{"id":16340,"date":"2025-06-25T11:20:23","date_gmt":"2025-06-25T09:20:23","guid":{"rendered":"https:\/\/orthopus.com\/?page_id=16340"},"modified":"2025-09-01T15:12:28","modified_gmt":"2025-09-01T13:12:28","slug":"maladies-neuromusculaires","status":"publish","type":"page","link":"https:\/\/orthopus.com\/fr\/maladies-neuromusculaires\/","title":{"rendered":"Tout savoir sur les maladies neuromusculaires"},"content":{"rendered":"\t\t<div data-elementor-type=\"wp-page\" data-elementor-id=\"16340\" class=\"elementor elementor-16340\" data-elementor-post-type=\"page\">\n\t\t\t\t\t\t<section class=\"elementor-section elementor-top-section elementor-element elementor-element-f251d47 elementor-section-boxed elementor-section-height-default elementor-section-height-default\" data-id=\"f251d47\" data-element_type=\"section\" data-e-type=\"section\" data-settings=\"{&quot;jet_parallax_layout_list&quot;:[]}\">\n\t\t\t\t\t\t<div class=\"elementor-container elementor-column-gap-default\">\n\t\t\t\t\t<div class=\"elementor-column elementor-col-100 elementor-top-column elementor-element elementor-element-7679ddf\" data-id=\"7679ddf\" data-element_type=\"column\" data-e-type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-1946a13 elementor-widget elementor-widget-spacer\" data-id=\"1946a13\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"spacer.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t<div class=\"elementor-spacer\">\n\t\t\t<div class=\"elementor-spacer-inner\"><\/div>\n\t\t<\/div>\n\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/section>\n\t\t\t\t<section class=\"elementor-section elementor-top-section elementor-element elementor-element-a7af5a2 elementor-section-full_width elementor-section-height-default elementor-section-height-default\" data-id=\"a7af5a2\" data-element_type=\"section\" data-e-type=\"section\" data-settings=\"{&quot;jet_parallax_layout_list&quot;:[]}\">\n\t\t\t\t\t\t<div class=\"elementor-container elementor-column-gap-default\">\n\t\t\t\t\t<div class=\"elementor-column elementor-col-100 elementor-top-column elementor-element elementor-element-3b9e001\" data-id=\"3b9e001\" data-element_type=\"column\" data-e-type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-61b3171 elementor-widget elementor-widget-heading\" data-id=\"61b3171\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"heading.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t<h1 class=\"elementor-heading-title elementor-size-default\">Tout savoir sur les maladies neuromusculaires<\/h1>\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/section>\n\t\t\t\t<section class=\"elementor-section elementor-top-section elementor-element elementor-element-8794112 elementor-section-full_width elementor-section-height-default elementor-section-height-default\" data-id=\"8794112\" data-element_type=\"section\" data-e-type=\"section\" data-settings=\"{&quot;jet_parallax_layout_list&quot;:[]}\">\n\t\t\t\t\t\t<div class=\"elementor-container elementor-column-gap-default\">\n\t\t\t\t\t<div class=\"elementor-column elementor-col-100 elementor-top-column elementor-element elementor-element-eaea273\" data-id=\"eaea273\" data-element_type=\"column\" data-e-type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-acbe3c7 elementor-widget elementor-widget-image\" data-id=\"acbe3c7\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"image.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t\t\t\t\t\t\t<img fetchpriority=\"high\" decoding=\"async\" width=\"2560\" height=\"913\" src=\"https:\/\/orthopus.com\/wp-content\/uploads\/2025\/06\/maladies-neuromusculaires.webp\" class=\"attachment-full size-full wp-image-16344\" alt=\"Repr\u00e9sentation stylis\u00e9e de neurones.\" srcset=\"https:\/\/orthopus.com\/wp-content\/uploads\/2025\/06\/maladies-neuromusculaires.webp 2560w, https:\/\/orthopus.com\/wp-content\/uploads\/2025\/06\/maladies-neuromusculaires-300x107.webp 300w, https:\/\/orthopus.com\/wp-content\/uploads\/2025\/06\/maladies-neuromusculaires-1024x365.webp 1024w, https:\/\/orthopus.com\/wp-content\/uploads\/2025\/06\/maladies-neuromusculaires-768x274.webp 768w, https:\/\/orthopus.com\/wp-content\/uploads\/2025\/06\/maladies-neuromusculaires-1536x548.webp 1536w, https:\/\/orthopus.com\/wp-content\/uploads\/2025\/06\/maladies-neuromusculaires-2048x730.webp 2048w, https:\/\/orthopus.com\/wp-content\/uploads\/2025\/06\/maladies-neuromusculaires-600x214.webp 600w, https:\/\/orthopus.com\/wp-content\/uploads\/2025\/06\/maladies-neuromusculaires-200x71.webp 200w\" sizes=\"(max-width: 2560px) 100vw, 2560px\" \/>\t\t\t\t\t\t\t\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/section>\n\t\t\t\t<section class=\"elementor-section elementor-top-section elementor-element elementor-element-d3b2f6b elementor-section-boxed elementor-section-height-default elementor-section-height-default\" data-id=\"d3b2f6b\" data-element_type=\"section\" data-e-type=\"section\" data-settings=\"{&quot;jet_parallax_layout_list&quot;:[]}\">\n\t\t\t\t\t\t<div class=\"elementor-container elementor-column-gap-default\">\n\t\t\t\t\t<div class=\"elementor-column elementor-col-100 elementor-top-column elementor-element elementor-element-72a56f4\" data-id=\"72a56f4\" data-element_type=\"column\" data-e-type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-d751728 elementor-widget elementor-widget-spacer\" data-id=\"d751728\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"spacer.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t<div class=\"elementor-spacer\">\n\t\t\t<div class=\"elementor-spacer-inner\"><\/div>\n\t\t<\/div>\n\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/section>\n\t\t\t\t<section class=\"elementor-section elementor-top-section elementor-element elementor-element-287729b elementor-section-boxed elementor-section-height-default elementor-section-height-default\" data-id=\"287729b\" data-element_type=\"section\" data-e-type=\"section\" data-settings=\"{&quot;jet_parallax_layout_list&quot;:[],&quot;background_background&quot;:&quot;classic&quot;}\">\n\t\t\t\t\t\t<div class=\"elementor-container elementor-column-gap-default\">\n\t\t\t\t\t<div class=\"elementor-column elementor-col-100 elementor-top-column elementor-element elementor-element-6d94aa9\" data-id=\"6d94aa9\" data-element_type=\"column\" data-e-type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-3dd1a64 elementor-widget elementor-widget-text-editor\" data-id=\"3dd1a64\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<p>Contenu relu et valid\u00e9 par le <a href=\"https:\/\/www.maiia.com\/medecin-specialiste-en-medecine-physique-et-de-readaptation\/44100-nantes\/de-lattre-capucine\" target=\"_blank\" rel=\"noopener\">Dr Capucine DE LATTRE<\/a>, m\u00e9decin sp\u00e9cialiste en m\u00e9decine physique et de r\u00e9adaptation<\/p>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/section>\n\t\t\t\t<section class=\"elementor-section elementor-top-section elementor-element elementor-element-5f27940 elementor-section-boxed elementor-section-height-default elementor-section-height-default\" data-id=\"5f27940\" data-element_type=\"section\" data-e-type=\"section\" data-settings=\"{&quot;jet_parallax_layout_list&quot;:[]}\">\n\t\t\t\t\t\t<div class=\"elementor-container elementor-column-gap-default\">\n\t\t\t\t\t<div class=\"elementor-column elementor-col-100 elementor-top-column elementor-element elementor-element-51c8a07\" data-id=\"51c8a07\" data-element_type=\"column\" data-e-type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-4f56888 elementor-widget elementor-widget-spacer\" data-id=\"4f56888\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"spacer.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t<div class=\"elementor-spacer\">\n\t\t\t<div class=\"elementor-spacer-inner\"><\/div>\n\t\t<\/div>\n\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/section>\n\t\t\t\t<section class=\"elementor-section elementor-top-section elementor-element elementor-element-64eb980 elementor-section-boxed elementor-section-height-default elementor-section-height-default\" data-id=\"64eb980\" data-element_type=\"section\" data-e-type=\"section\" data-settings=\"{&quot;jet_parallax_layout_list&quot;:[]}\">\n\t\t\t\t\t\t<div class=\"elementor-container elementor-column-gap-default\">\n\t\t\t\t\t<div class=\"elementor-column elementor-col-100 elementor-top-column elementor-element elementor-element-c6d6803\" data-id=\"c6d6803\" data-element_type=\"column\" data-e-type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-6b63d8d elementor-widget elementor-widget-text-editor\" data-id=\"6b63d8d\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<p>Les maladies neuromusculaires constituent un ensemble de maladies rares qui touchent le syst\u00e8me nerveux p\u00e9riph\u00e9rique. Elles entra\u00eenent un dysfonctionnement de la fonction motrice par diff\u00e9rents m\u00e9canismes.(1)<\/p><p><strong><br \/>Cette atteinte motrice peut \u00eatre dues \u00e0 :<\/strong><\/p><ul><li>des <strong>neurones moteurs (ou motoneurones)<\/strong><\/li><li>de la <strong>jonction neuromusculaire<\/strong><\/li><li>ou des <strong>fibres musculaire<\/strong><\/li><\/ul>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/section>\n\t\t\t\t<section class=\"elementor-section elementor-top-section elementor-element elementor-element-d9c9598 elementor-section-full_width elementor-section-height-default elementor-section-height-default\" data-id=\"d9c9598\" data-element_type=\"section\" data-e-type=\"section\" data-settings=\"{&quot;jet_parallax_layout_list&quot;:[]}\">\n\t\t\t\t\t\t<div class=\"elementor-container elementor-column-gap-default\">\n\t\t\t\t\t<div class=\"elementor-column elementor-col-100 elementor-top-column elementor-element elementor-element-c0d4bca\" data-id=\"c0d4bca\" data-element_type=\"column\" data-e-type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-ad8548d elementor-widget elementor-widget-image\" data-id=\"ad8548d\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"image.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t\t\t\t\t\t\t<img decoding=\"async\" width=\"2560\" height=\"998\" src=\"https:\/\/orthopus.com\/wp-content\/uploads\/2025\/06\/Schema-unite-motrice.webp\" class=\"elementor-animation-float attachment-full size-full wp-image-16349\" alt=\"Sch\u00e9ma explicatif de l&#039;unit\u00e9 motrice.\" srcset=\"https:\/\/orthopus.com\/wp-content\/uploads\/2025\/06\/Schema-unite-motrice.webp 2560w, https:\/\/orthopus.com\/wp-content\/uploads\/2025\/06\/Schema-unite-motrice-300x117.webp 300w, https:\/\/orthopus.com\/wp-content\/uploads\/2025\/06\/Schema-unite-motrice-1024x399.webp 1024w, https:\/\/orthopus.com\/wp-content\/uploads\/2025\/06\/Schema-unite-motrice-768x299.webp 768w, https:\/\/orthopus.com\/wp-content\/uploads\/2025\/06\/Schema-unite-motrice-1536x599.webp 1536w, https:\/\/orthopus.com\/wp-content\/uploads\/2025\/06\/Schema-unite-motrice-2048x798.webp 2048w, https:\/\/orthopus.com\/wp-content\/uploads\/2025\/06\/Schema-unite-motrice-600x234.webp 600w, https:\/\/orthopus.com\/wp-content\/uploads\/2025\/06\/Schema-unite-motrice-200x78.webp 200w\" sizes=\"(max-width: 2560px) 100vw, 2560px\" \/>\t\t\t\t\t\t\t\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/section>\n\t\t\t\t<section class=\"elementor-section elementor-top-section elementor-element elementor-element-04f22a3 elementor-section-boxed elementor-section-height-default elementor-section-height-default\" data-id=\"04f22a3\" data-element_type=\"section\" data-e-type=\"section\" data-settings=\"{&quot;jet_parallax_layout_list&quot;:[]}\">\n\t\t\t\t\t\t<div class=\"elementor-container elementor-column-gap-default\">\n\t\t\t\t\t<div class=\"elementor-column elementor-col-100 elementor-top-column elementor-element elementor-element-dd98508\" data-id=\"dd98508\" data-element_type=\"column\" data-e-type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-fd58aa0 elementor-widget elementor-widget-text-editor\" data-id=\"fd58aa0\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<p>Si l\u2019un de ces \u00e9l\u00e9ments ne fonctionne pas comme pr\u00e9vu, cela peut affecter certains gestes du quotidien comme marcher, respirer ou d\u00e9glutir(1).<\/p><p>Aujourd\u2019hui, il existe plus de\u00a0<strong>400 maladies neuromusculaires<\/strong>(2). Certaines sont\u00a0<strong>rares<\/strong>,\u00a0<strong>d\u2019autres plus fr\u00e9quentes<\/strong>.\u00a0<strong>Des dizaines de milliers de personnes en France<\/strong>\u00a0sont concern\u00e9es. C\u2019est pourquoi il est important de mieux les conna\u00eetre, de les rep\u00e9rer t\u00f4t et de proposer une prise en charge adapt\u00e9e.<\/p>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/section>\n\t\t\t\t<section class=\"elementor-section elementor-top-section elementor-element elementor-element-94c54c7 elementor-section-boxed elementor-section-height-default elementor-section-height-default\" data-id=\"94c54c7\" data-element_type=\"section\" data-e-type=\"section\" data-settings=\"{&quot;jet_parallax_layout_list&quot;:[]}\">\n\t\t\t\t\t\t<div class=\"elementor-container elementor-column-gap-default\">\n\t\t\t\t\t<div class=\"elementor-column elementor-col-100 elementor-top-column elementor-element elementor-element-de2af60\" data-id=\"de2af60\" data-element_type=\"column\" data-e-type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-7332309 elementor-widget elementor-widget-spacer\" data-id=\"7332309\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"spacer.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t<div class=\"elementor-spacer\">\n\t\t\t<div class=\"elementor-spacer-inner\"><\/div>\n\t\t<\/div>\n\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/section>\n\t\t\t\t<section class=\"elementor-section elementor-top-section elementor-element elementor-element-adddab8 elementor-section-boxed elementor-section-height-default elementor-section-height-default\" data-id=\"adddab8\" data-element_type=\"section\" data-e-type=\"section\" data-settings=\"{&quot;jet_parallax_layout_list&quot;:[]}\">\n\t\t\t\t\t\t<div class=\"elementor-container elementor-column-gap-default\">\n\t\t\t\t\t<div class=\"elementor-column elementor-col-100 elementor-top-column elementor-element elementor-element-c9373d0\" data-id=\"c9373d0\" data-element_type=\"column\" data-e-type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-8015613 elementor-widget elementor-widget-heading\" data-id=\"8015613\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"heading.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t<h2 class=\"elementor-heading-title elementor-size-default\">Qu'est-ce qu'une maladie neuromusculaire ?<\/h2>\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/section>\n\t\t\t\t<section class=\"elementor-section elementor-top-section elementor-element elementor-element-f458493 elementor-section-boxed elementor-section-height-default elementor-section-height-default\" data-id=\"f458493\" data-element_type=\"section\" data-e-type=\"section\" data-settings=\"{&quot;jet_parallax_layout_list&quot;:[]}\">\n\t\t\t\t\t\t<div class=\"elementor-container elementor-column-gap-default\">\n\t\t\t\t\t<div class=\"elementor-column elementor-col-100 elementor-top-column elementor-element elementor-element-15ecfa4\" data-id=\"15ecfa4\" data-element_type=\"column\" data-e-type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-f272d24 elementor-widget elementor-widget-heading\" data-id=\"f272d24\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"heading.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t<h3 class=\"elementor-heading-title elementor-size-default\">D\u00e9finition et m\u00e9canismes des maladies neuromusculaires<\/h3>\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/section>\n\t\t\t\t<section class=\"elementor-section elementor-top-section elementor-element elementor-element-2f2a66c elementor-section-boxed elementor-section-height-default elementor-section-height-default\" data-id=\"2f2a66c\" data-element_type=\"section\" data-e-type=\"section\" data-settings=\"{&quot;jet_parallax_layout_list&quot;:[]}\">\n\t\t\t\t\t\t<div class=\"elementor-container elementor-column-gap-default\">\n\t\t\t\t\t<div class=\"elementor-column elementor-col-100 elementor-top-column elementor-element elementor-element-c02a275\" data-id=\"c02a275\" data-element_type=\"column\" data-e-type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-bc5baa9 elementor-widget elementor-widget-text-editor\" data-id=\"bc5baa9\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<p>Les maladies neuromusculaires sont des maladies chroniques. Elles \u00e9voluent souvent et <strong>touchent le mouvement volontaire<\/strong>. Cela inclut les neurones moteurs, les nerfs, la jonction musculaire et les fibres musculaires. Les maladies neuromusculaires sont g\u00e9n\u00e9ralement\u00a0<strong>responsables d\u2019une faiblesse musculaire progressive, pouvant s\u2019accompagner de douleurs, de crampes, voire de paralysies.<\/strong><\/p><p>\u00a0<\/p><p>Elles emp\u00eachent les muscles de bouger comme il faut. Cela peut \u00eatre d\u00fb \u00e0 d<strong>es nerfs qui se d\u00e9t\u00e9riorent<\/strong>.<\/p><p>\u00a0<\/p><p>Cela peut aussi \u00eatre parce que les muscles ne r\u00e9agissent pas bien. Parfois, <strong>le message entre le nerf et le muscle ne passe pas <\/strong>correctement.(1)(3) Le processus pathologique ne permet donc pas l\u2019efficacit\u00e9 du mouvement ou de la contraction musculaire.<\/p>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/section>\n\t\t\t\t<section class=\"elementor-section elementor-top-section elementor-element elementor-element-8aa490b elementor-section-boxed elementor-section-height-default elementor-section-height-default\" data-id=\"8aa490b\" data-element_type=\"section\" data-e-type=\"section\" data-settings=\"{&quot;jet_parallax_layout_list&quot;:[]}\">\n\t\t\t\t\t\t<div class=\"elementor-container elementor-column-gap-default\">\n\t\t\t\t\t<div class=\"elementor-column elementor-col-100 elementor-top-column elementor-element elementor-element-3cc43f1\" data-id=\"3cc43f1\" data-element_type=\"column\" data-e-type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-8a79fa2 elementor-widget elementor-widget-spacer\" data-id=\"8a79fa2\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"spacer.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t<div class=\"elementor-spacer\">\n\t\t\t<div class=\"elementor-spacer-inner\"><\/div>\n\t\t<\/div>\n\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/section>\n\t\t\t\t<section class=\"elementor-section elementor-top-section elementor-element elementor-element-a6c6d21 elementor-section-boxed elementor-section-height-default elementor-section-height-default\" data-id=\"a6c6d21\" data-element_type=\"section\" data-e-type=\"section\" data-settings=\"{&quot;jet_parallax_layout_list&quot;:[]}\">\n\t\t\t\t\t\t<div class=\"elementor-container elementor-column-gap-default\">\n\t\t\t\t\t<div class=\"elementor-column elementor-col-100 elementor-top-column elementor-element elementor-element-46b0a7b\" data-id=\"46b0a7b\" data-element_type=\"column\" data-e-type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-6f51c4a elementor-widget elementor-widget-heading\" data-id=\"6f51c4a\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"heading.