2019exon th\u00e9rapeutique\u202f: un espoir pour les dystrophinopathies. m\u00e9decine\/sciences. 1 d\u00e9c 2004;20(12):1163\u20115. <a href=\"https:\/\/www.medecinesciences.org\/en\/articles\/medsci\/full_html\/2004\/10\/medsci20042012p1163\/medsci20042012p1163.html\" rel=\"nofollow\">https:\/\/www.medecinesciences.org\/en\/articles\/medsci\/full_html\/2004\/10\/medsci20042012p1163\/medsci20042012p1163.html<\/a><\/li>\n  <li>Inhibiteur de l\u2019enzyme de conversion. In: Wikip\u00e9dia [Internet]. 2025 [cit\u00e9 2 mai 2025]. Disponible sur: <a href=\"https:\/\/fr.wikipedia.org\/w\/index.php?title=Inhibiteur_de_l%27enzyme_de_conversion&amp;oldid=223651554\" rel=\"nofollow\">https:\/\/fr.wikipedia.org\/w\/index.php?title=Inhibiteur_de_l%27enzyme_de_conversion&amp;oldid=223651554<\/a><\/li>\n  <li>Th\u00e9rapie g\u00e9nique | AFM T\u00e9l\u00e9thon [Internet]. 2024 [cit\u00e9 2 mai 2025]. Disponible sur: <a href=\"https:\/\/www.afm-telethon.fr\/fr\/termes\/therapie-genique\" rel=\"nofollow\">https:\/\/www.afm-telethon.fr\/fr\/termes\/therapie-genique<\/a><\/li>\n  <li>Manuels MSD pour le grand public [Internet]. [cit\u00e9 2 mai 2025]. Table:Cortico\u00efdes\u202f: Utilisations et effets secondaires. Disponible sur: <a href=\"https:\/\/www.msdmanuals.com\/fr\/accueil\/multimedia\/table\/cortico\u00efdes-utilisations-et-effets-secondaires\" rel=\"nofollow\">https:\/\/www.msdmanuals.com\/fr\/accueil\/multimedia\/table\/cortico\u00efdes-utilisations-et-effets-secondaires<\/a><\/li>\n  <li>CRISPR-Cas9\u202f: une avanc\u00e9e pour les maladies g\u00e9n\u00e9tiques | AFM T\u00e9l\u00e9thon [Internet]. 2025 [cit\u00e9 2 mai 2025]. Disponible sur: <a href=\"https:\/\/www.afm-telethon.fr\/fr\/termes\/crisprcas9\" rel=\"nofollow\">https:\/\/www.afm-telethon.fr\/fr\/termes\/crisprcas9<\/a><\/li>\n  <li>Orphanet: Dystrophie musculaire de Becker [Internet]. [cit\u00e9 2 mai 2025]. Disponible sur: <a href=\"http:\/\/www.orpha.net\/fr\/disease\/detail\/98895\" rel=\"nofollow\">http:\/\/www.orpha.net\/fr\/disease\/detail\/98895<\/a><\/li>\n<\/ol>\n\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t","protected":false},"excerpt":{"rendered":"<p>Dystrophie musculaire de Becker : comprendre, traiter et vivre avec la maladie La dystrophie musculaire de Becker (DMB) est une maladie g\u00e9n\u00e9tique rare touchant le plus souvent les muscles squelettiques et le c\u0153ur. Cette pathologie provoque une faiblesse musculaire progressive, qui entra\u00eene une diminution de l\u2019autonomie et de la capacit\u00e9 \u00e0 se mouvoir, ce qui [&hellip;]<\/p>\n","protected":false},"author":15,"featured_media":0,"parent":16340,"menu_order":0,"comment_status":"closed","ping_status":"closed","template":"","meta":{"_jet_sm_ready_style":"","_jet_sm_style":"","_jet_sm_controls_values":"","_jet_sm_fonts_collection":"","_jet_sm_fonts_links":"","footnotes":""},"class_list":["post-17263","page","type-page","status-publish","hentry"],"yoast_head":"<!-- This site is optimized with the Yoast SEO plugin v27.4 - https:\/\/yoast.com\/product\/yoast-seo-wordpress\/ -->\n<title>Dystrophie musculaire de Becker - Traitements et Aide<\/title>\n<meta name=\"description\" content=\"Tout sur la dystrophie musculaire de Becker : sympt\u00f4mes, traitements, t\u00e9moignages, \u00e9volutions et solutions d&#039;assistance robotique.