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t<h3 class=\"elementor-heading-title elementor-size-default\">Quelles sont les causes des maladies neuromusculaires ?<\/h3>\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/section>\n\t\t\t\t<section class=\"elementor-section elementor-top-section elementor-element elementor-element-f758e20 elementor-section-boxed elementor-section-height-default elementor-section-height-default\" data-id=\"f758e20\" data-element_type=\"section\" data-e-type=\"section\" data-settings=\"{&quot;jet_parallax_layout_list&quot;:[]}\">\n\t\t\t\t\t\t<div class=\"elementor-container elementor-column-gap-default\">\n\t\t\t\t\t<div class=\"elementor-column elementor-col-100 elementor-top-column elementor-element elementor-element-3e8a922\" data-id=\"3e8a922\" data-element_type=\"column\" data-e-type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-6e83994 elementor-widget elementor-widget-text-editor\" data-id=\"6e83994\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<p><strong>Il y a plusieurs raisons possibles.<\/strong> Pour certaines affections, cela est d\u00fb \u00e0 une anomalie g\u00e9n\u00e9tique : celle-ci peut survenir de mani\u00e8re spontan\u00e9e ou \u00eatre h\u00e9rit\u00e9e des parents. Cette anomalie va causer un probl\u00e8me dans la transmission ou l&#8217;ex\u00e9cution du message moteur. Cela peut se produire au niveau d&#8217;une cellule, d&#8217;un nerf ou d&#8217;un muscle et entra\u00eener la maladie (3).<\/p><p>Il y a aussi d&#8217;autres causes acquises. Cela inclut l&#8217;utilisation de certains m\u00e9dicaments ou de substances toxiques. Une carence en vitamines peut aussi \u00eatre une cause. Des troubles hormonaux ou des infections peuvent \u00e9galement jouer un r\u00f4le.<\/p>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/section>\n\t\t\t\t<section class=\"elementor-section elementor-top-section elementor-element elementor-element-4cb37e8 elementor-section-boxed elementor-section-height-default elementor-section-height-default\" data-id=\"4cb37e8\" data-element_type=\"section\" data-e-type=\"section\" data-settings=\"{&quot;jet_parallax_layout_list&quot;:[]}\">\n\t\t\t\t\t\t<div class=\"elementor-container elementor-column-gap-default\">\n\t\t\t\t\t<div class=\"elementor-column elementor-col-100 elementor-top-column elementor-element elementor-element-fef81b1\" data-id=\"fef81b1\" data-element_type=\"column\" data-e-type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-c1ad69b elementor-widget elementor-widget-spacer\" data-id=\"c1ad69b\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"spacer.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t<div class=\"elementor-spacer\">\n\t\t\t<div class=\"elementor-spacer-inner\"><\/div>\n\t\t<\/div>\n\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/section>\n\t\t\t\t<section class=\"elementor-section elementor-top-section elementor-element elementor-element-2b31ac5 elementor-section-boxed elementor-section-height-default elementor-section-height-default\" data-id=\"2b31ac5\" data-element_type=\"section\" data-e-type=\"section\" data-settings=\"{&quot;jet_parallax_layout_list&quot;:[]}\">\n\t\t\t\t\t\t<div class=\"elementor-container elementor-column-gap-default\">\n\t\t\t\t\t<div class=\"elementor-column elementor-col-100 elementor-top-column elementor-element elementor-element-482c099\" data-id=\"482c099\" data-element_type=\"column\" data-e-type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-ad89118 elementor-widget elementor-widget-heading\" data-id=\"ad89118\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"heading.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t<h2 class=\"elementor-heading-title elementor-size-default\">Plus de 400 maladies neuromusculaires existent. <br>Quelles sont les plus communes ?<\/h2>\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/section>\n\t\t\t\t<section class=\"elementor-section elementor-top-section elementor-element elementor-element-860b098 elementor-section-boxed elementor-section-height-default elementor-section-height-default\" data-id=\"860b098\" data-element_type=\"section\" data-e-type=\"section\" data-settings=\"{&quot;jet_parallax_layout_list&quot;:[]}\">\n\t\t\t\t\t\t<div class=\"elementor-container elementor-column-gap-default\">\n\t\t\t\t\t<div class=\"elementor-column elementor-col-100 elementor-top-column elementor-element elementor-element-607f009\" data-id=\"607f009\" data-element_type=\"column\" data-e-type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-f9cc225 elementor-widget elementor-widget-heading\" data-id=\"f9cc225\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"heading.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t<h3 class=\"elementor-heading-title elementor-size-default\">Maladies fr\u00e9quentes<\/h3>\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/section>\n\t\t\t\t<section class=\"elementor-section elementor-top-section elementor-element elementor-element-18797c7 elementor-section-boxed elementor-section-height-default elementor-section-height-default\" data-id=\"18797c7\" data-element_type=\"section\" data-e-type=\"section\" data-settings=\"{&quot;jet_parallax_layout_list&quot;:[]}\">\n\t\t\t\t\t\t<div class=\"elementor-container elementor-column-gap-default\">\n\t\t\t\t\t<div class=\"elementor-column elementor-col-100 elementor-top-column elementor-element elementor-element-751146b\" data-id=\"751146b\" data-element_type=\"column\" data-e-type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-d425a7f elementor-widget elementor-widget-text-editor\" data-id=\"d425a7f\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<p>Certaines maladies neuromusculaires sont plus souvent diagnostiqu\u00e9es que d\u2019autres :<\/p><ol><li><strong>La dystrophie musculaire de <a href=\"https:\/\/orthopus.com\/fr\/maladies-neuromusculaires\/dystrophie-musculaire-de-duchenne\/\">Duchenne<\/a>\/<a href=\"https:\/\/orthopus.com\/fr\/maladies-neuromusculaires\/dystrophie-musculaire-de-becker\/\">Becker<\/a> :\u00a0maladie g\u00e9n\u00e9tique<\/strong> grave apparaissant chez les gar\u00e7ons touchant les muscles(4)(5).<\/li><li><strong>Les neuropathies de Charcot-Marie-Tooth <\/strong>sont des maladies h\u00e9r\u00e9ditaires. Elles touchent les <strong>nerfs p\u00e9riph\u00e9riques<\/strong>. Ces nerfs sont comme des &#8220;fils \u00e9lectriques&#8221; dans le corps. Ils transmettent les messages entre le cerveau et le reste du corps (6).<\/li><li><strong>La dystrophie myotonique de Steinert <\/strong>est une maladie. Elle se caract\u00e9rise par une myotonie. Cela signifie qu&#8217;il est difficile de rel\u00e2cher un muscle apr\u00e8s une contraction. Cette maladie cause aussi des troubles cardiaques et endocriniens (7).<\/li><li><strong>La myopathie facio-scapulo-hum\u00e9rale :<\/strong>\u00a0d\u00e9bute souvent par une faiblesse des muscles du visage et des \u00e9paules (8).<\/li><li><strong><a href=\"https:\/\/orthopus.com\/fr\/maladies-neuromusculaires\/maladies-neuromusculaires-amyotrophie-spinale-proximale\/\">L\u2019amyotrophie spinale proximale<\/a> li\u00e9e au g\u00e8ne SMN1 :<\/strong> maladie g\u00e9n\u00e9tique grave de la petite enfance qui touche le moto-neurone (= le messager qui envoie l\u2019ordre du cerveau jusqu\u2019aux muscles pour qu\u2019ils bougent)(9).<\/li><li><strong>Les myopathies mitochondriales : <\/strong>perturbation de la production d&#8217;\u00e9nergie dans les cellules musculaires(10).<\/li><li><strong>Les syndromes myasth\u00e9niques cong\u00e9nitaux : <\/strong>d\u00e9fauts de transmission neuromusculaire depuis la naissance(11).<\/li><\/ol>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/section>\n\t\t\t\t<section class=\"elementor-section elementor-top-section elementor-element elementor-element-36de53f elementor-section-boxed elementor-section-height-default elementor-section-height-default\" data-id=\"36de53f\" data-element_type=\"section\" data-e-type=\"section\" data-settings=\"{&quot;jet_parallax_layout_list&quot;:[]}\">\n\t\t\t\t\t\t<div class=\"elementor-container elementor-column-gap-default\">\n\t\t\t\t\t<div class=\"elementor-column elementor-col-100 elementor-top-column elementor-element elementor-element-f93b2aa\" data-id=\"f93b2aa\" data-element_type=\"column\" data-e-type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-11f379b elementor-widget elementor-widget-text-editor\" data-id=\"11f379b\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\tVoici une liste non exhaustive des pathologies neuromusculaires :\n\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/section>\n\t\t\t\t<section class=\"elementor-section elementor-top-section elementor-element elementor-element-09f37da elementor-hidden-tablet elementor-hidden-mobile elementor-section-boxed elementor-section-height-default elementor-section-height-default\" data-id=\"09f37da\" data-element_type=\"section\" data-e-type=\"section\" data-settings=\"{&quot;jet_parallax_layout_list&quot;:[],&quot;background_background&quot;:&quot;classic&quot;}\">\n\t\t\t\t\t\t<div class=\"elementor-container elementor-column-gap-default\">\n\t\t\t\t\t<div class=\"elementor-column elementor-col-50 elementor-top-column elementor-element elementor-element-b8bd0bd\" data-id=\"b8bd0bd\" data-element_type=\"column\" data-e-type=\"column\" data-settings=\"{&quot;background_background&quot;:&quot;classic&quot;}\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-74fbef8 elementor-widget elementor-widget-text-editor\" data-id=\"74fbef8\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<p>Nom<\/p>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t<div class=\"elementor-column elementor-col-50 elementor-top-column elementor-element elementor-element-b4bd3cf\" data-id=\"b4bd3cf\" data-element_type=\"column\" data-e-type=\"column\" data-settings=\"{&quot;background_background&quot;:&quot;classic&quot;}\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-30290e7 elementor-widget elementor-widget-text-editor\" data-id=\"30290e7\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<p>Description synth\u00e9tique<\/p>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/section>\n\t\t\t\t<section class=\"elementor-section elementor-top-section elementor-element elementor-element-7c2a5cf elementor-hidden-tablet elementor-hidden-mobile elementor-section-boxed elementor-section-height-default elementor-section-height-default\" data-id=\"7c2a5cf\" data-element_type=\"section\" data-e-type=\"section\" data-settings=\"{&quot;jet_parallax_layout_list&quot;:[]}\">\n\t\t\t\t\t\t<div class=\"elementor-container elementor-column-gap-default\">\n\t\t\t\t\t<div class=\"elementor-column elementor-col-50 elementor-top-column elementor-element elementor-element-6317d9f\" data-id=\"6317d9f\" data-element_type=\"column\" data-e-type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-2166ed7 elementor-widget elementor-widget-text-editor\" data-id=\"2166ed7\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<p><a href=\"https:\/\/orthopus.com\/fr\/maladies-neuromusculaires\/maladies-neuromusculaires-amyotrophie-spinale-proximale\/\">Amyotrophie spinale proximale<\/a> (SMN1)<\/p>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t<div class=\"elementor-column elementor-col-50 elementor-top-column elementor-element elementor-element-4b799da\" data-id=\"4b799da\" data-element_type=\"column\" data-e-type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-b054616 elementor-widget elementor-widget-text-editor\" data-id=\"b054616\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\tD\u00e9g\u00e9n\u00e9rescence des motoneurones entra\u00eenant une faiblesse musculaire grave.\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/section>\n\t\t\t\t<section class=\"elementor-section elementor-top-section elementor-element elementor-element-f5a793b elementor-hidden-tablet elementor-hidden-mobile elementor-section-boxed elementor-section-height-default elementor-section-height-default\" data-id=\"f5a793b\" data-element_type=\"section\" data-e-type=\"section\" data-settings=\"{&quot;jet_parallax_layout_list&quot;:[]}\">\n\t\t\t\t\t\t<div class=\"elementor-container elementor-column-gap-default\">\n\t\t\t\t\t<div class=\"elementor-column elementor-col-50 elementor-top-column elementor-element elementor-element-2113bb2\" data-id=\"2113bb2\" data-element_type=\"column\" data-e-type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-4a8d3b3 elementor-widget elementor-widget-text-editor\" data-id=\"4a8d3b3\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<p>Amyotrophies bulbo-spinales de l\u2019enfant<\/p>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t<div class=\"elementor-column elementor-col-50 elementor-top-column elementor-element elementor-element-3f07b4a\" data-id=\"3f07b4a\" data-element_type=\"column\" data-e-type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-257b6ca elementor-widget elementor-widget-text-editor\" data-id=\"257b6ca\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\tPathologie qui touche les muscles impliqu\u00e9s dans la parole, la d\u00e9glutition et la respiration.\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/section>\n\t\t\t\t<section class=\"elementor-section elementor-top-section elementor-element elementor-element-b51426d elementor-hidden-tablet elementor-hidden-mobile elementor-section-boxed elementor-section-height-default elementor-section-height-default\" data-id=\"b51426d\" data-element_type=\"section\" data-e-type=\"section\" data-settings=\"{&quot;jet_parallax_layout_list&quot;:[]}\">\n\t\t\t\t\t\t<div class=\"elementor-container elementor-column-gap-default\">\n\t\t\t\t\t<div class=\"elementor-column elementor-col-50 elementor-top-column elementor-element elementor-element-02b6be7\" data-id=\"02b6be7\" data-element_type=\"column\" data-e-type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-861a5e6 elementor-widget elementor-widget-text-editor\" data-id=\"861a5e6\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<p>Dermatomyosite<\/p>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t<div class=\"elementor-column elementor-col-50 elementor-top-column elementor-element elementor-element-060ba70\" data-id=\"060ba70\" data-element_type=\"column\" data-e-type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-95408e2 elementor-widget elementor-widget-text-editor\" data-id=\"95408e2\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\tInflammation des muscles et de la peau, souvent d\u2019origine auto-immune.\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/section>\n\t\t\t\t<section class=\"elementor-section elementor-top-section elementor-element elementor-element-d5eea9c elementor-hidden-tablet elementor-hidden-mobile elementor-section-boxed elementor-section-height-default elementor-section-height-default\" data-id=\"d5eea9c\" data-element_type=\"section\" data-e-type=\"section\" data-settings=\"{&quot;jet_parallax_layout_list&quot;:[]}\">\n\t\t\t\t\t\t<div class=\"elementor-container elementor-column-gap-default\">\n\t\t\t\t\t<div class=\"elementor-column elementor-col-50 elementor-top-column elementor-element elementor-element-b84b44e\" data-id=\"b84b44e\" data-element_type=\"column\" data-e-type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-3e6f52a elementor-widget elementor-widget-text-editor\" data-id=\"3e6f52a\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<p>Dystrophie musculaire de <a href=\"https:\/\/orthopus.com\/fr\/maladies-neuromusculaires\/dystrophie-musculaire-de-duchenne\/\">Duchenne<\/a><\/p>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t<div class=\"elementor-column elementor-col-50 elementor-top-column elementor-element elementor-element-c4d6488\" data-id=\"c4d6488\" data-element_type=\"column\" data-e-type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-7eb5690 elementor-widget elementor-widget-text-editor\" data-id=\"7eb5690\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\tMaladie g\u00e9n\u00e9tique grave affectant principalement les gar\u00e7ons, entra\u00eenant une perte de force progressive.\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/section>\n\t\t\t\t<section class=\"elementor-section elementor-top-section elementor-element elementor-element-686d7e0 elementor-hidden-tablet elementor-hidden-mobile elementor-section-boxed elementor-section-height-default elementor-section-height-default\" data-id=\"686d7e0\" data-element_type=\"section\" data-e-type=\"section\" data-settings=\"{&quot;jet_parallax_layout_list&quot;:[]}\">\n\t\t\t\t\t\t<div class=\"elementor-container elementor-column-gap-default\">\n\t\t\t\t\t<div class=\"elementor-column elementor-col-50 elementor-top-column elementor-element elementor-element-ec74cc6\" data-id=\"ec74cc6\" data-element_type=\"column\" data-e-type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-9e0fa03 elementor-widget elementor-widget-text-editor\" data-id=\"9e0fa03\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<p>Dystrophie musculaire de <a href=\"https:\/\/orthopus.com\/fr\/maladies-neuromusculaires\/dystrophie-musculaire-de-becker\/\">Becker<\/a><\/p>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t<div class=\"elementor-column elementor-col-50 elementor-top-column elementor-element elementor-element-53ec104\" data-id=\"53ec104\" data-element_type=\"column\" data-e-type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-73f4257 elementor-widget elementor-widget-text-editor\" data-id=\"73f4257\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\tVariante plus mod\u00e9r\u00e9e de la dystrophie de Duchenne.\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/section>\n\t\t\t\t<section class=\"elementor-section elementor-top-section elementor-element elementor-element-fdbea30 elementor-hidden-tablet elementor-hidden-mobile elementor-section-boxed elementor-section-height-default elementor-section-height-default\" data-id=\"fdbea30\" data-element_type=\"section\" data-e-type=\"section\" data-settings=\"{&quot;jet_parallax_layout_list&quot;:[]}\">\n\t\t\t\t\t\t<div class=\"elementor-container elementor-column-gap-default\">\n\t\t\t\t\t<div class=\"elementor-column elementor-col-50 elementor-top-column elementor-element elementor-element-8ae143a\" data-id=\"8ae143a\" data-element_type=\"column\" data-e-type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-d5b0694 elementor-widget elementor-widget-text-editor\" data-id=\"d5b0694\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<p>Dystrophies musculaires d\u2019Emery-Dreifuss<\/p>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t<div class=\"elementor-column elementor-col-50 elementor-top-column elementor-element elementor-element-ed26016\" data-id=\"ed26016\" data-element_type=\"column\" data-e-type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-14a1165 elementor-widget elementor-widget-text-editor\" data-id=\"14a1165\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\tPathologie qui affecte les muscles et le c\u0153ur, avec rigidit\u00e9 articulaire et faiblesse musculaire.\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/section>\n\t\t\t\t<section class=\"elementor-section elementor-top-section elementor-element elementor-element-9cf8750 elementor-hidden-tablet elementor-hidden-mobile elementor-section-boxed elementor-section-height-default elementor-section-height-default\" data-id=\"9cf8750\" data-element_type=\"section\" data-e-type=\"section\" data-settings=\"{&quot;jet_parallax_layout_list&quot;:[]}\">\n\t\t\t\t\t\t<div class=\"elementor-container elementor-column-gap-default\">\n\t\t\t\t\t<div class=\"elementor-column elementor-col-50 elementor-top-column elementor-element elementor-element-ba6bfd0\" data-id=\"ba6bfd0\" data-element_type=\"column\" data-e-type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-dec025f elementor-widget elementor-widget-text-editor\" data-id=\"dec025f\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<p>Dystrophie musculaire oculopharyng\u00e9e<\/p>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t<div class=\"elementor-column elementor-col-50 elementor-top-column elementor-element elementor-element-10d61ae\" data-id=\"10d61ae\" data-element_type=\"column\" data-e-type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-f7d5107 elementor-widget elementor-widget-text-editor\" data-id=\"f7d5107\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\tPathologie qui touche les muscles des paupi\u00e8res et de la gorge, avec chute des paupi\u00e8res et difficult\u00e9 \u00e0 avaler.\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/section>\n\t\t\t\t<section class=\"elementor-section elementor-top-section elementor-element elementor-element-bf411d4 elementor-hidden-tablet elementor-hidden-mobile elementor-section-boxed elementor-section-height-default elementor-section-height-default\" data-id=\"bf411d4\" data-element_type=\"section\" data-e-type=\"section\" data-settings=\"{&quot;jet_parallax_layout_list&quot;:[]}\">\n\t\t\t\t\t\t<div class=\"elementor-container elementor-column-gap-default\">\n\t\t\t\t\t<div class=\"elementor-column elementor-col-50 elementor-top-column elementor-element elementor-element-21fa669\" data-id=\"21fa669\" data-element_type=\"column\" data-e-type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-d6973a9 elementor-widget elementor-widget-text-editor\" data-id=\"d6973a9\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<p>Dystrophie myotonique de Steinert<\/p>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t<div class=\"elementor-column elementor-col-50 elementor-top-column elementor-element elementor-element-0125a1e\" data-id=\"0125a1e\" data-element_type=\"column\" data-e-type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-1b84e59 elementor-widget elementor-widget-text-editor\" data-id=\"1b84e59\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\tMaladie multisyst\u00e9mique avec myotonie (difficult\u00e9 \u00e0 rel\u00e2cher un muscle apr\u00e8s contraction), troubles cardiaques et endocriniens.\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/section>\n\t\t\t\t<section class=\"elementor-section elementor-top-section elementor-element elementor-element-9d23d91 elementor-hidden-tablet elementor-hidden-mobile elementor-section-boxed elementor-section-height-default elementor-section-height-default\" data-id=\"9d23d91\" data-element_type=\"section\" data-e-type=\"section\" data-settings=\"{&quot;jet_parallax_layout_list&quot;:[]}\">\n\t\t\t\t\t\t<div class=\"elementor-container elementor-column-gap-default\">\n\t\t\t\t\t<div class=\"elementor-column elementor-col-50 elementor-top-column elementor-element elementor-element-630e9df\" data-id=\"630e9df\" data-element_type=\"column\" data-e-type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-260b0db elementor-widget__width-initial elementor-widget elementor-widget-text-editor\" data-id=\"260b0db\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<p>Dystrophie myotonique de type 2<\/p>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t<div class=\"elementor-column elementor-col-50 elementor-top-column elementor-element elementor-element-5d7aea3\" data-id=\"5d7aea3\" data-element_type=\"column\" data-e-type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-7e95a20 elementor-widget elementor-widget-text-editor\" data-id=\"7e95a20\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\tForme plus l\u00e9g\u00e8re de la dystrophie myotonique avec atteinte proximale (les muscles proches du tronc comme le cou, les hanches, les \u00e9paules, etc.).\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/section>\n\t\t\t\t<section class=\"elementor-section elementor-top-section elementor-element elementor-element-5413a89 elementor-hidden-tablet elementor-hidden-mobile elementor-section-boxed elementor-section-height-default elementor-section-height-default\" data-id=\"5413a89\" data-element_type=\"section\" data-e-type=\"section\" data-settings=\"{&quot;jet_parallax_layout_list&quot;:[]}\">\n\t\t\t\t\t\t<div class=\"elementor-container elementor-column-gap-default\">\n\t\t\t\t\t<div class=\"elementor-column elementor-col-50 elementor-top-column elementor-element elementor-element-7ecfc9e\" data-id=\"7ecfc9e\" data-element_type=\"column\" data-e-type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-5ba478e elementor-widget elementor-widget-text-editor\" data-id=\"5ba478e\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<p>Dystrophies musculaires cong\u00e9nitales<\/p>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t<div class=\"elementor-column elementor-col-50 elementor-top-column elementor-element elementor-element-8384df4\" data-id=\"8384df4\" data-element_type=\"column\" data-e-type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-1630079 elementor-widget elementor-widget-text-editor\" data-id=\"1630079\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\tAnomalies musculaires pr\u00e9sentes d\u00e8s la naissance avec un retard moteur.\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/section>\n\t\t\t\t<section class=\"elementor-section elementor-top-section elementor-element elementor-element-e5e7509 elementor-hidden-tablet elementor-hidden-mobile elementor-section-boxed elementor-section-height-default elementor-section-height-default\" data-id=\"e5e7509\" data-element_type=\"section\" data-e-type=\"section\" data-settings=\"{&quot;jet_parallax_layout_list&quot;:[]}\">\n\t\t\t\t\t\t<div class=\"elementor-container elementor-column-gap-default\">\n\t\t\t\t\t<div class=\"elementor-column elementor-col-50 elementor-top-column elementor-element elementor-element-04e0eb7\" data-id=\"04e0eb7\" data-element_type=\"column\" data-e-type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-365b96f elementor-widget elementor-widget-text-editor\" data-id=\"365b96f\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<p><a href=\"https:\/\/orthopus.com\/fr\/maladies-neuromusculaires\/maladies-neuromusculaires-charcot-marie-tooth\/\">Maladie de Charcot-Marie-Tooth<\/a><\/p>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t<div class=\"elementor-column elementor-col-50 elementor-top-column elementor-element elementor-element-d02039c\" data-id=\"d02039c\" data-element_type=\"column\" data-e-type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-25c44f8 elementor-widget elementor-widget-text-editor\" data-id=\"25c44f8\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\tAtteinte des nerfs p\u00e9riph\u00e9riques (nerfs qui relient le cerveau aux muscles), provoquant faiblesse et atrophie musculaire.\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/section>\n\t\t\t\t<section class=\"elementor-section elementor-top-section elementor-element elementor-element-44a2cdb elementor-hidden-tablet elementor-hidden-mobile elementor-section-boxed elementor-section-height-default elementor-section-height-default\" data-id=\"44a2cdb\" data-element_type=\"section\" data-e-type=\"section\" data-settings=\"{&quot;jet_parallax_layout_list&quot;:[]}\">\n\t\t\t\t\t\t<div class=\"elementor-container elementor-column-gap-default\">\n\t\t\t\t\t<div class=\"elementor-column elementor-col-50 elementor-top-column elementor-element elementor-element-eb58145\" data-id=\"eb58145\" data-element_type=\"column\" data-e-type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-88054e4 elementor-widget elementor-widget-text-editor\" data-id=\"88054e4\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<p>Maladie de McArdle<\/p>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t<div class=\"elementor-column elementor-col-50 elementor-top-column elementor-element elementor-element-d0a2d56\" data-id=\"d0a2d56\" data-element_type=\"column\" data-e-type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-1c9e808 elementor-widget elementor-widget-text-editor\" data-id=\"1c9e808\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\tD\u00e9faut du m\u00e9tabolisme du glycog\u00e8ne (sucre) dans les muscles, entra\u00eenant une intol\u00e9rance \u00e0 l&#8217;effort.\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/section>\n\t\t\t\t<section class=\"elementor-section elementor-top-section elementor-element elementor-element-7556592 elementor-hidden-tablet elementor-hidden-mobile elementor-section-boxed elementor-section-height-default elementor-section-height-default\" data-id=\"7556592\" data-element_type=\"section\" data-e-type=\"section\" data-settings=\"{&quot;jet_parallax_layout_list&quot;:[]}\">\n\t\t\t\t\t\t<div class=\"elementor-container elementor-column-gap-default\">\n\t\t\t\t\t<div class=\"elementor-column elementor-col-50 elementor-top-column elementor-element elementor-element-c13b98d\" data-id=\"c13b98d\" data-element_type=\"column\" data-e-type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-f5d32e8 elementor-widget elementor-widget-text-editor\" data-id=\"f5d32e8\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<p>Maladie de Pompe (forme infantile)<\/p>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t<div class=\"elementor-column elementor-col-50 elementor-top-column elementor-element elementor-element-b3cd4d0\" data-id=\"b3cd4d0\" data-element_type=\"column\" data-e-type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-2a4996d elementor-widget elementor-widget-text-editor\" data-id=\"2a4996d\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\tMaladie rare du nourrisson li\u00e9e \u00e0 un d\u00e9faut de d\u00e9gradation du sucre (glycog\u00e8ne) dans les muscles. Ce sucre s\u2019accumule, ce qui fait gonfler et affaiblir les muscles.\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/section>\n\t\t\t\t<section class=\"elementor-section elementor-top-section elementor-element elementor-element-f263681 elementor-hidden-tablet elementor-hidden-mobile elementor-section-boxed elementor-section-height-default elementor-section-height-default\" data-id=\"f263681\" data-element_type=\"section\" data-e-type=\"section\" data-settings=\"{&quot;jet_parallax_layout_list&quot;:[]}\">\n\t\t\t\t\t\t<div class=\"elementor-container elementor-column-gap-default\">\n\t\t\t\t\t<div class=\"elementor-column elementor-col-50 elementor-top-column elementor-element elementor-element-d8c4765\" data-id=\"d8c4765\" data-element_type=\"column\" data-e-type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-2660861 elementor-widget elementor-widget-text-editor\" data-id=\"2660861\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<p>Myasth\u00e9nie auto-immune<\/p>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t<div class=\"elementor-column elementor-col-50 elementor-top-column elementor-element elementor-element-165701d\" data-id=\"165701d\" data-element_type=\"column\" data-e-type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-fa86c99 elementor-widget elementor-widget-text-editor\" data-id=\"fa86c99\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\tAffection de la jonction neuromusculaire (lieu o\u00f9 un nerf ordonne \u00e0 un muscle de bouger) entra\u00eenant une faiblesse fluctuante.\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/section>\n\t\t\t\t<section class=\"elementor-section elementor-top-section elementor-element elementor-element-4084173 elementor-hidden-tablet elementor-hidden-mobile elementor-section-boxed elementor-section-height-default elementor-section-height-default\" data-id=\"4084173\" data-element_type=\"section\" data-e-type=\"section\" data-settings=\"{&quot;jet_parallax_layout_list&quot;:[]}\">\n\t\t\t\t\t\t<div class=\"elementor-container elementor-column-gap-default\">\n\t\t\t\t\t<div class=\"elementor-column elementor-col-50 elementor-top-column elementor-element elementor-element-e304a24\" data-id=\"e304a24\" data-element_type=\"column\" data-e-type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-a7c8460 elementor-widget elementor-widget-text-editor\" data-id=\"a7c8460\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<p>Myopathie auto-immune n\u00e9crosante<\/p>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t<div class=\"elementor-column elementor-col-50 elementor-top-column elementor-element elementor-element-be0a99f\" data-id=\"be0a99f\" data-element_type=\"column\" data-e-type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-dcb1f18 elementor-widget elementor-widget-text-editor\" data-id=\"dcb1f18\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\tInflammation musculaire grave causant une n\u00e9crose (mort cellulaire) rapide des fibres musculaires.\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/section>\n\t\t\t\t<section class=\"elementor-section elementor-top-section elementor-element elementor-element-f779b44 elementor-hidden-tablet elementor-hidden-mobile elementor-section-boxed elementor-section-height-default elementor-section-height-default\" data-id=\"f779b44\" data-element_type=\"section\" data-e-type=\"section\" data-settings=\"{&quot;jet_parallax_layout_list&quot;:[]}\">\n\t\t\t\t\t\t<div class=\"elementor-container elementor-column-gap-default\">\n\t\t\t\t\t<div class=\"elementor-column elementor-col-50 elementor-top-column elementor-element elementor-element-e6c7c18\" data-id=\"e6c7c18\" data-element_type=\"column\" data-e-type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-4bdb18b elementor-widget elementor-widget-text-editor\" data-id=\"4bdb18b\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<p>Myopathie GNE<\/p>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t<div class=\"elementor-column elementor-col-50 elementor-top-column elementor-element elementor-element-39182f2\" data-id=\"39182f2\" data-element_type=\"column\" data-e-type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-1405b2c elementor-widget elementor-widget-text-editor\" data-id=\"1405b2c\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\tMaladie rare affectant les muscles distaux (les pieds et les jambes) des membres inf\u00e9rieurs.\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/section>\n\t\t\t\t<section class=\"elementor-section elementor-top-section elementor-element elementor-element-356ba78 elementor-hidden-tablet elementor-hidden-mobile elementor-section-boxed elementor-section-height-default elementor-section-height-default\" data-id=\"356ba78\" data-element_type=\"section\" data-e-type=\"section\" data-settings=\"{&quot;jet_parallax_layout_list&quot;:[]}\">\n\t\t\t\t\t\t<div class=\"elementor-container elementor-column-gap-default\">\n\t\t\t\t\t<div class=\"elementor-column elementor-col-50 elementor-top-column elementor-element elementor-element-593975e\" data-id=\"593975e\" data-element_type=\"column\" data-e-type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-a4182f9 elementor-widget elementor-widget-text-editor\" data-id=\"a4182f9\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<p>Myopathie \u00e0 n\u00e9maline acquise de l\u2019adulte<\/p>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t<div class=\"elementor-column elementor-col-50 elementor-top-column elementor-element elementor-element-cf24426\" data-id=\"cf24426\" data-element_type=\"column\" data-e-type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-ff402b2 elementor-widget elementor-widget-text-editor\" data-id=\"ff402b2\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\tMaladie rare caract\u00e9ris\u00e9e par la pr\u00e9sence de b\u00e2tonnets anormaux (cellules de l&#8217;\u0153il qui ne fonctionnent pas correctement) dans les fibres musculaires.\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/section>\n\t\t\t\t<section class=\"elementor-section elementor-top-section elementor-element elementor-element-688102e elementor-hidden-tablet elementor-hidden-mobile elementor-section-boxed elementor-section-height-default elementor-section-height-default\" data-id=\"688102e\" data-element_type=\"section\" data-e-type=\"section\" data-settings=\"{&quot;jet_parallax_layout_list&quot;:[]}\">\n\t\t\t\t\t\t<div class=\"elementor-container elementor-column-gap-default\">\n\t\t\t\t\t<div class=\"elementor-column elementor-col-50 elementor-top-column elementor-element elementor-element-63f22c8\" data-id=\"63f22c8\" data-element_type=\"column\" data-e-type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-8576e71 elementor-widget elementor-widget-text-editor\" data-id=\"8576e71\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<p>Myopathies cong\u00e9nitales<\/p>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t<div class=\"elementor-column elementor-col-50 elementor-top-column elementor-element elementor-element-5463316\" data-id=\"5463316\" data-element_type=\"column\" data-e-type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-d6ace40 elementor-widget elementor-widget-text-editor\" data-id=\"d6ace40\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\tTroubles musculaires d\u2019origine g\u00e9n\u00e9tique, apparus d\u00e8s l\u2019enfance.\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/section>\n\t\t\t\t<section class=\"elementor-section elementor-top-section elementor-element elementor-element-1dadae9 elementor-hidden-tablet elementor-hidden-mobile elementor-section-boxed elementor-section-height-default elementor-section-height-default\" data-id=\"1dadae9\" data-element_type=\"section\" data-e-type=\"section\" data-settings=\"{&quot;jet_parallax_layout_list&quot;:[]}\">\n\t\t\t\t\t\t<div class=\"elementor-container elementor-column-gap-default\">\n\t\t\t\t\t<div class=\"elementor-column elementor-col-50 elementor-top-column elementor-element elementor-element-27240e6\" data-id=\"27240e6\" data-element_type=\"column\" data-e-type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-55246ed elementor-widget elementor-widget-text-editor\" data-id=\"55246ed\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<p>Myopathies des ceintures<\/p>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t<div class=\"elementor-column elementor-col-50 elementor-top-column elementor-element elementor-element-18aed2d\" data-id=\"18aed2d\" data-element_type=\"column\" data-e-type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-23c56ad elementor-widget elementor-widget-text-editor\" data-id=\"23c56ad\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<p>Faiblesse des muscles des hanches et des \u00e9paules.