\" \/>\n<meta name=\"robots\" content=\"index, follow, max-snippet:-1, max-image-preview:large, max-video-preview:-1\" \/>\n<link rel=\"canonical\" href=\"https:\/\/orthopus.com\/fr\/maladies-neuromusculaires\/dystrophie-musculaire-de-becker\/\" \/>\n<meta property=\"og:locale\" content=\"fr_FR\" \/>\n<meta property=\"og:type\" content=\"article\" \/>\n<meta property=\"og:title\" content=\"Dystrophie musculaire de Becker - Traitements et Aide\" \/>\n<meta property=\"og:description\" content=\"Tout sur la dystrophie musculaire de Becker : sympt\u00f4mes, traitements, t\u00e9moignages, \u00e9volutions et solutions d&#039;assistance robotique.\" \/>\n<meta property=\"og:url\" content=\"https:\/\/orthopus.com\/fr\/maladies-neuromusculaires\/dystrophie-musculaire-de-becker\/\" \/>\n<meta property=\"og:site_name\" content=\"ORTHOPUS\" \/>\n<meta property=\"article:modified_time\" content=\"2025-09-01T14:39:54+00:00\" \/>\n<meta property=\"og:image\" content=\"https:\/\/orthopus.com\/wp-content\/uploads\/2025\/08\/orthopus-dystrophie-musculaire-de-duchenne.webp\" \/>\n<meta name=\"twitter:card\" content=\"summary_large_image\" \/>\n<meta name=\"twitter:label1\" content=\"Dur\u00e9e de lecture estim\u00e9e\" \/>\n\t<meta name=\"twitter:data1\" content=\"18 minutes\" \/>\n<script type=\"application\/ld+json\" class=\"yoast-schema-graph\">{\"@context\":\"https:\\\/\\\/schema.org\",\"@graph\":[{\"@type\":\"WebPage\",\"@id\":\"https:\\\/\\\/orthopus.com\\\/fr\\\/maladies-neuromusculaires\\\/dystrophie-musculaire-de-becker\\\/\",\"url\":\"https:\\\/\\\/orthopus.com\\\/fr\\\/maladies-neuromusculaires\\\/dystrophie-musculaire-de-becker\\\/\",\"name\":\"Dystrophie musculaire de Becker - Traitements et Aide\",\"isPartOf\":{\"@id\":\"https:\\\/\\\/orthopus.com\\\/#website\"},\"primaryImageOfPage\":{\"@id\":\"https:\\\/\\\/orthopus.com\\\/fr\\\/maladies-neuromusculaires\\\/dystrophie-musculaire-de-becker\\\/#primaryimage\"},\"image\":{\"@id\":\"https:\\\/\\\/orthopus.com\\\/fr\\\/maladies-neuromusculaires\\\/dystrophie-musculaire-de-becker\\\/#primaryimage\"},\"thumbnailUrl\":\"https:\\\/\\\/orthopus.com\\\/wp-content\\\/uploads\\\/2025\\\/08\\\/orthopus-dystrophie-musculaire-de-duchenne.webp\",\"datePublished\":\"2025-08-25T14:34:11+00:00\",\"dateModified\":\"2025-09-01T14:39:54+00:00\",\"description\":\"Tout sur la dystrophie musculaire de Becker : sympt\u00f4mes, traitements, t\u00e9moignages, \u00e9volutions et solutions d'assistance robotique.\",\"breadcrumb\":{\"@id\":\"https:\\\/\\\/orthopus.com\\\/fr\\\/maladies-neuromusculaires\\\/dystrophie-musculaire-de-becker\\\/#breadcrumb\"},\"inLanguage\":\"fr-FR\",\"potentialAction\":[{\"@type\":\"ReadAction\",\"target\":[\"https:\\\/\\\/orthopus.com\\\/fr\\\/maladies-neuromusculaires\\\/dystrophie-musculaire-de-becker\\\/\"]}]},{\"@type\":\"ImageObject\",\"inLanguage\":\"fr-FR\",\"@id\":\"https:\\\/\\\/orthopus.com\\\/fr\\\/maladies-neuromusculaires\\\/dystrophie-musculaire-de-becker\\\/#primaryimage\",\"url\":\"https:\\\/\\\/orthopus.com\\\/wp-content\\\/uploads\\\/2025\\\/08\\\/orthopus-dystrophie-musculaire-de-duchenne.webp\",\"contentUrl\":\"https:\\\/\\\/orthopus.com\\\/wp-content\\\/uploads\\\/2025\\\/08\\\/orthopus-dystrophie-musculaire-de-duchenne.webp\"},{\"@type\":\"BreadcrumbList\",\"@id\":\"https:\\\/\\\/orthopus.com\\\/fr\\\/maladies-neuromusculaires\\\/dystrophie-musculaire-de-becker\\\/#breadcrumb\",\"itemListElement\":[{\"@type\":\"ListItem\",\"position\":1,\"name\":\"Accueil\",\"item\":\"https:\\\/\\\/orthopus.com\\\/fr\\\/\"},{\"@type\":\"ListItem\",\"position\":2,\"name\":\"Tout savoir sur les maladies neuromusculaires\",\"item\":\"https:\\\/\\\/orthopus.com\\\/fr\\\/maladies-neuromusculaires\\\/\"},{\"@type\":\"ListItem\",\"position\":3,\"name\":\"Dystrophie musculaire de Becker &#8211; 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