<\/p>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/section>\n\t\t\t\t<section class=\"elementor-section elementor-top-section elementor-element elementor-element-fc5dc89 elementor-hidden-tablet elementor-hidden-mobile elementor-section-boxed elementor-section-height-default elementor-section-height-default\" data-id=\"fc5dc89\" data-element_type=\"section\" data-e-type=\"section\" data-settings=\"{&quot;jet_parallax_layout_list&quot;:[]}\">\n\t\t\t\t\t\t<div class=\"elementor-container elementor-column-gap-default\">\n\t\t\t\t\t<div class=\"elementor-column elementor-col-50 elementor-top-column elementor-element elementor-element-73f29dc\" data-id=\"73f29dc\" data-element_type=\"column\" data-e-type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-5b56d3a elementor-widget elementor-widget-text-editor\" data-id=\"5b56d3a\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<p>Myopathies distales<\/p>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t<div class=\"elementor-column elementor-col-50 elementor-top-column elementor-element elementor-element-5243e0f\" data-id=\"5243e0f\" data-element_type=\"column\" data-e-type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-5686c0b elementor-widget elementor-widget-text-editor\" data-id=\"5686c0b\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\tFaiblesse musculaire touchant d&#8217;abord les extr\u00e9mit\u00e9s (mains, pieds).\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/section>\n\t\t\t\t<section class=\"elementor-section elementor-top-section elementor-element elementor-element-2ce953e elementor-hidden-tablet elementor-hidden-mobile elementor-section-boxed elementor-section-height-default elementor-section-height-default\" data-id=\"2ce953e\" data-element_type=\"section\" data-e-type=\"section\" data-settings=\"{&quot;jet_parallax_layout_list&quot;:[]}\">\n\t\t\t\t\t\t<div class=\"elementor-container elementor-column-gap-default\">\n\t\t\t\t\t<div class=\"elementor-column elementor-col-50 elementor-top-column elementor-element elementor-element-13cfcd1\" data-id=\"13cfcd1\" data-element_type=\"column\" data-e-type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-1e2ae84 elementor-widget elementor-widget-text-editor\" data-id=\"1e2ae84\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<p>Myopathies mitochondriales<\/p>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t<div class=\"elementor-column elementor-col-50 elementor-top-column elementor-element elementor-element-8817c70\" data-id=\"8817c70\" data-element_type=\"column\" data-e-type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-b7e68c4 elementor-widget elementor-widget-text-editor\" data-id=\"b7e68c4\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\tD\u00e9fauts dans la production d&#8217;\u00e9nergie cellulaire (\u00e9nergie produite par la nourriture et l\u2019oxyg\u00e8ne que nous consommons, servant \u00e0 faire fonctionner les cellules), touchant souvent plusieurs organes.\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/section>\n\t\t\t\t<section class=\"elementor-section elementor-top-section elementor-element elementor-element-160813d elementor-hidden-tablet elementor-hidden-mobile elementor-section-boxed elementor-section-height-default elementor-section-height-default\" data-id=\"160813d\" data-element_type=\"section\" data-e-type=\"section\" data-settings=\"{&quot;jet_parallax_layout_list&quot;:[]}\">\n\t\t\t\t\t\t<div class=\"elementor-container elementor-column-gap-default\">\n\t\t\t\t\t<div class=\"elementor-column elementor-col-50 elementor-top-column elementor-element elementor-element-7cc6a9a\" data-id=\"7cc6a9a\" data-element_type=\"column\" data-e-type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-ceb1a54 elementor-widget elementor-widget-text-editor\" data-id=\"ceb1a54\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<p>Myopathies myofibrillaires<\/p>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t<div class=\"elementor-column elementor-col-50 elementor-top-column elementor-element elementor-element-0350236\" data-id=\"0350236\" data-element_type=\"column\" data-e-type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-a065ced elementor-widget elementor-widget-text-editor\" data-id=\"a065ced\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\tD\u00e9sorganisation des fibres musculaires (cellules du muscle, fines et longues, qui se serrent et se d\u00e9tendent pour permettre de bouger), entra\u00eenant une perte de force progressive.\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/section>\n\t\t\t\t<section class=\"elementor-section elementor-top-section elementor-element elementor-element-ac620fd elementor-hidden-tablet elementor-hidden-mobile elementor-section-boxed elementor-section-height-default elementor-section-height-default\" data-id=\"ac620fd\" data-element_type=\"section\" data-e-type=\"section\" data-settings=\"{&quot;jet_parallax_layout_list&quot;:[]}\">\n\t\t\t\t\t\t<div class=\"elementor-container elementor-column-gap-default\">\n\t\t\t\t\t<div class=\"elementor-column elementor-col-50 elementor-top-column elementor-element elementor-element-d306d96\" data-id=\"d306d96\" data-element_type=\"column\" data-e-type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-c9d2556 elementor-widget elementor-widget-text-editor\" data-id=\"c9d2556\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<p>Myotonies cong\u00e9nitales (Thomsen et Becker)<\/p>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t<div class=\"elementor-column elementor-col-50 elementor-top-column elementor-element elementor-element-554ece9\" data-id=\"554ece9\" data-element_type=\"column\" data-e-type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-461855b elementor-widget elementor-widget-text-editor\" data-id=\"461855b\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\tDifficult\u00e9 \u00e0 rel\u00e2cher les muscles apr\u00e8s contraction, pr\u00e9sente d\u00e8s la naissance.\n\n\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/section>\n\t\t\t\t<section class=\"elementor-section elementor-top-section elementor-element elementor-element-b345fd1 elementor-hidden-tablet elementor-hidden-mobile elementor-section-boxed elementor-section-height-default elementor-section-height-default\" data-id=\"b345fd1\" data-element_type=\"section\" data-e-type=\"section\" data-settings=\"{&quot;jet_parallax_layout_list&quot;:[]}\">\n\t\t\t\t\t\t<div class=\"elementor-container elementor-column-gap-default\">\n\t\t\t\t\t<div class=\"elementor-column elementor-col-50 elementor-top-column elementor-element elementor-element-a5c9b81\" data-id=\"a5c9b81\" data-element_type=\"column\" data-e-type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-70a352c elementor-widget elementor-widget-text-editor\" data-id=\"70a352c\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<p>Myosites \u00e0 inclusions<\/p>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t<div class=\"elementor-column elementor-col-50 elementor-top-column elementor-element elementor-element-bc2606d\" data-id=\"bc2606d\" data-element_type=\"column\" data-e-type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-f1fcb47 elementor-widget elementor-widget-text-editor\" data-id=\"f1fcb47\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\tInflammation chronique des muscles avec inclusions anormales dans les fibres (d\u00e9p\u00f4ts parasites qui s&#8217;accumulent).\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/section>\n\t\t\t\t<section class=\"elementor-section elementor-top-section elementor-element elementor-element-c468c95 elementor-hidden-tablet elementor-hidden-mobile elementor-section-boxed elementor-section-height-default elementor-section-height-default\" data-id=\"c468c95\" data-element_type=\"section\" data-e-type=\"section\" data-settings=\"{&quot;jet_parallax_layout_list&quot;:[]}\">\n\t\t\t\t\t\t<div class=\"elementor-container elementor-column-gap-default\">\n\t\t\t\t\t<div class=\"elementor-column elementor-col-50 elementor-top-column elementor-element elementor-element-b60c823\" data-id=\"b60c823\" data-element_type=\"column\" data-e-type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-873c5fe elementor-widget elementor-widget-text-editor\" data-id=\"873c5fe\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<p>Paramyotonie d\u2019Eulenburg<\/p>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t<div class=\"elementor-column elementor-col-50 elementor-top-column elementor-element elementor-element-ab47d93\" data-id=\"ab47d93\" data-element_type=\"column\" data-e-type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-147da87 elementor-widget elementor-widget-text-editor\" data-id=\"147da87\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\tMyotonie (difficult\u00e9 \u00e0 rel\u00e2cher un muscle apr\u00e8s contraction) aggrav\u00e9e par le froid, affectant les muscles faciaux et des membres.\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/section>\n\t\t\t\t<section class=\"elementor-section elementor-top-section elementor-element elementor-element-ecb4b54 elementor-hidden-tablet elementor-hidden-mobile elementor-section-boxed elementor-section-height-default elementor-section-height-default\" data-id=\"ecb4b54\" data-element_type=\"section\" data-e-type=\"section\" data-settings=\"{&quot;jet_parallax_layout_list&quot;:[]}\">\n\t\t\t\t\t\t<div class=\"elementor-container elementor-column-gap-default\">\n\t\t\t\t\t<div class=\"elementor-column elementor-col-50 elementor-top-column elementor-element elementor-element-dd739a1\" data-id=\"dd739a1\" data-element_type=\"column\" data-e-type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-decc7dd elementor-widget elementor-widget-text-editor\" data-id=\"decc7dd\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<p>Paralysies p\u00e9riodiques hypo\/hyperkali\u00e9miques<\/p>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t<div class=\"elementor-column elementor-col-50 elementor-top-column elementor-element elementor-element-32710c6\" data-id=\"32710c6\" data-element_type=\"column\" data-e-type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-230afd9 elementor-widget elementor-widget-text-editor\" data-id=\"230afd9\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\tCrises temporaires o\u00f9 la personne ne peut plus bouger ses muscles, comme si elle \u00e9tait &#8220;paralys\u00e9e&#8221; pendant un moment.\nElles sont caus\u00e9es par un d\u00e9s\u00e9quilibre du potassium dans le sang. Ce potassium est essentiel pour que les muscles re\u00e7oivent les bons signaux du cerveau.\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/section>\n\t\t\t\t<section class=\"elementor-section elementor-top-section elementor-element elementor-element-dcd1820 elementor-hidden-tablet elementor-hidden-mobile elementor-section-boxed elementor-section-height-default elementor-section-height-default\" data-id=\"dcd1820\" data-element_type=\"section\" data-e-type=\"section\" data-settings=\"{&quot;jet_parallax_layout_list&quot;:[]}\">\n\t\t\t\t\t\t<div class=\"elementor-container elementor-column-gap-default\">\n\t\t\t\t\t<div class=\"elementor-column elementor-col-50 elementor-top-column elementor-element elementor-element-899f152\" data-id=\"899f152\" data-element_type=\"column\" data-e-type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-80321da elementor-widget elementor-widget-text-editor\" data-id=\"80321da\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<p>Syndrome des antisynth\u00e9tases<\/p>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t<div class=\"elementor-column elementor-col-50 elementor-top-column elementor-element elementor-element-3342467\" data-id=\"3342467\" data-element_type=\"column\" data-e-type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-9ea67a5 elementor-widget elementor-widget-text-editor\" data-id=\"9ea67a5\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\tMaladie auto-immune avec atteinte musculaire, articulaire et pulmonaire.\n\n\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/section>\n\t\t\t\t<section class=\"elementor-section elementor-top-section elementor-element elementor-element-a702c7f elementor-hidden-tablet elementor-hidden-mobile elementor-section-boxed elementor-section-height-default elementor-section-height-default\" data-id=\"a702c7f\" data-element_type=\"section\" data-e-type=\"section\" data-settings=\"{&quot;jet_parallax_layout_list&quot;:[]}\">\n\t\t\t\t\t\t<div class=\"elementor-container elementor-column-gap-default\">\n\t\t\t\t\t<div class=\"elementor-column elementor-col-50 elementor-top-column elementor-element elementor-element-a8254d8\" data-id=\"a8254d8\" data-element_type=\"column\" data-e-type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-2df5024 elementor-widget elementor-widget-text-editor\" data-id=\"2df5024\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<p>Syndromes myasth\u00e9niques cong\u00e9nitaux<\/p>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t<div class=\"elementor-column elementor-col-50 elementor-top-column elementor-element elementor-element-e8fbc2d\" data-id=\"e8fbc2d\" data-element_type=\"column\" data-e-type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-94c452a elementor-widget elementor-widget-text-editor\" data-id=\"94c452a\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\tD\u00e9fauts h\u00e9r\u00e9ditaires de la transmission entre nerf et muscle.\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/section>\n\t\t<div class=\"elementor-element elementor-element-6036a86 elementor-hidden-desktop e-flex e-con-boxed e-con e-parent\" data-id=\"6036a86\" data-element_type=\"container\" data-e-type=\"container\" data-settings=\"{&quot;jet_parallax_layout_list&quot;:[]}\">\n\t\t\t\t\t<div class=\"e-con-inner\">\n\t\t\t\t<div class=\"elementor-element elementor-element-b137478 elementor-widget elementor-widget-jet-table\" data-id=\"b137478\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"jet-table.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t<div class=\"elementor-jet-table jet-elements\">\n\t\t<div class=\"jet-table-wrapper jet-table-responsive-tablet jet-table-responsive-mobile\">\n\t\t\t<table class=\"jet-table jet-table--fa5-compat\">\n\t\t\t\t<thead class=\"jet-table__head\"><tr class=\"jet-table__head-row\"><th class=\"jet-table__cell elementor-repeater-item-83d94a3 jet-table__head-cell\" colspan=\"1\" scope=\"col\"><div class=\"jet-table__cell-inner\"><div class=\"jet-table__cell-content\"><div class=\"jet-table__cell-text\">Nom<\/div><\/div><\/div><\/th><th class=\"jet-table__cell elementor-repeater-item-493e60a jet-table__head-cell\" colspan=\"1\" scope=\"col\"><div class=\"jet-table__cell-inner\"><div class=\"jet-table__cell-content\"><div class=\"jet-table__cell-text\">Description synth\u00e9tique<\/div><\/div><\/div><\/th><\/tr><\/thead>\n\t\t\t\t\t\t\t\t<tbody class=\"jet-table__body\"><td class=\"jet-table__cell elementor-repeater-item-758ae34 jet-table__body-cell\"><a class=\"jet-table__cell-inner jet-table__cell-link\" href=\"https:\/\/orthopus.com\/fr\/maladies-neuromusculaires\/maladies-neuromusculaires-amyotrophie-spinale-proximale\/\"><div class=\"jet-table__cell-content\"><div class=\"jet-table__cell-text\">Amyotrophie spinale proximale (SMN1)\n\n<\/div><\/div><\/a><\/td><td class=\"jet-table__cell elementor-repeater-item-528d336 jet-table__body-cell\"><div class=\"jet-table__cell-inner\"><div class=\"jet-table__cell-content\"><div class=\"jet-table__cell-text\">D\u00e9g\u00e9n\u00e9rescence des motoneurones entra\u00eenant une faiblesse musculaire grave.<\/div><\/div><\/div><\/td><tr class=\"jet-table__body-row elementor-repeater-item-a35ff46\"><td class=\"jet-table__cell elementor-repeater-item-7bfd3f6 jet-table__body-cell\"><div class=\"jet-table__cell-inner\"><div class=\"jet-table__cell-content\"><div class=\"jet-table__cell-text\">Amyotrophies bulbo-spinales de l\u2019enfant\n\n\n<\/div><\/div><\/div><\/td><td class=\"jet-table__cell elementor-repeater-item-da5fffa jet-table__body-cell\"><div class=\"jet-table__cell-inner\"><div class=\"jet-table__cell-content\"><div class=\"jet-table__cell-text\">Pathologie qui touche les muscles impliqu\u00e9s dans la parole, la d\u00e9glutition et la respiration.<\/div><\/div><\/div><\/td><\/tr><tr class=\"jet-table__body-row elementor-repeater-item-be9f1b4\"><td class=\"jet-table__cell elementor-repeater-item-277bd30 jet-table__body-cell\"><div class=\"jet-table__cell-inner\"><div class=\"jet-table__cell-content\"><div class=\"jet-table__cell-text\">Dermatomyosite\n<\/div><\/div><\/div><\/td><td class=\"jet-table__cell elementor-repeater-item-8b20398 jet-table__body-cell\"><div class=\"jet-table__cell-inner\"><div class=\"jet-table__cell-content\"><div class=\"jet-table__cell-text\">Inflammation des muscles et de la peau, souvent d\u2019origine auto-immune.<\/div><\/div><\/div><\/td><\/tr><tr class=\"jet-table__body-row elementor-repeater-item-22ed66e\"><td class=\"jet-table__cell elementor-repeater-item-d1622a3 jet-table__body-cell\"><a class=\"jet-table__cell-inner jet-table__cell-link\" href=\"https:\/\/orthopus.com\/fr\/maladies-neuromusculaires\/dystrophie-musculaire-de-duchenne\/\"><div class=\"jet-table__cell-content\"><div class=\"jet-table__cell-text\">Dystrophie musculaire de Duchenne\n\n\n<\/div><\/div><\/a><\/td><td class=\"jet-table__cell elementor-repeater-item-078049a jet-table__body-cell\"><div class=\"jet-table__cell-inner\"><div class=\"jet-table__cell-content\"><div class=\"jet-table__cell-text\">Maladie g\u00e9n\u00e9tique grave affectant principalement les gar\u00e7ons, entra\u00eenant une perte de force progressive.<\/div><\/div><\/div><\/td><\/tr><tr class=\"jet-table__body-row elementor-repeater-item-aa0e7ad\"><td class=\"jet-table__cell elementor-repeater-item-a2355fd jet-table__body-cell\"><a class=\"jet-table__cell-inner jet-table__cell-link\" href=\"https:\/\/orthopus.com\/fr\/maladies-neuromusculaires\/dystrophie-musculaire-de-becker\/\"><div class=\"jet-table__cell-content\"><div class=\"jet-table__cell-text\">Dystrophie musculaire de Becker<\/div><\/div><\/a><\/td><td class=\"jet-table__cell elementor-repeater-item-362c02c jet-table__body-cell\"><div class=\"jet-table__cell-inner\"><div class=\"jet-table__cell-content\"><div class=\"jet-table__cell-text\">Variante plus mod\u00e9r\u00e9e de la dystrophie de Duchenne.<\/div><\/div><\/div><\/td><\/tr><tr class=\"jet-table__body-row elementor-repeater-item-71b5793\"><td class=\"jet-table__cell elementor-repeater-item-f071468 jet-table__body-cell\"><div class=\"jet-table__cell-inner\"><div class=\"jet-table__cell-content\"><div class=\"jet-table__cell-text\">Dystrophies musculaires d\u2019Emery-Dreifuss<\/div><\/div><\/div><\/td><td class=\"jet-table__cell elementor-repeater-item-9182699 jet-table__body-cell\"><div class=\"jet-table__cell-inner\"><div class=\"jet-table__cell-content\"><div class=\"jet-table__cell-text\">Pathologie qui affecte les muscles et le c\u0153ur, avec rigidit\u00e9 articulaire et faiblesse musculaire.<\/div><\/div><\/div><\/td><\/tr><tr class=\"jet-table__body-row elementor-repeater-item-249acff\"><td class=\"jet-table__cell elementor-repeater-item-31ed03b jet-table__body-cell\"><div class=\"jet-table__cell-inner\"><div class=\"jet-table__cell-content\"><div class=\"jet-table__cell-text\">Dystrophie musculaire oculopharyng\u00e9e<\/div><\/div><\/div><\/td><td class=\"jet-table__cell elementor-repeater-item-3f15089 jet-table__body-cell\"><div class=\"jet-table__cell-inner\"><div class=\"jet-table__cell-content\"><div class=\"jet-table__cell-text\">Pathologie qui touche les muscles des paupi\u00e8res et de la gorge, avec chute des paupi\u00e8res et difficult\u00e9 \u00e0 avaler.<\/div><\/div><\/div><\/td><\/tr><tr class=\"jet-table__body-row elementor-repeater-item-94cdf77\"><td class=\"jet-table__cell elementor-repeater-item-28277de jet-table__body-cell\"><div class=\"jet-table__cell-inner\"><div class=\"jet-table__cell-content\"><div class=\"jet-table__cell-text\">Dystrophie myotonique de Steinert<\/div><\/div><\/div><\/td><td class=\"jet-table__cell elementor-repeater-item-6ffe642 jet-table__body-cell\"><div class=\"jet-table__cell-inner\"><div class=\"jet-table__cell-content\"><div class=\"jet-table__cell-text\">Maladie multisyst\u00e9mique avec myotonie (difficult\u00e9 \u00e0 rel\u00e2cher un muscle apr\u00e8s contraction), troubles cardiaques et endocriniens.<\/div><\/div><\/div><\/td><\/tr><tr class=\"jet-table__body-row elementor-repeater-item-b7dc001\"><td class=\"jet-table__cell elementor-repeater-item-bb58c06 jet-table__body-cell\"><div class=\"jet-table__cell-inner\"><div class=\"jet-table__cell-content\"><div class=\"jet-table__cell-text\">Dystrophie myotonique de type 2<\/div><\/div><\/div><\/td><td class=\"jet-table__cell elementor-repeater-item-458fbb1 jet-table__body-cell\"><div class=\"jet-table__cell-inner\"><div class=\"jet-table__cell-content\"><div class=\"jet-table__cell-text\">Forme plus l\u00e9g\u00e8re de la dystrophie myotonique avec atteinte proximale (les muscles proches du tronc comme le cou, les hanches, les \u00e9paules, etc.).<\/div><\/div><\/div><\/td><\/tr><tr class=\"jet-table__body-row elementor-repeater-item-0cd1c9a\"><td class=\"jet-table__cell elementor-repeater-item-1c8c2d5 jet-table__body-cell\"><div class=\"jet-table__cell-inner\"><div class=\"jet-table__cell-content\"><div class=\"jet-table__cell-text\">Dystrophies musculaires cong\u00e9nitales<\/div><\/div><\/div><\/td><td class=\"jet-table__cell elementor-repeater-item-98dbaf9 jet-table__body-cell\"><div class=\"jet-table__cell-inner\"><div class=\"jet-table__cell-content\"><div class=\"jet-table__cell-text\">Anomalies musculaires pr\u00e9sentes d\u00e8s la naissance avec un retard moteur.<\/div><\/div><\/div><\/td><\/tr><tr class=\"jet-table__body-row elementor-repeater-item-0507ed5\"><td class=\"jet-table__cell elementor-repeater-item-18c8bca jet-table__body-cell\"><a class=\"jet-table__cell-inner jet-table__cell-link\" href=\"https:\/\/orthopus.com\/fr\/maladies-neuromusculaires\/maladies-neuromusculaires-charcot-marie-tooth\/\"><div class=\"jet-table__cell-content\"><div class=\"jet-table__cell-text\">Maladie de Charcot-Marie-Tooth<\/div><\/div><\/a><\/td><td class=\"jet-table__cell elementor-repeater-item-5022df4 jet-table__body-cell\"><div class=\"jet-table__cell-inner\"><div class=\"jet-table__cell-content\"><div class=\"jet-table__cell-text\">Atteinte des nerfs p\u00e9riph\u00e9riques (nerfs qui relient le cerveau aux muscles), provoquant faiblesse et atrophie musculaire.<\/div><\/div><\/div><\/td><\/tr><tr class=\"jet-table__body-row elementor-repeater-item-0fe5200\"><td class=\"jet-table__cell elementor-repeater-item-b8e6412 jet-table__body-cell\"><div class=\"jet-table__cell-inner\"><div class=\"jet-table__cell-content\"><div class=\"jet-table__cell-text\">Maladie de McArdle<\/div><\/div><\/div><\/td><td class=\"jet-table__cell elementor-repeater-item-68457ea jet-table__body-cell\"><div class=\"jet-table__cell-inner\"><div class=\"jet-table__cell-content\"><div class=\"jet-table__cell-text\">D\u00e9faut du m\u00e9tabolisme du glycog\u00e8ne (sucre) dans les muscles, entra\u00eenant une intol\u00e9rance \u00e0 l\u2019effort.<\/div><\/div><\/div><\/td><\/tr><tr class=\"jet-table__body-row elementor-repeater-item-63a2d7d\"><td class=\"jet-table__cell elementor-repeater-item-6c649cd jet-table__body-cell\"><div class=\"jet-table__cell-inner\"><div class=\"jet-table__cell-content\"><div class=\"jet-table__cell-text\">Maladie de Pompe (forme infantile)<\/div><\/div><\/div><\/td><td class=\"jet-table__cell elementor-repeater-item-0e45c64 jet-table__body-cell\"><div class=\"jet-table__cell-inner\"><div class=\"jet-table__cell-content\"><div class=\"jet-table__cell-text\">Maladie rare du nourrisson li\u00e9e \u00e0 un d\u00e9faut de d\u00e9gradation du sucre (glycog\u00e8ne) dans les muscles. Ce sucre s\u2019accumule, ce qui fait gonfler et affaiblir les muscles.<\/div><\/div><\/div><\/td><\/tr><tr class=\"jet-table__body-row elementor-repeater-item-b246d76\"><td class=\"jet-table__cell elementor-repeater-item-4929b91 jet-table__body-cell\"><div class=\"jet-table__cell-inner\"><div class=\"jet-table__cell-content\"><div class=\"jet-table__cell-text\">Myasth\u00e9nie auto-immune<\/div><\/div><\/div><\/td><td class=\"jet-table__cell elementor-repeater-item-0ead765 jet-table__body-cell\"><div class=\"jet-table__cell-inner\"><div class=\"jet-table__cell-content\"><div class=\"jet-table__cell-text\">Affection de la jonction neuromusculaire (lieu o\u00f9 un nerf ordonne \u00e0 un muscle de bouger) entra\u00eenant une faiblesse fluctuante.<\/div><\/div><\/div><\/td><\/tr><tr class=\"jet-table__body-row elementor-repeater-item-bda529e\"><td class=\"jet-table__cell elementor-repeater-item-d529852 jet-table__body-cell\"><div class=\"jet-table__cell-inner\"><div class=\"jet-table__cell-content\"><div class=\"jet-table__cell-text\">Myopathie auto-immune n\u00e9crosante<\/div><\/div><\/div><\/td><td class=\"jet-table__cell elementor-repeater-item-39e0ae2 jet-table__body-cell\"><div class=\"jet-table__cell-inner\"><div class=\"jet-table__cell-content\"><div class=\"jet-table__cell-text\">Inflammation musculaire grave causant une n\u00e9crose (mort cellulaire) rapide des fibres musculaires.<\/div><\/div><\/div><\/td><\/tr><tr class=\"jet-table__body-row elementor-repeater-item-205a62c\"><td class=\"jet-table__cell elementor-repeater-item-4bf9c15 jet-table__body-cell\"><div class=\"jet-table__cell-inner\"><div class=\"jet-table__cell-content\"><div class=\"jet-table__cell-text\">Myopathie GNE<\/div><\/div><\/div><\/td><td class=\"jet-table__cell elementor-repeater-item-e2f9390 jet-table__body-cell\"><div class=\"jet-table__cell-inner\"><div class=\"jet-table__cell-content\"><div class=\"jet-table__cell-text\">Maladie rare affectant les muscles distaux (les pieds et les jambes) des membres inf\u00e9rieurs.<\/div><\/div><\/div><\/td><\/tr><tr class=\"jet-table__body-row elementor-repeater-item-7fc1ddd\"><td class=\"jet-table__cell elementor-repeater-item-a9f432b jet-table__body-cell\"><div class=\"jet-table__cell-inner\"><div class=\"jet-table__cell-content\"><div class=\"jet-table__cell-text\">Myopathie \u00e0 n\u00e9maline acquise de l\u2019adulte<\/div><\/div><\/div><\/td><td class=\"jet-table__cell elementor-repeater-item-6d2421c jet-table__body-cell\"><div class=\"jet-table__cell-inner\"><div class=\"jet-table__cell-content\"><div class=\"jet-table__cell-text\">Maladie rare caract\u00e9ris\u00e9e par la pr\u00e9sence de b\u00e2tonnets anormaux (cellules de l\u2019\u0153il qui ne fonctionnent pas correctement) dans les fibres musculaires.<\/div><\/div><\/div><\/td><\/tr><tr class=\"jet-table__body-row elementor-repeater-item-034e071\"><td class=\"jet-table__cell elementor-repeater-item-1a98caa jet-table__body-cell\"><div class=\"jet-table__cell-inner\"><div class=\"jet-table__cell-content\"><div class=\"jet-table__cell-text\">Myopathies cong\u00e9nitales<\/div><\/div><\/div><\/td><td class=\"jet-table__cell elementor-repeater-item-f461347 jet-table__body-cell\"><div class=\"jet-table__cell-inner\"><div class=\"jet-table__cell-content\"><div class=\"jet-table__cell-text\">Troubles musculaires d\u2019origine g\u00e9n\u00e9tique, apparus d\u00e8s l\u2019enfance.<\/div><\/div><\/div><\/td><\/tr><tr class=\"jet-table__body-row elementor-repeater-item-aa82487\"><td class=\"jet-table__cell elementor-repeater-item-0a44b88 jet-table__body-cell\"><div class=\"jet-table__cell-inner\"><div class=\"jet-table__cell-content\"><div class=\"jet-table__cell-text\">Myopathies des ceintures<\/div><\/div><\/div><\/td><td class=\"jet-table__cell elementor-repeater-item-b36bc39 jet-table__body-cell\"><div class=\"jet-table__cell-inner\"><div class=\"jet-table__cell-content\"><div class=\"jet-table__cell-text\">Faiblesse des muscles des hanches et des \u00e9paules.<\/div><\/div><\/div><\/td><\/tr><tr class=\"jet-table__body-row elementor-repeater-item-2ae9e77\"><td class=\"jet-table__cell elementor-repeater-item-fd23ed1 jet-table__body-cell\"><div class=\"jet-table__cell-inner\"><div class=\"jet-table__cell-content\"><div class=\"jet-table__cell-text\">Myopathies distales<\/div><\/div><\/div><\/td><td class=\"jet-table__cell elementor-repeater-item-571ff22 jet-table__body-cell\"><div class=\"jet-table__cell-inner\"><div class=\"jet-table__cell-content\"><div class=\"jet-table__cell-text\">Faiblesse musculaire touchant d\u2019abord les extr\u00e9mit\u00e9s (mains, pieds).<\/div><\/div><\/div><\/td><\/tr><tr class=\"jet-table__body-row elementor-repeater-item-8a3ae61\"><td class=\"jet-table__cell elementor-repeater-item-88ee557 jet-table__body-cell\"><div class=\"jet-table__cell-inner\"><div class=\"jet-table__cell-content\"><div class=\"jet-table__cell-text\">Myopathies mitochondriales<\/div><\/div><\/div><\/td><td class=\"jet-table__cell elementor-repeater-item-52ea64e jet-table__body-cell\"><div class=\"jet-table__cell-inner\"><div class=\"jet-table__cell-content\"><div class=\"jet-table__cell-text\">D\u00e9fauts dans la production d\u2019\u00e9nergie cellulaire (\u00e9nergie produite par la nourriture et l\u2019oxyg\u00e8ne que nous consommons, servant \u00e0 faire fonctionner les cellules), touchant souvent plusieurs organes.<\/div><\/div><\/div><\/td><\/tr><tr class=\"jet-table__body-row elementor-repeater-item-c01ab90\"><td class=\"jet-table__cell elementor-repeater-item-fd1f390 jet-table__body-cell\"><div class=\"jet-table__cell-inner\"><div class=\"jet-table__cell-content\"><div class=\"jet-table__cell-text\">Myopathies myofibrillaires<\/div><\/div><\/div><\/td><td class=\"jet-table__cell elementor-repeater-item-23346cd jet-table__body-cell\"><div class=\"jet-table__cell-inner\"><div class=\"jet-table__cell-content\"><div class=\"jet-table__cell-text\">D\u00e9sorganisation des fibres musculaires (cellules du muscle, fines et longues, qui se serrent et se d\u00e9tendent pour permettre de bouger), entra\u00eenant une perte de force progressive.<\/div><\/div><\/div><\/td><\/tr><tr class=\"jet-table__body-row elementor-repeater-item-abff219\"><td class=\"jet-table__cell elementor-repeater-item-a1abacc jet-table__body-cell\"><div class=\"jet-table__cell-inner\"><div class=\"jet-table__cell-content\"><div class=\"jet-table__cell-text\">Myotonies cong\u00e9nitales (Thomsen et Becker)<\/div><\/div><\/div><\/td><td class=\"jet-table__cell elementor-repeater-item-481f67d jet-table__body-cell\"><div class=\"jet-table__cell-inner\"><div class=\"jet-table__cell-content\"><div class=\"jet-table__cell-text\">Difficult\u00e9 \u00e0 rel\u00e2cher les muscles apr\u00e8s contraction, pr\u00e9sente d\u00e8s la naissance.<\/div><\/div><\/div><\/td><\/tr><tr class=\"jet-table__body-row elementor-repeater-item-e802bf5\"><td class=\"jet-table__cell elementor-repeater-item-bcc501c jet-table__body-cell\"><div class=\"jet-table__cell-inner\"><div class=\"jet-table__cell-content\"><div class=\"jet-table__cell-text\">Myosites \u00e0 inclusions<\/div><\/div><\/div><\/td><td class=\"jet-table__cell elementor-repeater-item-85e3d79 jet-table__body-cell\"><div class=\"jet-table__cell-inner\"><div class=\"jet-table__cell-content\"><div class=\"jet-table__cell-text\">Inflammation chronique des muscles avec inclusions anormales dans les fibres (d\u00e9p\u00f4ts parasites qui s\u2019accumulent).<\/div><\/div><\/div><\/td><\/tr><tr class=\"jet-table__body-row elementor-repeater-item-f464662\"><td class=\"jet-table__cell elementor-repeater-item-4dfa3d8 jet-table__body-cell\"><div class=\"jet-table__cell-inner\"><div class=\"jet-table__cell-content\"><div class=\"jet-table__cell-text\">Paramyotonie d\u2019Eulenburg<\/div><\/div><\/div><\/td><td class=\"jet-table__cell elementor-repeater-item-c0d438d jet-table__body-cell\"><div class=\"jet-table__cell-inner\"><div class=\"jet-table__cell-content\"><div class=\"jet-table__cell-text\">Myotonie (difficult\u00e9 \u00e0 rel\u00e2cher un muscle apr\u00e8s contraction) aggrav\u00e9e par le froid, affectant les muscles faciaux et des membres.<\/div><\/div><\/div><\/td><\/tr><tr class=\"jet-table__body-row elementor-repeater-item-5d62421\"><td class=\"jet-table__cell elementor-repeater-item-8655edc jet-table__body-cell\"><div class=\"jet-table__cell-inner\"><div class=\"jet-table__cell-content\"><div class=\"jet-table__cell-text\">Paralysies p\u00e9riodiques hypo\/hyperkali\u00e9miques<\/div><\/div><\/div><\/td><td class=\"jet-table__cell elementor-repeater-item-45bf89c jet-table__body-cell\"><div class=\"jet-table__cell-inner\"><div class=\"jet-table__cell-content\"><div class=\"jet-table__cell-text\">Crises temporaires o\u00f9 la personne ne peut plus bouger ses muscles, comme si elle \u00e9tait \u201cparalys\u00e9e\u201d pendant un moment. Elles sont caus\u00e9es par un d\u00e9s\u00e9quilibre du potassium dans le sang. Ce potassium est essentiel pour que les muscles re\u00e7oivent les bons signaux du cerveau.<\/div><\/div><\/div><\/td><\/tr><tr class=\"jet-table__body-row elementor-repeater-item-ef64de0\"><td class=\"jet-table__cell elementor-repeater-item-43a456b jet-table__body-cell\"><div class=\"jet-table__cell-inner\"><div class=\"jet-table__cell-content\"><div class=\"jet-table__cell-text\">Syndrome des antisynth\u00e9tases<\/div><\/div><\/div><\/td><td class=\"jet-table__cell elementor-repeater-item-4b26ac6 jet-table__body-cell\"><div class=\"jet-table__cell-inner\"><div class=\"jet-table__cell-content\"><div class=\"jet-table__cell-text\">Maladie auto-immune avec atteinte musculaire, articulaire et pulmonaire.<\/div><\/div><\/div><\/td><\/tr><tr class=\"jet-table__body-row elementor-repeater-item-48ea0d5\"><td class=\"jet-table__cell elementor-repeater-item-f67b8a9 jet-table__body-cell\"><div class=\"jet-table__cell-inner\"><div class=\"jet-table__cell-content\"><div class=\"jet-table__cell-text\">Syndromes myasth\u00e9niques cong\u00e9nitaux<\/div><\/div><\/div><\/td><td class=\"jet-table__cell elementor-repeater-item-09a8b07 jet-table__body-cell\"><div class=\"jet-table__cell-inner\"><div class=\"jet-table__cell-content\"><div class=\"jet-table__cell-text\">D\u00e9fauts h\u00e9r\u00e9ditaires de la transmission entre nerf et muscle.<\/div><\/div><\/div><\/td><\/tr><\/tbody>\n\t\t\t<\/table>\n\t\t<\/div>\n\n\t\t<\/div>\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t<section class=\"elementor-section elementor-top-section elementor-element elementor-element-00fedf7 elementor-section-boxed elementor-section-height-default elementor-section-height-default\" data-id=\"00fedf7\" data-element_type=\"section\" data-e-type=\"section\" data-settings=\"{&quot;jet_parallax_layout_list&quot;:[]}\">\n\t\t\t\t\t\t<div class=\"elementor-container elementor-column-gap-default\">\n\t\t\t\t\t<div class=\"elementor-column elementor-col-100 elementor-top-column elementor-element elementor-element-7c5ff91\" data-id=\"7c5ff91\" data-element_type=\"column\" data-e-type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-079fd8f elementor-widget elementor-widget-spacer\" data-id=\"079fd8f\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"spacer.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t<div class=\"elementor-spacer\">\n\t\t\t<div class=\"elementor-spacer-inner\"><\/div>\n\t\t<\/div>\n\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/section>\n\t\t\t\t<section class=\"elementor-section elementor-top-section elementor-element elementor-element-9d0c27f elementor-section-boxed elementor-section-height-default elementor-section-height-default\" data-id=\"9d0c27f\" data-element_type=\"section\" data-e-type=\"section\" data-settings=\"{&quot;jet_parallax_layout_list&quot;:[]}\">\n\t\t\t\t\t\t<div class=\"elementor-container elementor-column-gap-default\">\n\t\t\t\t\t<div class=\"elementor-column elementor-col-100 elementor-top-column elementor-element elementor-element-a44c1e2\" data-id=\"a44c1e2\" data-element_type=\"column\" data-e-type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-50d8f4f elementor-widget elementor-widget-heading\" data-id=\"50d8f4f\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"heading.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t<h3 class=\"elementor-heading-title elementor-size-default\">Sympt\u00f4mes des maladies neuromusculaires<\/h3>\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/section>\n\t\t\t\t<section class=\"elementor-section elementor-top-section elementor-element elementor-element-11a20b5 elementor-section-boxed elementor-section-height-default elementor-section-height-default\" data-id=\"11a20b5\" data-element_type=\"section\" data-e-type=\"section\" data-settings=\"{&quot;jet_parallax_layout_list&quot;:[]}\">\n\t\t\t\t\t\t<div class=\"elementor-container elementor-column-gap-default\">\n\t\t\t\t\t<div class=\"elementor-column elementor-col-100 elementor-top-column elementor-element elementor-element-624c45b\" data-id=\"624c45b\" data-element_type=\"column\" data-e-type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-393660d elementor-widget elementor-widget-text-editor\" data-id=\"393660d\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<p>La nature des sympt\u00f4mes des maladies neuromusculaires est\u00a0<strong>propre \u00e0 chaque type de pathologie<\/strong>(1). Toutefois, plusieurs signes cliniques sont r\u00e9currents et doivent interpeller.<\/p><p>\u00a0<\/p><p><strong>La faiblesse musculaire progressive est le sympt\u00f4me le plus commun.<\/strong>\u00a0Elle d\u00e9bute dans les jambes, les bras ou les muscles du visage, selon la maladie concern\u00e9e(3).<\/p><p>\u00a0<\/p><p>Certaines personnes d\u00e9crivent \u00e9galement des douleurs musculaires, une fatigue inhabituelle, ou des crampes r\u00e9p\u00e9t\u00e9es. Ces troubles peuvent alt\u00e9rer la marche, la prise en main ou m\u00eame la respiration(1)(3).<\/p><p>\u00a0<\/p><p>Certaines maladies, comme les dystrophies myotoniques, ont des sympt\u00f4mes sp\u00e9cifiques. Ces sympt\u00f4mes incluent la myotonie, qui est la difficult\u00e9 \u00e0 rel\u00e2cher un muscle apr\u00e8s l&#8217;avoir contract\u00e9. D&#8217;autres sympt\u00f4mes peuvent \u00eatre des probl\u00e8mes cardiaques ou des cataractes pr\u00e9coces(3).<\/p><p>\u00a0<\/p><p><strong>L\u2019identification de ces signes, m\u00eame s&#8217;ils sont discrets, oriente vers un diagnostic.<\/strong><\/p>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/section>\n\t\t\t\t<section class=\"elementor-section elementor-top-section elementor-element elementor-element-2a58ae8 elementor-section-boxed elementor-section-height-default elementor-section-height-default\" data-id=\"2a58ae8\" data-element_type=\"section\" data-e-type=\"section\" data-settings=\"{&quot;jet_parallax_layout_list&quot;:[]}\">\n\t\t\t\t\t\t<div class=\"elementor-container elementor-column-gap-default\">\n\t\t\t\t\t<div class=\"elementor-column elementor-col-100 elementor-top-column elementor-element elementor-element-dfd0e1e\" data-id=\"dfd0e1e\" data-element_type=\"column\" data-e-type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-7f1cd11 elementor-widget elementor-widget-spacer\" data-id=\"7f1cd11\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"spacer.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t<div class=\"elementor-spacer\">\n\t\t\t<div class=\"elementor-spacer-inner\"><\/div>\n\t\t<\/div>\n\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/section>\n\t\t\t\t<section class=\"elementor-section elementor-top-section elementor-element elementor-element-e6c9fa7 elementor-section-boxed elementor-section-height-default elementor-section-height-default\" data-id=\"e6c9fa7\" data-element_type=\"section\" data-e-type=\"section\" data-settings=\"{&quot;jet_parallax_layout_list&quot;:[]}\">\n\t\t\t\t\t\t<div class=\"elementor-container elementor-column-gap-default\">\n\t\t\t\t\t<div class=\"elementor-column elementor-col-100 elementor-top-column elementor-element elementor-element-89f2116\" data-id=\"89f2116\" data-element_type=\"column\" data-e-type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-9ebc2ff elementor-widget elementor-widget-heading\" data-id=\"9ebc2ff\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"heading.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t<h2 class=\"elementor-heading-title elementor-size-default\">Comment diagnostiquer une maladie neuromusculaire ?<\/h2>\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/section>\n\t\t\t\t<section class=\"elementor-section elementor-top-section elementor-element elementor-element-75f55e2 elementor-section-boxed elementor-section-height-default elementor-section-height-default\" data-id=\"75f55e2\" data-element_type=\"section\" data-e-type=\"section\" data-settings=\"{&quot;jet_parallax_layout_list&quot;:[]}\">\n\t\t\t\t\t\t<div class=\"elementor-container elementor-column-gap-default\">\n\t\t\t\t\t<div class=\"elementor-column elementor-col-100 elementor-top-column elementor-element elementor-element-fd3e754\" data-id=\"fd3e754\" data-element_type=\"column\" data-e-type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-8f4dd97 elementor-widget elementor-widget-heading\" data-id=\"8f4dd97\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"heading.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t<h3 class=\"elementor-heading-title elementor-size-default\">Examens m\u00e9dicaux et tests g\u00e9n\u00e9tiques<\/h3>\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/section>\n\t\t\t\t<section class=\"elementor-section elementor-top-section elementor-element elementor-element-1ad41a9 elementor-section-boxed elementor-section-height-default elementor-section-height-default\" data-id=\"1ad41a9\" data-element_type=\"section\" data-e-type=\"section\" data-settings=\"{&quot;jet_parallax_layout_list&quot;:[]}\">\n\t\t\t\t\t\t<div class=\"elementor-container elementor-column-gap-default\">\n\t\t\t\t\t<div class=\"elementor-column elementor-col-100 elementor-top-column elementor-element elementor-element-ffa0ad9\" data-id=\"ffa0ad9\" data-element_type=\"column\" data-e-type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-e492f3f elementor-widget elementor-widget-text-editor\" data-id=\"e492f3f\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<p>Pour \u00e9tablir le diagnostic d\u2019une <a href=\"https:\/\/orthopus.com\/fr\/maladies-neuromusculaires\/traitement-maladie-neuromusculaire\/dystrophie-musculaire-traitement-technologie\/\">maladie neuromusculaire<\/a>, l\u2019ensemble des examens cliniques et biologiques a son importance(3).<\/p><p>Le m\u00e9decin r\u00e9alise un examen clinique neurologique et demande des examens compl\u00e9mentaires sp\u00e9cifiques :<\/p><ul><li><strong>\u00c9lectromyogramme (EMG)<\/strong> pour mesurer l\u2019activit\u00e9 \u00e9lectrique des muscles.<\/li><li><strong>Biopsie musculaire<\/strong> pour observer les cellules musculaires au microscope.<\/li><li><strong>Tests g\u00e9n\u00e9tiques<\/strong> pour identifier une \u00e9ventuelle mutation responsable de la maladie.<\/li><\/ul><p>Des analyses sanguines peuvent montrer parfois un taux plus \u00e9lev\u00e9 de CPK (cr\u00e9atine phosphokinase), signe d\u2019une destruction musculaire.<\/p>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/section>\n\t\t\t\t<section class=\"elementor-section elementor-top-section elementor-element elementor-element-14becd6 elementor-section-boxed elementor-section-height-default elementor-section-height-default\" data-id=\"14becd6\" data-element_type=\"section\" data-e-type=\"section\" data-settings=\"{&quot;jet_parallax_layout_list&quot;:[]}\">\n\t\t\t\t\t\t<div class=\"elementor-container elementor-column-gap-default\">\n\t\t\t\t\t<div class=\"elementor-column elementor-col-100 elementor-top-column elementor-element elementor-element-c829a9f\" data-id=\"c829a9f\" data-element_type=\"column\" data-e-type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-162679a elementor-widget elementor-widget-spacer\" data-id=\"162679a\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"spacer.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t<div class=\"elementor-spacer\">\n\t\t\t<div class=\"elementor-spacer-inner\"><\/div>\n\t\t<\/div>\n\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/section>\n\t\t\t\t<section class=\"elementor-section elementor-top-section elementor-element elementor-element-be09e56 elementor-section-boxed elementor-section-height-default elementor-section-height-default\" data-id=\"be09e56\" data-element_type=\"section\" data-e-type=\"section\" data-settings=\"{&quot;jet_parallax_layout_list&quot;:[]}\">\n\t\t\t\t\t\t<div class=\"elementor-container elementor-column-gap-default\">\n\t\t\t\t\t<div class=\"elementor-column elementor-col-100 elementor-top-column elementor-element elementor-element-7183461\" data-id=\"7183461\" data-element_type=\"column\" data-e-type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-c301cf1 elementor-widget elementor-widget-heading\" data-id=\"c301cf1\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"heading.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t<h3 class=\"elementor-heading-title elementor-size-default\">Importance d\u2019un diagnostic pr\u00e9coce<\/h3>\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/section>\n\t\t\t\t<section class=\"elementor-section elementor-top-section elementor-element elementor-element-5063d10 elementor-section-boxed elementor-section-height-default elementor-section-height-default\" data-id=\"5063d10\" data-element_type=\"section\" data-e-type=\"section\" data-settings=\"{&quot;jet_parallax_layout_list&quot;:[]}\">\n\t\t\t\t\t\t<div class=\"elementor-container elementor-column-gap-default\">\n\t\t\t\t\t<div class=\"elementor-column elementor-col-100 elementor-top-column elementor-element elementor-element-2b39dd2\" data-id=\"2b39dd2\" data-element_type=\"column\" data-e-type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-9424ada elementor-widget elementor-widget-text-editor\" data-id=\"9424ada\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<p><strong>Un diagnostic pr\u00e9coce <\/strong>aide \u00e0<strong> une prise en charge plus rapide<\/strong>. Dans certains cas, il permet un traitement innovant. Cela peut ralentir la progression de la maladie.<\/p><p>\u00a0<\/p><p>C\u2019est aussi un levier pour\u00a0<strong>acc\u00e9der \u00e0 un protocole de recherche<\/strong>. Il aide aussi avec le conseil g\u00e9n\u00e9tique.<\/p><p>\u00a0<\/p><p>Cela signifie un entretien avec un sp\u00e9cialiste. Ce sp\u00e9cialiste explique si une maladie g\u00e9n\u00e9tique peut toucher une personne ou sa famille. Il parle aussi des risques de transmission(3)(12).<\/p>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/section>\n\t\t\t\t<section class=\"elementor-section elementor-top-section elementor-element elementor-element-ee711ac elementor-section-boxed elementor-section-height-default elementor-section-height-default\" data-id=\"ee711ac\" data-element_type=\"section\" data-e-type=\"section\" data-settings=\"{&quot;jet_parallax_layout_list&quot;:[]}\">\n\t\t\t\t\t\t<div class=\"elementor-container elementor-column-gap-default\">\n\t\t\t\t\t<div class=\"elementor-column elementor-col-100 elementor-top-column elementor-element elementor-element-4f89ceb\" data-id=\"4f89ceb\" data-element_type=\"column\" data-e-type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-b9c2803 elementor-widget elementor-widget-spacer\" data-id=\"b9c2803\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"spacer.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t<div class=\"elementor-spacer\">\n\t\t\t<div class=\"elementor-spacer-inner\"><\/div>\n\t\t<\/div>\n\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/section>\n\t\t\t\t<section class=\"elementor-section elementor-top-section elementor-element elementor-element-f235342 elementor-section-boxed elementor-section-height-default elementor-section-height-default\" data-id=\"f235342\" data-element_type=\"section\" data-e-type=\"section\" data-settings=\"{&quot;jet_parallax_layout_list&quot;:[]}\">\n\t\t\t\t\t\t<div class=\"elementor-container elementor-column-gap-default\">\n\t\t\t\t\t<div class=\"elementor-column elementor-col-100 elementor-top-column elementor-element elementor-element-e331f46\" data-id=\"e331f46\" data-element_type=\"column\" data-e-type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-5064299 elementor-widget elementor-widget-heading\" data-id=\"5064299\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"heading.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t<h2 class=\"elementor-heading-title elementor-size-default\">Traitements et prise en charge des maladies neuromusculaires<\/h2>\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/section>\n\t\t\t\t<section class=\"elementor-section elementor-top-section elementor-element elementor-element-5cacb79 elementor-section-boxed elementor-section-height-default elementor-section-height-default\" data-id=\"5cacb79\" data-element_type=\"section\" data-e-type=\"section\" data-settings=\"{&quot;jet_parallax_layout_list&quot;:[]}\">\n\t\t\t\t\t\t<div class=\"elementor-container elementor-column-gap-default\">\n\t\t\t\t\t<div class=\"elementor-column elementor-col-100 elementor-top-column elementor-element elementor-element-517875b\" data-id=\"517875b\" data-element_type=\"column\" data-e-type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-249d225 elementor-widget elementor-widget-heading\" data-id=\"249d225\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"heading.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t<h3 class=\"elementor-heading-title elementor-size-default\">Approche m\u00e9dicamenteuse et th\u00e9rapies en d\u00e9veloppement<\/h3>\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/section>\n\t\t\t\t<section class=\"elementor-section elementor-top-section elementor-element elementor-element-49b4502 elementor-section-boxed elementor-section-height-default elementor-section-height-default\" data-id=\"49b4502\" data-element_type=\"section\" data-e-type=\"section\" data-settings=\"{&quot;jet_parallax_layout_list&quot;:[]}\">\n\t\t\t\t\t\t<div class=\"elementor-container elementor-column-gap-default\">\n\t\t\t\t\t<div class=\"elementor-column elementor-col-100 elementor-top-column elementor-element elementor-element-b009d49\" data-id=\"b009d49\" data-element_type=\"column\" data-e-type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-7316fac elementor-widget elementor-widget-text-editor\" data-id=\"7316fac\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<p>Depuis quelques ann\u00e9es, des <a href=\"https:\/\/orthopus.com\/fr\/maladies-neuromusculaires\/traitement-maladie-neuromusculaire\/\">th\u00e9rapies innovantes<\/a> sont accessibles pour certaines de ces maladies. Certaines stabilisent, d\u2019autres freinent la d\u00e9gradation motrice et peuvent apaiser les sympt\u00f4mes et ralentir l\u2019\u00e9volution.<\/p><p>Certains m\u00e9dicaments sont d\u00e9j\u00e0 utilis\u00e9s :<\/p><ul><li>Les <strong>corticost\u00e9ro\u00efdes\u00a0<\/strong>(13) (comme la prednisone) sont prescrits pour certaines formes, comme la <a href=\"https:\/\/orthopus.com\/fr\/maladies-neuromusculaires\/dystrophie-musculaire-de-duchenne\/\"><strong>myopathie de Duchenne<\/strong><\/a>. Ils aident \u00e0 pr\u00e9server la force musculaire et \u00e0 retarder la perte de mobilit\u00e9.<\/li><li>Les traitements <strong>immunosuppresseurs<\/strong> sont utilis\u00e9s dans les formes auto-immunes. Ils visent \u00e0 r\u00e9duire l\u2019inflammation lorsque le <strong>syst\u00e8me immunitaire<\/strong> s\u2019attaque aux muscles.<\/li><\/ul><p>De nouvelles pistes de recherche sont aussi en cours :<\/p><ul><li>Les <strong>th\u00e9rapies g\u00e9niques<\/strong>, comme l<strong>&#8216;exon skipping<\/strong>(14) ou la technique <strong>CRISPR<\/strong>(15), visent \u00e0 traiter la cause de la maladie. <strong>CRISPR<\/strong> est une sorte de &#8220;ciseaux g\u00e9n\u00e9tiques&#8221; qui corrige les erreurs dans l&#8217;ADN.<\/li><li>La th\u00e9rapie cellulaire et certains <strong>biom\u00e9dicaments<\/strong> font aussi l\u2019objet d\u2019essais cliniques. L\u2019objectif : d\u00e9velopper des traitements plus cibl\u00e9s et durables.<\/li><\/ul>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/section>\n\t\t\t\t<section class=\"elementor-section elementor-top-section elementor-element elementor-element-7889280 elementor-section-boxed elementor-section-height-default elementor-section-height-default\" data-id=\"7889280\" data-element_type=\"section\" data-e-type=\"section\" data-settings=\"{&quot;jet_parallax_layout_list&quot;:[]}\">\n\t\t\t\t\t\t<div class=\"elementor-container elementor-column-gap-default\">\n\t\t\t\t\t<div class=\"elementor-column elementor-col-100 elementor-top-column elementor-element elementor-element-33b6876\" data-id=\"33b6876\" data-element_type=\"column\" data-e-type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-c38f2aa elementor-widget elementor-widget-spacer\" data-id=\"c38f2aa\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"spacer.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t<div class=\"elementor-spacer\">\n\t\t\t<div class=\"elementor-spacer-inner\"><\/div>\n\t\t<\/div>\n\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/section>\n\t\t\t\t<section class=\"elementor-section elementor-top-section elementor-element elementor-element-d396c6d elementor-section-boxed elementor-section-height-default elementor-section-height-default\" data-id=\"d396c6d\" data-element_type=\"section\" data-e-type=\"section\" data-settings=\"{&quot;jet_parallax_layout_list&quot;:[]}\">\n\t\t\t\t\t\t<div class=\"elementor-container elementor-column-gap-default\">\n\t\t\t\t\t<div class=\"elementor-column elementor-col-100 elementor-top-column elementor-element elementor-element-bbb2a47\" data-id=\"bbb2a47\" data-element_type=\"column\" data-e-type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-3216076 elementor-widget elementor-widget-heading\" data-id=\"3216076\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"heading.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t<h3 class=\"elementor-heading-title elementor-size-default\">R\u00e9\u00e9ducation et maintien des capacit\u00e9s motrices<\/h3>\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/section>\n\t\t\t\t<section class=\"elementor-section elementor-top-section elementor-element elementor-element-9394cc5 elementor-section-boxed elementor-section-height-default elementor-section-height-default\" data-id=\"9394cc5\" data-element_type=\"section\" data-e-type=\"section\" data-settings=\"{&quot;jet_parallax_layout_list&quot;:[]}\">\n\t\t\t\t\t\t<div class=\"elementor-container elementor-column-gap-default\">\n\t\t\t\t\t<div class=\"elementor-column elementor-col-100 elementor-top-column elementor-element elementor-element-d9ff3d3\" data-id=\"d9ff3d3\" data-element_type=\"column\" data-e-type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-d61edd1 elementor-widget elementor-widget-text-editor\" data-id=\"d61edd1\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<p>La r\u00e9\u00e9ducation fonctionnelle est un pilier central de la prise en charge. Elle vise \u00e0 maintenir l\u2019autonomie et \u00e0 \u00e9viter les complications.<\/p><p>Les outils et m\u00e9thodes utilis\u00e9s incluent :<\/p><ul><li><strong>La <a href=\"https:\/\/orthopus.com\/fr\/professionnels-de-sante\/kine-pour-neuropathie\/\">kin\u00e9sith\u00e9rapie<\/a> sp\u00e9cialis\u00e9e<\/strong><\/li><li><strong>Des exercices d\u2019assouplissement et de renforcement<\/strong><\/li><li><strong>Des orth\u00e8ses pour soutenir les membres affaiblis<\/strong><\/li><\/ul><p>Le recours \u00e0 des <strong>fauteuils roulants \u00e9lectriques<\/strong> ou <strong>aides \u00e0 la marche<\/strong> peut \u00eatre n\u00e9cessaire, selon le degr\u00e9 d\u2019atteinte(3).<\/p>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/section>\n\t\t\t\t<section class=\"elementor-section elementor-top-section elementor-element elementor-element-ad83fa1 elementor-section-boxed elementor-section-height-default elementor-section-height-default\" data-id=\"ad83fa1\" data-element_type=\"section\" data-e-type=\"section\" data-settings=\"{&quot;jet_parallax_layout_list&quot;:[]}\">\n\t\t\t\t\t\t<div class=\"elementor-container elementor-column-gap-default\">\n\t\t\t\t\t<div class=\"elementor-column elementor-col-100 elementor-top-column elementor-element elementor-element-4607be9\" data-id=\"4607be9\" data-element_type=\"column\" data-e-type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-6e62feb elementor-widget elementor-widget-spacer\" data-id=\"6e62feb\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"spacer.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t<div class=\"elementor-spacer\">\n\t\t\t<div class=\"elementor-spacer-inner\"><\/div>\n\t\t<\/div>\n\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/section>\n\t\t\t\t<section class=\"elementor-section elementor-top-section elementor-element elementor-element-b1d194f elementor-section-boxed elementor-section-height-default elementor-section-height-default\" data-id=\"b1d194f\" data-element_type=\"section\" data-e-type=\"section\" data-settings=\"{&quot;jet_parallax_layout_list&quot;:[]}\">\n\t\t\t\t\t\t<div class=\"elementor-container elementor-column-gap-default\">\n\t\t\t\t\t<div class=\"elementor-column elementor-col-100 elementor-top-column elementor-element elementor-element-d655040\" data-id=\"d655040\" data-element_type=\"column\" data-e-type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-b3fb238 elementor-widget elementor-widget-heading\" data-id=\"b3fb238\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"heading.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t<h3 class=\"elementor-heading-title elementor-size-default\">Solutions innovantes pour am\u00e9liorer la qualit\u00e9 de vie<\/h3>\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/section>\n\t\t\t\t<section class=\"elementor-section elementor-top-section elementor-element elementor-element-bc910ac elementor-section-boxed elementor-section-height-default elementor-section-height-default\" data-id=\"bc910ac\" data-element_type=\"section\" data-e-type=\"section\" data-settings=\"{&quot;jet_parallax_layout_list&quot;:[]}\">\n\t\t\t\t\t\t<div class=\"elementor-container elementor-column-gap-default\">\n\t\t\t\t\t<div class=\"elementor-column elementor-col-100 elementor-top-column elementor-element elementor-element-ea2de78\" data-id=\"ea2de78\" data-element_type=\"column\" data-e-type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-964df6d elementor-widget__width-initial elementor-widget elementor-widget-text-editor\" data-id=\"964df6d\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<p><strong>L\u2019innovation technologique apporte des solutions concr\u00e8tes pour le quotidien :<\/strong><\/p>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/section>\n\t\t\t\t<section class=\"elementor-section elementor-top-section elementor-element elementor-element-76559ef elementor-section-boxed elementor-section-height-default elementor-section-height-default\" data-id=\"76559ef\" data-element_type=\"section\" data-e-type=\"section\" data-settings=\"{&quot;jet_parallax_layout_list&quot;:[]}\">\n\t\t\t\t\t\t<div class=\"elementor-container elementor-column-gap-default\">\n\t\t\t\t\t<div class=\"elementor-column elementor-col-50 elementor-top-column elementor-element elementor-element-9d03f70\" data-id=\"9d03f70\" data-element_type=\"column\" data-e-type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-0e16c5d elementor-widget elementor-widget-text-editor\" data-id=\"0e16c5d\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<ul><li><strong>Bras articul\u00e9s<\/strong>\u00a0fix\u00e9s sur fauteuils pour soutenir et\/ou all\u00e9ger le poids des bras.<\/li><li><strong>Les exosquelettes passifs<\/strong> sont des dispositifs sans source d\u2019\u00e9nergie. Ils utilisent des mat\u00e9riaux comme des ressorts. Leur but est d\u2019assister les mouvements r\u00e9p\u00e9titifs et de r\u00e9duire la fatigue.<\/li><li><strong>Orth\u00e8ses dynamiques<\/strong>\u00a0qui permettent un certain mouvement tout en offrant un soutien.<\/li><li><strong><a href=\"https:\/\/orthopus.com\/fr\/aide-technique\/bras-robotique-handicap-orthopus\/\">Bras robotiques<\/a> d\u2019assistance<\/strong>\u00a0pilotables par l\u2019utilisateur.rice : ils permettent de r\u00e9aliser des gestes du quotidien en toute autonomie. De nombreuses personnes t\u00e9moignent aujourd\u2019hui de leur impact positif sur l\u2019ind\u00e9pendance et la qualit\u00e9 de vie.<\/li><\/ul>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t<div class=\"elementor-column elementor-col-50 elementor-top-column elementor-element elementor-element-37da8ef\" data-id=\"37da8ef\" data-element_type=\"column\" data-e-type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-4ffa63a elementor-widget elementor-widget-video\" data-id=\"4ffa63a\" data-element_type=\"widget\" data-e-type=\"widget\" data-settings=\"{&quot;youtube_url&quot;:&quot;https:\\\/\\\/www.youtube.com\\\/watch?v=FodOrCqKKZ0&quot;,&quot;video_type&quot;:&quot;youtube&quot;,&quot;controls&quot;:&quot;yes&quot;}\" data-widget_type=\"video.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t<div class=\"elementor-wrapper elementor-open-inline\">\n\t\t\t<div class=\"elementor-video\"><\/div>\t\t<\/div>\n\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/section>\n\t\t\t\t<section class=\"elementor-section elementor-top-section elementor-element elementor-element-e6a7538 elementor-section-boxed elementor-section-height-default elementor-section-height-default\" data-id=\"e6a7538\" data-element_type=\"section\" data-e-type=\"section\" data-settings=\"{&quot;jet_parallax_layout_list&quot;:[]}\">\n\t\t\t\t\t\t<div class=\"elementor-container elementor-column-gap-default\">\n\t\t\t\t\t<div class=\"elementor-column elementor-col-100 elementor-top-column elementor-element elementor-element-c177ad6\" data-id=\"c177ad6\" data-element_type=\"column\" data-e-type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-5216434 elementor-widget elementor-widget-text-editor\" data-id=\"5216434\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<p><strong>Les maladies neuromusculaires<\/strong>\u00a0n\u00e9cessitent une approche multidisciplinaire alliant m\u00e9decine, g\u00e9n\u00e9tique, r\u00e9\u00e9ducation et innovations techniques. Une meilleure compr\u00e9hension de ces affections ouvre la voie \u00e0 des traitements plus cibl\u00e9s et efficaces(3).\u00a0<strong>Informer, diagnostiquer t\u00f4t et accompagner<\/strong>\u00a0sont les piliers d\u2019une prise en charge r\u00e9ussie pour les maladies neuromusculaires.<\/p>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/section>\n\t\t<div class=\"elementor-element elementor-element-9dd6006 e-flex e-con-boxed e-con e-parent\" data-id=\"9dd6006\" data-element_type=\"container\" data-e-type=\"container\" data-settings=\"{&quot;jet_parallax_layout_list&quot;:[]}\">\n\t\t\t\t\t<div class=\"e-con-inner\">\n\t\t\t\t<div class=\"elementor-element elementor-element-7f88b4f elementor-widget elementor-widget-toggle\" data-id=\"7f88b4f\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"toggle.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t<div class=\"elementor-toggle\">\n\t\t\t\t\t\t\t<div class=\"elementor-toggle-item\">\n\t\t\t\t\t<div id=\"elementor-tab-title-1331\" class=\"elementor-tab-title\" data-tab=\"1\" role=\"button\" aria-controls=\"elementor-tab-content-1331\" aria-expanded=\"false\">\n\t\t\t\t\t\t\t\t\t\t\t\t<span class=\"elementor-toggle-icon elementor-toggle-icon-right\" aria-hidden=\"true\">\n\t\t\t\t\t\t\t\t\t\t\t\t\t\t\t<span class=\"elementor-toggle-icon-closed\"><i class=\"fas fa-caret-right\"><\/i><\/span>\n\t\t\t\t\t\t\t\t<span class=\"elementor-toggle-icon-opened\"><i class=\"elementor-toggle-icon-opened fas fa-caret-up\"><\/i><\/span>\n\t\t\t\t\t\t\t\t\t\t\t\t\t<\/span>\n\t\t\t\t\t\t\t\t\t\t\t\t<a class=\"elementor-toggle-title\" tabindex=\"0\">Quelles sont les principales maladies neuromusculaires\u202f?<\/a>\n\t\t\t\t\t<\/div>\n\n\t\t\t\t\t<div id=\"elementor-tab-content-1331\" class=\"elementor-tab-content elementor-clearfix\" data-tab=\"1\" role=\"region\" aria-labelledby=\"elementor-tab-title-1331\"><p>Les maladies neuromusculaires regroupent environ 400 affections diff\u00e9rentes qui touchent soit les muscles, soit les nerfs p\u00e9riph\u00e9riques, soit la jonction entre les deux. Parmi les principales, on retrouve\u202f:<\/p><ul><li>Les dystrophies musculaires (ex\u202f: <a href=\"https:\/\/orthopus.com\/fr\/maladies-neuromusculaires\/dystrophie-musculaire-de-duchenne\/\">Duchenne<\/a>, <a href=\"https:\/\/orthopus.com\/fr\/maladies-neuromusculaires\/dystrophie-musculaire-de-becker\/\">Becker<\/a>, Emery-Dreifuss)<\/li><li>Les myopathies cong\u00e9nitales ou m\u00e9taboliques<\/li><li>Les neuropathies (ex\u202f: <a href=\"https:\/\/orthopus.com\/fr\/maladies-neuromusculaires\/maladies-neuromusculaires-charcot-marie-tooth\/\">maladie de Charcot-Marie-Tooth<\/a>)<\/li><li>Les maladies de la jonction neuromusculaire (ex\u202f: myasth\u00e9nie)<\/li><li>Les amyotrophies spinales<\/li><li>Les ataxies h\u00e9r\u00e9ditaires (ex\u202f: ataxie de Friedreich)<\/li><li>La dystrophie myotonique de Steinert.<\/li><\/ul><\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t\t\t<div class=\"elementor-toggle-item\">\n\t\t\t\t\t<div id=\"elementor-tab-title-1332\" class=\"elementor-tab-title\" data-tab=\"2\" role=\"button\" aria-controls=\"elementor-tab-content-1332\" aria-expanded=\"false\">\n\t\t\t\t\t\t\t\t\t\t\t\t<span class=\"elementor-toggle-icon elementor-toggle-icon-right\" aria-hidden=\"true\">\n\t\t\t\t\t\t\t\t\t\t\t\t\t\t\t<span class=\"elementor-toggle-icon-closed\"><i class=\"fas fa-caret-right\"><\/i><\/span>\n\t\t\t\t\t\t\t\t<span class=\"elementor-toggle-icon-opened\"><i class=\"elementor-toggle-icon-opened fas fa-caret-up\"><\/i><\/span>\n\t\t\t\t\t\t\t\t\t\t\t\t\t<\/span>\n\t\t\t\t\t\t\t\t\t\t\t\t<a class=\"elementor-toggle-title\" tabindex=\"0\">Comment savoir si je souffre de troubles neuromusculaires\u202f?<\/a>\n\t\t\t\t\t<\/div>\n\n\t\t\t\t\t<div id=\"elementor-tab-content-1332\" class=\"elementor-tab-content elementor-clearfix\" data-tab=\"2\" role=\"region\" aria-labelledby=\"elementor-tab-title-1332\"><p>Les signes \u00e9vocateurs sont\u202f:<\/p><ul><li>Faiblesse musculaire persistante ou progressive<\/li><li>Difficult\u00e9s \u00e0 effectuer des gestes du quotidien (monter les escaliers, se lever d\u2019une chaise, soulever des objets)<\/li><li>Chutes fr\u00e9quentes, maladresse<\/li><li>Crampes, spasmes, fatigue musculaire<\/li><li>Atrophie visible de certains muscles<\/li><li>Troubles de la d\u00e9glutition, de la parole ou de la respiration dans certains cas<br \/>Un diagnostic pr\u00e9cis n\u00e9cessite une \u00e9valuation m\u00e9dicale\u202f: examen clinique, \u00e9lectromyogramme, analyses sanguines, tests g\u00e9n\u00e9tiques, etc.<\/li><\/ul><\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t\t\t<div class=\"elementor-toggle-item\">\n\t\t\t\t\t<div id=\"elementor-tab-title-1333\" class=\"elementor-tab-title\" data-tab=\"3\" role=\"button\" aria-controls=\"elementor-tab-content-1333\" aria-expanded=\"false\">\n\t\t\t\t\t\t\t\t\t\t\t\t<span class=\"elementor-toggle-icon elementor-toggle-icon-right\" aria-hidden=\"true\">\n\t\t\t\t\t\t\t\t\t\t\t\t\t\t\t<span class=\"elementor-toggle-icon-closed\"><i class=\"fas fa-caret-right\"><\/i><\/span>\n\t\t\t\t\t\t\t\t<span class=\"elementor-toggle-icon-opened\"><i class=\"elementor-toggle-icon-opened fas fa-caret-up\"><\/i><\/span>\n\t\t\t\t\t\t\t\t\t\t\t\t\t<\/span>\n\t\t\t\t\t\t\t\t\t\t\t\t<a class=\"elementor-toggle-title\" tabindex=\"0\">Quelle est la maladie qui attaque les muscles et les nerfs\u202f?<\/a>\n\t\t\t\t\t<\/div>\n\n\t\t\t\t\t<div id=\"elementor-tab-content-1333\" class=\"elementor-tab-content elementor-clearfix\" data-tab=\"3\" role=\"region\" aria-labelledby=\"elementor-tab-title-1333\"><p>Plusieurs maladies neuromusculaires s\u2019attaquent \u00e0 la fois aux muscles et aux nerfs. Par exemple, la scl\u00e9rose lat\u00e9rale amyotrophique (SLA ou maladie de Charcot) d\u00e9truit les motoneurones responsables de la commande musculaire, entra\u00eenant une faiblesse et une atrophie musculaires progressives. <a href=\"https:\/\/orthopus.com\/fr\/maladies-neuromusculaires\/maladies-neuromusculaires-charcot-marie-tooth\/\">La maladie de Charcot-Marie-Tooth<\/a> touche les nerfs p\u00e9riph\u00e9riques et provoque une perte de force et une atrophie des muscles distaux.<\/p><\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t\t\t<div class=\"elementor-toggle-item\">\n\t\t\t\t\t<div id=\"elementor-tab-title-1334\" class=\"elementor-tab-title\" data-tab=\"4\" role=\"button\" aria-controls=\"elementor-tab-content-1334\" aria-expanded=\"false\">\n\t\t\t\t\t\t\t\t\t\t\t\t<span class=\"elementor-toggle-icon elementor-toggle-icon-right\" aria-hidden=\"true\">\n\t\t\t\t\t\t\t\t\t\t\t\t\t\t\t<span class=\"elementor-toggle-icon-closed\"><i class=\"fas fa-caret-right\"><\/i><\/span>\n\t\t\t\t\t\t\t\t<span class=\"elementor-toggle-icon-opened\"><i class=\"elementor-toggle-icon-opened fas fa-caret-up\"><\/i><\/span>\n\t\t\t\t\t\t\t\t\t\t\t\t\t<\/span>\n\t\t\t\t\t\t\t\t\t\t\t\t<a class=\"elementor-toggle-title\" tabindex=\"0\">Quelle maladie neurologique provoque une perte de force des membres\u202f?<\/a>\n\t\t\t\t\t<\/div>\n\n\t\t\t\t\t<div id=\"elementor-tab-content-1334\" class=\"elementor-tab-content elementor-clearfix\" data-tab=\"4\" role=\"region\" aria-labelledby=\"elementor-tab-title-1334\"><p>La SLA (scl\u00e9rose lat\u00e9rale amyotrophique) est l\u2019exemple le plus connu\u202f: elle entra\u00eene une perte progressive de la force dans les bras et les jambes, puis une atrophie musculaire. D\u2019autres maladies comme l\u2019amyotrophie spinale, certaines myopathies ou la maladie de <a href=\"https:\/\/orthopus.com\/fr\/maladies-neuromusculaires\/maladies-neuromusculaires-charcot-marie-tooth\/\">Charcot-Marie-Tooth<\/a> peuvent \u00e9galement provoquer une perte de force des membres.<\/p><\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t\t\t<div class=\"elementor-toggle-item\">\n\t\t\t\t\t<div id=\"elementor-tab-title-1335\" class=\"elementor-tab-title\" data-tab=\"5\" role=\"button\" aria-controls=\"elementor-tab-content-1335\" aria-expanded=\"false\">\n\t\t\t\t\t\t\t\t\t\t\t\t<span class=\"elementor-toggle-icon elementor-toggle-icon-right\" aria-hidden=\"true\">\n\t\t\t\t\t\t\t\t\t\t\t\t\t\t\t<span class=\"elementor-toggle-icon-closed\"><i class=\"fas fa-caret-right\"><\/i><\/span>\n\t\t\t\t\t\t\t\t<span class=\"elementor-toggle-icon-opened\"><i class=\"elementor-toggle-icon-opened fas fa-caret-up\"><\/i><\/span>\n\t\t\t\t\t\t\t\t\t\t\t\t\t<\/span>\n\t\t\t\t\t\t\t\t\t\t\t\t<a class=\"elementor-toggle-title\" tabindex=\"0\">Comment reconna\u00eetre les signes pr\u00e9coces d\u2019une faiblesse musculaire\u202f?<\/a>\n\t\t\t\t\t<\/div>\n\n\t\t\t\t\t<div id=\"elementor-tab-content-1335\" class=\"elementor-tab-content elementor-clearfix\" data-tab=\"5\" role=\"region\" aria-labelledby=\"elementor-tab-title-1335\"><p class=\"my-0\">Soyez attentif \u00e0\u202f:<\/p><ul class=\"marker:text-textOff list-disc\"><li><p class=\"my-0\">Une difficult\u00e9 inhabituelle \u00e0 monter ou descendre les escaliers<\/p><\/li><li><p class=\"my-0\">Une fatigue musculaire excessive apr\u00e8s un effort mod\u00e9r\u00e9<\/p><\/li><li><p class=\"my-0\">Une tendance \u00e0 tr\u00e9bucher ou \u00e0 tomber plus souvent<\/p><\/li><li><p class=\"my-0\">Une perte de masse musculaire visible (amincissement des bras, jambes, mollets)<\/p><\/li><li><p class=\"my-0\">Des difficult\u00e9s \u00e0 effectuer des gestes fins ou \u00e0 tenir des objets<\/p><\/li><li><p class=\"my-0\">Des crampes ou des fasciculations (petits mouvements involontaires des muscles)<\/p><\/li><\/ul><\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t\t\t<div class=\"elementor-toggle-item\">\n\t\t\t\t\t<div id=\"elementor-tab-title-1336\" class=\"elementor-tab-title\" data-tab=\"6\" role=\"button\" aria-controls=\"elementor-tab-content-1336\" aria-expanded=\"false\">\n\t\t\t\t\t\t\t\t\t\t\t\t<span class=\"elementor-toggle-icon elementor-toggle-icon-right\" aria-hidden=\"true\">\n\t\t\t\t\t\t\t\t\t\t\t\t\t\t\t<span class=\"elementor-toggle-icon-closed\"><i class=\"fas fa-caret-right\"><\/i><\/span>\n\t\t\t\t\t\t\t\t<span class=\"elementor-toggle-icon-opened\"><i class=\"elementor-toggle-icon-opened fas fa-caret-up\"><\/i><\/span>\n\t\t\t\t\t\t\t\t\t\t\t\t\t<\/span>\n\t\t\t\t\t\t\t\t\t\t\t\t<a class=\"elementor-toggle-title\" tabindex=\"0\">Quelles sont les principales causes g\u00e9n\u00e9tiques des maladies neuromusculaires\u202f?<\/a>\n\t\t\t\t\t<\/div>\n\n\t\t\t\t\t<div id=\"elementor-tab-content-1336\" class=\"elementor-tab-content elementor-clearfix\" data-tab=\"6\" role=\"region\" aria-labelledby=\"elementor-tab-title-1336\"><p class=\"my-0\">La majorit\u00e9 des maladies neuromusculaires sont d\u2019origine g\u00e9n\u00e9tique. Les mutations concernent\u202f:<\/p><ul class=\"marker:text-textOff list-disc\"><li><p class=\"my-0\">Des g\u00e8nes codant pour des prot\u00e9ines essentielles du muscle (ex\u202f: dystrophine dans la <a href=\"https:\/\/orthopus.com\/fr\/maladies-neuromusculaires\/dystrophie-musculaire-de-duchenne\/\">dystrophie de Duchenne<\/a>)<\/p><\/li><li><p class=\"my-0\">Des g\u00e8nes impliqu\u00e9s dans la transmission nerveuse (ex\u202f: SMN1 pour l\u2019<a href=\"https:\/\/orthopus.com\/fr\/maladies-neuromusculaires\/maladies-neuromusculaires-amyotrophie-spinale-proximale\/\">amyotrophie spinale<\/a>)<\/p><\/li><li><p class=\"my-0\">Des g\u00e8nes responsables du bon fonctionnement des nerfs p\u00e9riph\u00e9riques (ex\u202f: PMP22 dans la <a href=\"https:\/\/orthopus.com\/fr\/maladies-neuromusculaires\/maladies-neuromusculaires-charcot-marie-tooth\/\">maladie de Charcot-Marie-Tooth<\/a>)<\/p><\/li><li><p class=\"my-0\">D\u2019autres g\u00e8nes impliqu\u00e9s dans le m\u00e9tabolisme musculaire ou la jonction neuromusculaire<br \/>Un conseil\u202f: si vous avez des ant\u00e9c\u00e9dents familiaux ou des sympt\u00f4mes \u00e9vocateurs, parlez-en \u00e0 votre m\u00e9decin pour envisager un d\u00e9pistage g\u00e9n\u00e9tique adapt\u00e9<\/p><\/li><\/ul><\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t<section class=\"elementor-section elementor-top-section elementor-element elementor-element-23ec2a8 elementor-section-boxed elementor-section-height-default elementor-section-height-default\" data-id=\"23ec2a8\" data-element_type=\"section\" data-e-type=\"section\" data-settings=\"{&quot;jet_parallax_layout_list&quot;:[]}\">\n\t\t\t\t\t\t<div class=\"elementor-container elementor-column-gap-default\">\n\t\t\t\t\t<div class=\"elementor-column elementor-col-100 elementor-top-column elementor-element elementor-element-74c219b\" data-id=\"74c219b\" data-element_type=\"column\" data-e-type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-66a3a08 elementor-widget elementor-widget-text-editor\" data-id=\"66a3a08\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<div class=\"border-borderMain\/50 ring-borderMain\/50 divide-borderMain\/50 dark:divide-borderMainDark\/50 dark:ring-borderMainDark\/50 dark:border-borderMainDark\/50 bg-transparent\"><div class=\"gap-y-sm md:gap-y-md flex flex-col\"><div class=\"relative font-sans text-base text-textMain dark:text-textMainDark selection:bg-super\/50 selection:text-textMain dark:selection:bg-superDuper\/10 dark:selection:text-superDark\"><div class=\"min-w-0 break-words [word-break:break-word]\"><div id=\"markdown-content-1\" class=\"gap-y-md after:clear-both after:block after:content-['']\" dir=\"auto\"><div class=\"relative\"><div class=\"prose text-pretty dark:prose-invert inline leading-normal break-words min-w-0 [word-break:break-word]\"><p class=\"my-0\">Pour toute question ou pour un accompagnement personnalis\u00e9, n\u2019h\u00e9sitez pas \u00e0 consulter un professionnel de sant\u00e9 sp\u00e9cialis\u00e9 dans les maladies neuromusculaires.<\/p><\/div><\/div><\/div><\/div><\/div><\/div><\/div>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/section>\n\t\t\t\t<section class=\"elementor-section elementor-top-section elementor-element elementor-element-a674d3f elementor-section-boxed elementor-section-height-default elementor-section-height-default\" data-id=\"a674d3f\" data-element_type=\"section\" data-e-type=\"section\" data-settings=\"{&quot;jet_parallax_layout_list&quot;:[]}\">\n\t\t\t\t\t\t<div class=\"elementor-container elementor-column-gap-default\">\n\t\t\t\t\t<div class=\"elementor-column elementor-col-100 elementor-top-column elementor-element elementor-element-bd2a852\" data-id=\"bd2a852\" data-element_type=\"column\" data-e-type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-4c7e0e5 elementor-widget elementor-widget-spacer\" data-id=\"4c7e0e5\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"spacer.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t<div class=\"elementor-spacer\">\n\t\t\t<div class=\"elementor-spacer-inner\"><\/div>\n\t\t<\/div>\n\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/section>\n\t\t\t\t<section class=\"elementor-section elementor-top-section elementor-element elementor-element-b5ee586 elementor-section-boxed elementor-section-height-default elementor-section-height-default\" data-id=\"b5ee586\" data-element_type=\"section\" data-e-type=\"section\" data-settings=\"{&quot;jet_parallax_layout_list&quot;:[]}\">\n\t\t\t\t\t\t<div class=\"elementor-container elementor-column-gap-default\">\n\t\t\t\t\t<div class=\"elementor-column elementor-col-100 elementor-top-column elementor-element elementor-element-d0300bf\" data-id=\"d0300bf\" data-element_type=\"column\" data-e-type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-4faae02 elementor-widget elementor-widget-heading\" data-id=\"4faae02\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"heading.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t<h2 class=\"elementor-heading-title elementor-size-default\">Sources<\/h2>\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/section>\n\t\t\t\t<section class=\"elementor-section elementor-top-section elementor-element elementor-element-aece1f8 elementor-section-boxed elementor-section-height-default elementor-section-height-default\" data-id=\"aece1f8\" data-element_type=\"section\" data-e-type=\"section\" data-settings=\"{&quot;jet_parallax_layout_list&quot;:[]}\">\n\t\t\t\t\t\t<div class=\"elementor-container elementor-column-gap-default\">\n\t\t\t\t\t<div class=\"elementor-column elementor-col-100 elementor-top-column elementor-element elementor-element-417c684\" data-id=\"417c684\" data-element_type=\"column\" data-e-type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-caa409a elementor-widget elementor-widget-text-editor\" data-id=\"caa409a\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<p>1. Anamorphik. Maladies neuromusculaires [Internet]. F\u00e9d\u00e9ration Fran\u00e7aise de Neurologie. 2024 [cit\u00e9 2 mai 2025]. Disponible sur: <a href=\"https:\/\/www.ffn-neurologie.fr\/maladies\/maladies-neuromusculaires\/\" target=\"_blank\" rel=\"nofollow noopener\">https:\/\/www.ffn-neurologie.fr\/maladies\/maladies-neuromusculaires\/<\/a><br \/>2. Centre de r\u00e9f\u00e9rence constitutif des maladies rares neuromusculaires Nord\/Est\/Ile-de-France \u2013 GNMH \u2013 ESMARA [Internet]. [cit\u00e9 2 mai 2025]. Disponible sur: <a href=\"https:\/\/esmaramaladiesrares.fr\/centre-de-reference-des-maladies-rares-neuromusculaires-gnmh\/\" target=\"_blank\" rel=\"nofollow noopener\">https:\/\/esmaramaladiesrares.fr\/centre-de-reference-des-maladies-rares-neuromusculaires-gnmh\/<\/a><br \/>3. Maladies neuromusculaires | AFM T\u00e9l\u00e9thon [Internet]. 2020 [cit\u00e9 2 mai 2025]. Disponible sur: <a href=\"https:\/\/www.afm-telethon.fr\/fr\/fiches-maladies\/maladies-neuromusculaires\" target=\"_blank\" rel=\"nofollow noopener\">https:\/\/www.afm-telethon.fr\/fr\/fiches-maladies\/maladies-neuromusculaires<\/a><br \/>4. Dystrophie musculaire de Duchenne | AFM T\u00e9l\u00e9thon [Internet]. 2024 [cit\u00e9 2 mai 2025]. Disponible sur: <a href=\"https:\/\/www.afm-telethon.fr\/fr\/fiches-maladies\/dystrophie-musculaire-de-duchenne\" target=\"_blank\" rel=\"nofollow noopener\">https:\/\/www.afm-telethon.fr\/fr\/fiches-maladies\/dystrophie-musculaire-de-duchenne<\/a><br \/>5. Dystrophie musculaire de Becker | AFM T\u00e9l\u00e9thon [Internet]. 2024 [cit\u00e9 2 mai 2025]. Disponible sur: <a href=\"https:\/\/www.afm-telethon.fr\/fr\/fiches-maladies\/dystrophie-musculaire-de-becker\" target=\"_blank\" rel=\"nofollow noopener\">https:\/\/www.afm-telethon.fr\/fr\/fiches-maladies\/dystrophie-musculaire-de-becker<\/a><br \/>6. Maladie de Charcot-Marie-Tooth | AFM T\u00e9l\u00e9thon [Internet]. 2024 [cit\u00e9 2 mai 2025]. Disponible sur: <a href=\"https:\/\/www.afm-telethon.fr\/fr\/fiches-maladies\/maladie-de-charcot-marie-tooth\" target=\"_blank\" rel=\"nofollow noopener\">https:\/\/www.afm-telethon.fr\/fr\/fiches-maladies\/maladie-de-charcot-marie-tooth<\/a><br \/>7. Maladie de Steinert | AFM T\u00e9l\u00e9thon [Internet]. 2020 [cit\u00e9 2 mai 2025]. Disponible sur: <a href=\"https:\/\/www.afm-telethon.fr\/fr\/fiches-maladies\/maladie-de-steinert\" target=\"_blank\" rel=\"nofollow noopener\">https:\/\/www.afm-telethon.fr\/fr\/fiches-maladies\/maladie-de-steinert<\/a><br \/>8. Myopathie facio-scapulo-hum\u00e9rale | AFM T\u00e9l\u00e9thon [Internet]. 2024 [cit\u00e9 2 mai 2025]. Disponible sur: <a href=\"https:\/\/www.afm-telethon.fr\/fr\/fiches-maladies\/myopathie-facio-scapulo-humerale\" target=\"_blank\" rel=\"nofollow noopener\">https:\/\/www.afm-telethon.fr\/fr\/fiches-maladies\/myopathie-facio-scapulo-humerale<\/a><br \/>9. Amyotrophie spinale proximale li\u00e9e \u00e0 SMN1 | AFM T\u00e9l\u00e9thon [Internet]. 2025 [cit\u00e9 2 mai 2025]. Disponible sur: <a href=\"https:\/\/www.afm-telethon.fr\/fr\/fiches-maladies\/amyotrophie-spinale-proximale-liee-smn1\" target=\"_blank\" rel=\"nofollow noopener\">https:\/\/www.afm-telethon.fr\/fr\/fiches-maladies\/amyotrophie-spinale-proximale-liee-smn1<\/a><br \/>10. Myopathies mitochondriales | AFM T\u00e9l\u00e9thon [Internet]. 2024 [cit\u00e9 2 mai 2025]. Disponible sur: <a href=\"https:\/\/www.afm-telethon.fr\/fr\/fiches-maladies\/myopathies-mitochondriales\" target=\"_blank\" rel=\"nofollow noopener\">https:\/\/www.afm-telethon.fr\/fr\/fiches-maladies\/myopathies-mitochondriales<\/a><br \/>11. Syndromes myasth\u00e9niques cong\u00e9nitaux | AFM T\u00e9l\u00e9thon [Internet]. 2020 [cit\u00e9 2 mai 2025]. Disponible sur: <a href=\"https:\/\/www.afm-telethon.fr\/fr\/fiches-maladies\/syndromes-myastheniques-congenitaux\" target=\"_blank\" rel=\"nofollow noopener\">https:\/\/www.afm-telethon.fr\/fr\/fiches-maladies\/syndromes-myastheniques-congenitaux<\/a><br \/>12. La consultation de conseil g\u00e9n\u00e9tique | AFM T\u00e9l\u00e9thon [Internet]. 2014 [cit\u00e9 2 mai 2025]. Disponible sur: <a href=\"https:\/\/www.afm-telethon.fr\/fr\/vivre-avec-la-maladie\/je-m-informe-sur-les-maladies\/comprendre-les-maladies-genetiques\/consultation-genetique\" target=\"_blank\" rel=\"nofollow noopener\">https:\/\/www.afm-telethon.fr\/fr\/vivre-avec-la-maladie\/je-m-informe-sur-les-maladies\/comprendre-les-maladies-genetiques\/consultation-genetique<\/a><br \/>13. Manuels MSD pour le grand public [Internet]. [cit\u00e9 2 mai 2025]. Table:Cortico\u00efdes\u202f: Utilisations et effets secondaires. Disponible sur: <a href=\"https:\/\/www.msdmanuals.com\/fr\/accueil\/multimedia\/table\/cortico\u00efdes-utilisations-et-effets-secondaires\" target=\"_blank\" rel=\"nofollow noopener\">https:\/\/www.msdmanuals.com\/fr\/accueil\/multimedia\/table\/cortico\u00efdes-utilisations-et-effets-secondaires<\/a><br \/>14. Goyenvalle A, Vulin A, Fougerousse F, Leturcq F, Kaplan JC, Garcia L, et al. Le saut d\u2019exon th\u00e9rapeutique\u202f: un espoir pour les dystrophinopathies. m\u00e9decine\/sciences. 1 d\u00e9c 2004;20(12):1163\u20115.<br \/>15. CRISPR-Cas9\u202f: une avanc\u00e9e pour les maladies g\u00e9n\u00e9tiques | AFM T\u00e9l\u00e9thon [Internet]. 2025 [cit\u00e9 2 mai 2025]. Disponible sur: <a href=\"https:\/\/www.afm-telethon.fr\/fr\/termes\/crisprcas9\" target=\"_blank\" rel=\"nofollow noopener\">https:\/\/www.afm-telethon.fr\/fr\/termes\/crisprcas9<\/a><\/p>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/section>\n\t\t\t\t<section class=\"elementor-section elementor-top-section elementor-element elementor-element-e87a44d elementor-section-boxed elementor-section-height-default elementor-section-height-default\" data-id=\"e87a44d\" data-element_type=\"section\" data-e-type=\"section\" data-settings=\"{&quot;jet_parallax_layout_list&quot;:[]}\">\n\t\t\t\t\t\t<div class=\"elementor-container elementor-column-gap-default\">\n\t\t\t\t\t<div class=\"elementor-column elementor-col-100 elementor-top-column elementor-element elementor-element-d06f987\" data-id=\"d06f987\" data-element_type=\"column\" data-e-type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-eb02e9b elementor-widget elementor-widget-html\" data-id=\"eb02e9b\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"html.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t<script type=\"application\/ld+json\">\n{\n  \"@context\": \"https:\/\/schema.org\",\n  \"@graph\": [\n    {\n      \"@type\": \"WebPage\",\n      \"name\": \"Maladies neuromusculaires\",\n      \"url\": \"https:\/\/orthopus.com\/fr\/maladies-neuromusculaires\/\",\n      \"reviewedBy\": {\n        \"@type\": \"Person\",\n        \"name\": \"Dr Capucine de Lattre\",\n        \"jobTitle\": \"M\u00e9decin sp\u00e9cialiste en m\u00e9decine physique et de r\u00e9adaptation\",\n        \"affiliation\": {\n          \"@type\": \"Organization\",\n          \"name\": \"\u00c9tablissement de Sant\u00e9 pour Enfants et Adolescents de la r\u00e9gion Nantaise\"\n        }\n      }\n    },\n    {\n      \"@type\": \"MedicalCondition\",\n      \"name\": \"Dystrophie musculaire de Duchenne\/Becker\",\n      \"description\": \"Maladie g\u00e9n\u00e9tique grave apparaissant chez les gar\u00e7ons, affectant principalement les muscles.\"\n    },\n    {\n      \"@type\": \"MedicalCondition\",\n      \"name\": \"Neuropathies de Charcot-Marie-Tooth\",\n      \"description\": \"Maladies h\u00e9r\u00e9ditaires affectant les nerfs p\u00e9riph\u00e9riques, responsables de la transmission des signaux entre le cerveau et le corps.\"\n    },\n    {\n      \"@type\": \"MedicalCondition\",\n      \"name\": \"Dystrophie myotonique de Steinert\",\n      \"description\": \"Maladie caract\u00e9ris\u00e9e par une myotonie (difficult\u00e9 \u00e0 rel\u00e2cher les muscles apr\u00e8s contraction), avec complications cardiaques et endocriniennes.\"\n    },\n    {\n      \"@type\": \"MedicalCondition\",\n      \"name\": \"Myopathie facio-scapulo-hum\u00e9rale\",\n      \"description\": \"Maladie d\u00e9butant g\u00e9n\u00e9ralement par une faiblesse des muscles du visage et des \u00e9paules.\"\n    },\n    {\n      \"@type\": \"MedicalCondition\",\n      \"name\": \"Amyotrophie spinale proximale li\u00e9e au g\u00e8ne SMN1\",\n      \"description\": \"Maladie g\u00e9n\u00e9tique grave de la petite enfance affectant le moto-neurone, responsable de la transmission des ordres du cerveau aux muscles.\"\n    },\n    {\n      \"@type\": \"MedicalCondition\",\n      \"name\": \"Myopathies mitochondriales\",\n      \"description\": \"Affections caus\u00e9es par une perturbation de la production d'\u00e9nergie dans les cellules musculaires.\"\n    },\n    {\n      \"@type\": \"MedicalCondition\",\n      \"name\": \"Syndromes myasth\u00e9niques cong\u00e9nitaux\",\n      \"description\": \"Troubles de la transmission neuromusculaire pr\u00e9sents d\u00e8s la naissance.\"\n    },\n    {\n      \"@type\": \"FAQPage\",\n      \"mainEntity\": [\n        {\n          \"@type\": \"Question\",\n          \"name\": \"Quelles sont les principales maladies neuromusculaires\u202f?\",\n          \"acceptedAnswer\": {\n            \"@type\": \"Answer\",\n            \"text\": \"Les maladies neuromusculaires regroupent environ 300 affections diff\u00e9rentes qui touchent soit les muscles, soit les nerfs p\u00e9riph\u00e9riques, soit la jonction entre les deux. Parmi les principales, on retrouve : les dystrophies musculaires (ex : Duchenne, Becker, Emery-Dreifuss), les myopathies cong\u00e9nitales ou m\u00e9taboliques, les neuropathies (ex : maladie de Charcot-Marie-Tooth), les maladies de la jonction neuromusculaire (ex : myasth\u00e9nie), les amyotrophies spinales, les ataxies h\u00e9r\u00e9ditaires (ex : ataxie de Friedreich), la dystrophie myotonique de Steinert.\"\n          }\n        },\n        {\n          \"@type\": \"Question\",\n          \"name\": \"Comment savoir si je souffre de troubles neuromusculaires\u202f?\",\n          \"acceptedAnswer\": {\n            \"@type\": \"Answer\",\n            \"text\": \"Les signes \u00e9vocateurs sont : faiblesse musculaire persistante ou progressive, difficult\u00e9s \u00e0 effectuer des gestes du quotidien (monter les escaliers, se lever d\u2019une chaise, soulever des objets), chutes fr\u00e9quentes, maladresse, crampes, spasmes, fatigue musculaire, atrophie visible de certains muscles, troubles de la d\u00e9glutition, de la parole ou de la respiration dans certains cas. Un diagnostic pr\u00e9cis n\u00e9cessite une \u00e9valuation m\u00e9dicale : examen clinique, \u00e9lectromyogramme, analyses sanguines, tests g\u00e9n\u00e9tiques, etc.\"\n          }\n        },\n        {\n          \"@type\": \"Question\",\n          \"name\": \"Quelle est la maladie qui attaque les muscles et les nerfs\u202f?\",\n          \"acceptedAnswer\": {\n            \"@type\": \"Answer\",\n            \"text\": \"Plusieurs maladies neuromusculaires s\u2019attaquent \u00e0 la fois aux muscles et aux nerfs. Par exemple, la scl\u00e9rose lat\u00e9rale amyotrophique (SLA ou maladie de Charcot) d\u00e9truit les motoneurones responsables de la commande musculaire, entra\u00eenant une faiblesse et une atrophie musculaires progressives. La maladie de Charcot-Marie-Tooth touche les nerfs p\u00e9riph\u00e9riques et provoque une perte de force et une atrophie des muscles distaux.\"\n          }\n        },\n        {\n          \"@type\": \"Question\",\n          \"name\": \"Quelle maladie neurologique provoque une perte de force des membres\u202f?\",\n          \"acceptedAnswer\": {\n            \"@type\": \"Answer\",\n            \"text\": \"La SLA (scl\u00e9rose lat\u00e9rale amyotrophique) est l\u2019exemple le plus connu : elle entra\u00eene une perte progressive de la force dans les bras et les jambes, puis une atrophie musculaire. D\u2019autres maladies comme l\u2019amyotrophie spinale, certaines myopathies ou la maladie de Charcot-Marie-Tooth peuvent \u00e9galement provoquer une perte de force des membres.\"\n          }\n        },\n        {\n          \"@type\": \"Question\",\n          \"name\": \"Comment reconna\u00eetre les signes pr\u00e9coces d\u2019une faiblesse musculaire\u202f?\",\n          \"acceptedAnswer\": {\n            \"@type\": \"Answer\",\n            \"text\": \"Soyez attentif \u00e0 : une difficult\u00e9 inhabituelle \u00e0 monter ou descendre les escaliers, une fatigue musculaire excessive apr\u00e8s un effort mod\u00e9r\u00e9, une tendance \u00e0 tr\u00e9bucher ou \u00e0 tomber plus souvent, une perte de masse musculaire visible (amincissement des bras, jambes, mollets), des difficult\u00e9s \u00e0 effectuer des gestes fins ou \u00e0 tenir des objets, des crampes ou des fasciculations (petits mouvements involontaires des muscles).\"\n          }\n        },\n        {\n          \"@type\": \"Question\",\n          \"name\": \"Quelles sont les principales causes g\u00e9n\u00e9tiques des maladies neuromusculaires\u202f?\",\n          \"acceptedAnswer\": {\n            \"@type\": \"Answer\",\n            \"text\": \"La majorit\u00e9 des maladies neuromusculaires sont d\u2019origine g\u00e9n\u00e9tique. Les mutations concernent : des g\u00e8nes codant pour des prot\u00e9ines essentielles du muscle (ex : dystrophine dans la dystrophie de Duchenne), des g\u00e8nes impliqu\u00e9s dans la transmission nerveuse (ex : SMN1 pour l\u2019amyotrophie spinale), des g\u00e8nes responsables du bon fonctionnement des nerfs p\u00e9riph\u00e9riques (ex : PMP22 dans la maladie de Charcot-Marie-Tooth), ou encore d\u2019autres g\u00e8nes impliqu\u00e9s dans le m\u00e9tabolisme musculaire ou la jonction neuromusculaire. Si vous avez des ant\u00e9c\u00e9dents familiaux ou des sympt\u00f4mes \u00e9vocateurs, parlez-en \u00e0 votre m\u00e9decin pour envisager un d\u00e9pistage g\u00e9n\u00e9tique adapt\u00e9.\"\n          }\n        }\n      ]\n    }\n  ]\n}\n<\/script>\n\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/section>\n\t\t\t\t<\/div>\n\t\t","protected":false},"excerpt":{"rendered":"<p>Tout savoir sur les maladies neuromusculaires Contenu relu et valid\u00e9 par le Dr Capucine DE LATTRE, m\u00e9decin sp\u00e9cialiste en m\u00e9decine physique et de r\u00e9adaptation Les maladies neuromusculaires constituent un ensemble de maladies rares qui touchent le syst\u00e8me nerveux p\u00e9riph\u00e9rique. Elles entra\u00eenent un dysfonctionnement de la fonction motrice par diff\u00e9rents m\u00e9canismes.(1) Cette atteinte motrice peut \u00eatre [&hellip;]<\/p>\n","protected":false},"author":15,"featured_media":0,"parent":0,"menu_order":0,"comment_status":"closed","ping_status":"closed","template":"","meta":{"_jet_sm_ready_style":"","_jet_sm_style":"","_jet_sm_controls_values":"","_jet_sm_fonts_collection":"","_jet_sm_fonts_links":"","footnotes":""},"class_list":["post-16340","page","type-page","status-publish","hentry"],"yoast_head":"<!-- This site is optimized with the Yoast SEO plugin v27.4 - https:\/\/yoast.com\/product\/yoast-seo-wordpress\/ -->\n<title>Maladies neuromusculaires: guide complet<\/title>\n<meta name=\"description\" content=\"D\u00e9couvrez les maladies neuromusculaires, leurs sympt\u00f4mes, traitements et liste d\u00e9taill\u00e9e. 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